Idiopathic sclerosing encapsulating peritonitis: an uncommon cause of intestinal obstruction

Sclerosing encapsulating peritonitis (SEP), also called encapsulating peritonitis, is a rare and benign cause of intestinal obstruction of unknown etiology. Its onset may be acute or subacute although there are some reports with a two-month history. More commonly, this entity is secondary to chronic...

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Main Authors: José de Arimatéia Batista Araújo Filho, João Augusto Santos Martines, Brenda Margatho Ramos Martines, Adriano Ferreira Silva, Silvana Maria Lovisolo, Cláudio Campi de Castro
Format: Article
Language:English
Published: University of São Paulo 2012-09-01
Series:Autopsy and Case Reports
Subjects:
Online Access:http://www.revistas.usp.br/autopsy/article/view/48232
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author José de Arimatéia Batista Araújo Filho
João Augusto Santos Martines
Brenda Margatho Ramos Martines
Adriano Ferreira Silva
Silvana Maria Lovisolo
Cláudio Campi de Castro
author_facet José de Arimatéia Batista Araújo Filho
João Augusto Santos Martines
Brenda Margatho Ramos Martines
Adriano Ferreira Silva
Silvana Maria Lovisolo
Cláudio Campi de Castro
author_sort José de Arimatéia Batista Araújo Filho
collection DOAJ
description Sclerosing encapsulating peritonitis (SEP), also called encapsulating peritonitis, is a rare and benign cause of intestinal obstruction of unknown etiology. Its onset may be acute or subacute although there are some reports with a two-month history. More commonly, this entity is secondary to chronic peritoneal dialysis, ventriculoperitoneal and peritoneovenous shunting, the use of β-blockers and systemic lupus erythematous. Recurrent episodes of bacterial peritonitis, intestinal tuberculosis, sarcoidosis, familial Mediterranean fever, gastrointestinal cancer, liver transplantation, intra-abdominal fibrogenic foreign bodies, and luteinized ovarian thecomas are also related to SEP. The idiopathic presentation is more rare. Abdominal pain, nausea, vomiting, weight loss, malnutrition, and clinically palpable mass characterize the clinical features. Diagnosis is frequently made with gross findings during surgery, imaging workup and histopathology. The authors report the case of a 36-yearold male patient with a 10-day history of abdominal pain that was operated on because of intestinal obstruction. Diagnosis was made preoperatively and confirmed by the intraoperative findings and histopathology.
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spelling doaj.art-72f6e98c3a0548409a670f58e8bcb5e32022-12-21T19:53:03ZengUniversity of São PauloAutopsy and Case Reports2236-19602012-09-012310.4322/acr.%y.4823247925Idiopathic sclerosing encapsulating peritonitis: an uncommon cause of intestinal obstructionJosé de Arimatéia Batista Araújo Filho0João Augusto Santos Martines1Brenda Margatho Ramos Martines2Adriano Ferreira Silva3Silvana Maria Lovisolo4Cláudio Campi de Castro5Heart Institute – Hospital das Clínicas – Faculdade de Medicina – Universidade de São PauloDiagnostic Imaging Service – Hospital Universitário – Universidade de São PauloDiagnostic Imaging Service – Hospital Universitário – Universidade de São PauloDiagnostic Imaging Service – Hospital Universitário – Universidade de São PauloAnatomic Pathology Service – Hospital Universitário – Universidade de São PauloDiagnostic Imaging Service – Hospital Universitário – Universidade de São Paulo; Department of Radiology – Faculdade de Medicina – Universidade de São PauloSclerosing encapsulating peritonitis (SEP), also called encapsulating peritonitis, is a rare and benign cause of intestinal obstruction of unknown etiology. Its onset may be acute or subacute although there are some reports with a two-month history. More commonly, this entity is secondary to chronic peritoneal dialysis, ventriculoperitoneal and peritoneovenous shunting, the use of β-blockers and systemic lupus erythematous. Recurrent episodes of bacterial peritonitis, intestinal tuberculosis, sarcoidosis, familial Mediterranean fever, gastrointestinal cancer, liver transplantation, intra-abdominal fibrogenic foreign bodies, and luteinized ovarian thecomas are also related to SEP. The idiopathic presentation is more rare. Abdominal pain, nausea, vomiting, weight loss, malnutrition, and clinically palpable mass characterize the clinical features. Diagnosis is frequently made with gross findings during surgery, imaging workup and histopathology. The authors report the case of a 36-yearold male patient with a 10-day history of abdominal pain that was operated on because of intestinal obstruction. Diagnosis was made preoperatively and confirmed by the intraoperative findings and histopathology.http://www.revistas.usp.br/autopsy/article/view/48232Abdominal painIntestinal obstructionPeritoneal fibrosisSurgery
spellingShingle José de Arimatéia Batista Araújo Filho
João Augusto Santos Martines
Brenda Margatho Ramos Martines
Adriano Ferreira Silva
Silvana Maria Lovisolo
Cláudio Campi de Castro
Idiopathic sclerosing encapsulating peritonitis: an uncommon cause of intestinal obstruction
Autopsy and Case Reports
Abdominal pain
Intestinal obstruction
Peritoneal fibrosis
Surgery
title Idiopathic sclerosing encapsulating peritonitis: an uncommon cause of intestinal obstruction
title_full Idiopathic sclerosing encapsulating peritonitis: an uncommon cause of intestinal obstruction
title_fullStr Idiopathic sclerosing encapsulating peritonitis: an uncommon cause of intestinal obstruction
title_full_unstemmed Idiopathic sclerosing encapsulating peritonitis: an uncommon cause of intestinal obstruction
title_short Idiopathic sclerosing encapsulating peritonitis: an uncommon cause of intestinal obstruction
title_sort idiopathic sclerosing encapsulating peritonitis an uncommon cause of intestinal obstruction
topic Abdominal pain
Intestinal obstruction
Peritoneal fibrosis
Surgery
url http://www.revistas.usp.br/autopsy/article/view/48232
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