An unexpected and unusual cause of pulmonary hypertension in a patient with hypersensitivity pneumonitis: partial anomalous pulmonary venous connection causing pulmonary artery hypertension
Partial anomalous pulmonary venous connection (PAPVC) occurs when any pulmonary vein, but not all, drains directly into the right atrium or its venous tributaries. PAPVC can very rarely present as an individual cause of pulmonary artery hypertension. Here we are presenting a case of a 41-year-old f...
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| Format: | Article |
| Language: | English |
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PAGEPress Publications
2023-03-01
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| Series: | Monaldi Archives for Chest Disease |
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| Online Access: | https://www.monaldi-archives.org/index.php/macd/article/view/2497 |
| _version_ | 1811160224466206720 |
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| author | Pratap Upadhya Shivam Garg Jeevanandham A. Nesamani Daniel Ponraj Ahmed Wayez |
| author_facet | Pratap Upadhya Shivam Garg Jeevanandham A. Nesamani Daniel Ponraj Ahmed Wayez |
| author_sort | Pratap Upadhya |
| collection | DOAJ |
| description |
Partial anomalous pulmonary venous connection (PAPVC) occurs when any pulmonary vein, but not all, drains directly into the right atrium or its venous tributaries. PAPVC can very rarely present as an individual cause of pulmonary artery hypertension. Here we are presenting a case of a 41-year-old farmer with a history of exertional dyspnoea for the past three years, which increased over 6 months. Chest high-resolution computed tomography (HRCT) was suggestive of non-fibrotic hypersensitivity pneumonitis. Hence the patient was started on systemic steroids, with which the patient’s oxygen saturation improved. On 2D-ECHO, the right ventricle systolic pressure was 48+RAP. Right heart catheterization showed mean pulmonary artery pressure of 73 mmHG, PVR 8.7. On further evaluation, CTPA was done, which surprisingly revealed the left superior pulmonary vein draining into the left brachiocephalic vein.
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| first_indexed | 2024-04-10T05:55:10Z |
| format | Article |
| id | doaj.art-74bb8d8b448142c387c31036e7d41011 |
| institution | Directory Open Access Journal |
| issn | 1122-0643 2532-5264 |
| language | English |
| last_indexed | 2024-04-10T05:55:10Z |
| publishDate | 2023-03-01 |
| publisher | PAGEPress Publications |
| record_format | Article |
| series | Monaldi Archives for Chest Disease |
| spelling | doaj.art-74bb8d8b448142c387c31036e7d410112023-03-03T17:43:35ZengPAGEPress PublicationsMonaldi Archives for Chest Disease1122-06432532-52642023-03-0110.4081/monaldi.2023.2497An unexpected and unusual cause of pulmonary hypertension in a patient with hypersensitivity pneumonitis: partial anomalous pulmonary venous connection causing pulmonary artery hypertensionPratap Upadhya0Shivam Garg1Jeevanandham A.2Nesamani Daniel Ponraj3Ahmed Wayez4Department of Pulmonary Medicine,Jawaharlal Institute of Postgraduate Medical Education and Research, PuducherryDepartment of Pulmonary Medicine, Jawaharlal Institute of Postgraduate Medical Education and Research, PuducherryDepartment of Pulmonary Medicine, Jawaharlal Institute of Postgraduate Medical Education and Research, PuducherryDepartment of Radiodiagnosis, Jawaharlal Institute of Postgraduate Medical Education and Research, PuducherryDepartment of Cardiology, Jawaharlal Institute of Postgraduate Medical Education and Research, Puducherry Partial anomalous pulmonary venous connection (PAPVC) occurs when any pulmonary vein, but not all, drains directly into the right atrium or its venous tributaries. PAPVC can very rarely present as an individual cause of pulmonary artery hypertension. Here we are presenting a case of a 41-year-old farmer with a history of exertional dyspnoea for the past three years, which increased over 6 months. Chest high-resolution computed tomography (HRCT) was suggestive of non-fibrotic hypersensitivity pneumonitis. Hence the patient was started on systemic steroids, with which the patient’s oxygen saturation improved. On 2D-ECHO, the right ventricle systolic pressure was 48+RAP. Right heart catheterization showed mean pulmonary artery pressure of 73 mmHG, PVR 8.7. On further evaluation, CTPA was done, which surprisingly revealed the left superior pulmonary vein draining into the left brachiocephalic vein. https://www.monaldi-archives.org/index.php/macd/article/view/2497Partial anomalous pulmonary venous connectionnon-fibrotic hypersensitivity pneumonitispulmonary hypertension |
| spellingShingle | Pratap Upadhya Shivam Garg Jeevanandham A. Nesamani Daniel Ponraj Ahmed Wayez An unexpected and unusual cause of pulmonary hypertension in a patient with hypersensitivity pneumonitis: partial anomalous pulmonary venous connection causing pulmonary artery hypertension Monaldi Archives for Chest Disease Partial anomalous pulmonary venous connection non-fibrotic hypersensitivity pneumonitis pulmonary hypertension |
| title | An unexpected and unusual cause of pulmonary hypertension in a patient with hypersensitivity pneumonitis: partial anomalous pulmonary venous connection causing pulmonary artery hypertension |
| title_full | An unexpected and unusual cause of pulmonary hypertension in a patient with hypersensitivity pneumonitis: partial anomalous pulmonary venous connection causing pulmonary artery hypertension |
| title_fullStr | An unexpected and unusual cause of pulmonary hypertension in a patient with hypersensitivity pneumonitis: partial anomalous pulmonary venous connection causing pulmonary artery hypertension |
| title_full_unstemmed | An unexpected and unusual cause of pulmonary hypertension in a patient with hypersensitivity pneumonitis: partial anomalous pulmonary venous connection causing pulmonary artery hypertension |
| title_short | An unexpected and unusual cause of pulmonary hypertension in a patient with hypersensitivity pneumonitis: partial anomalous pulmonary venous connection causing pulmonary artery hypertension |
| title_sort | unexpected and unusual cause of pulmonary hypertension in a patient with hypersensitivity pneumonitis partial anomalous pulmonary venous connection causing pulmonary artery hypertension |
| topic | Partial anomalous pulmonary venous connection non-fibrotic hypersensitivity pneumonitis pulmonary hypertension |
| url | https://www.monaldi-archives.org/index.php/macd/article/view/2497 |
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