Scrotal fibrous hamartoma of infancy: A case report and literature review of a rare tumor of the genitourinary tract

Fibrous hamartoma of infancy (FHI) is a rare, benign soft tissue lesion observed in infants characterized histologically by triphasic appearance of bland fibroblastic fascicles, mature adipose tissue, and nodules of primitive myxoid mesenchyme. Preoperative and intraoperative recognition of FHI pres...

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Main Authors: Savannah Starr, Neil Mendhiratta, Paul J. Iskander, Huihui Ye, Renea Sturm
Format: Article
Language:English
Published: Elsevier 2022-11-01
Series:Urology Case Reports
Subjects:
Online Access:http://www.sciencedirect.com/science/article/pii/S2214442022002303
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author Savannah Starr
Neil Mendhiratta
Paul J. Iskander
Huihui Ye
Renea Sturm
author_facet Savannah Starr
Neil Mendhiratta
Paul J. Iskander
Huihui Ye
Renea Sturm
author_sort Savannah Starr
collection DOAJ
description Fibrous hamartoma of infancy (FHI) is a rare, benign soft tissue lesion observed in infants characterized histologically by triphasic appearance of bland fibroblastic fascicles, mature adipose tissue, and nodules of primitive myxoid mesenchyme. Preoperative and intraoperative recognition of FHI presents a significant diagnostic challenge due to nonspecific imaging findings and its histologic similarities to alternate benign and malignant entities. Management requires complete local excision and clinical follow-up to monitor for recurrence. Here, we present the diagnosis, management, and two-year follow-up of a 13-month-old boy with a scrotal FHI in addition to a comprehensive literature review of this entity.
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spelling doaj.art-755893a5142849078b26ee39f71b37f82022-12-22T02:48:44ZengElsevierUrology Case Reports2214-44202022-11-0145102218Scrotal fibrous hamartoma of infancy: A case report and literature review of a rare tumor of the genitourinary tractSavannah Starr0Neil Mendhiratta1Paul J. Iskander2Huihui Ye3Renea Sturm4Department of Urology, University of California Los Angeles, USADepartment of Urology, University of California Los Angeles, USADepartment of Radiology, University of California Los Angeles, USADepartment of Pathology, University of California Los Angeles, USADepartment of Urology, University of California Los Angeles, USA; Corresponding author. Department of Urology, Division of Pediatric Urology, 200 Westwood Plaza, #140, Los Angeles, CA, 90095, USA.Fibrous hamartoma of infancy (FHI) is a rare, benign soft tissue lesion observed in infants characterized histologically by triphasic appearance of bland fibroblastic fascicles, mature adipose tissue, and nodules of primitive myxoid mesenchyme. Preoperative and intraoperative recognition of FHI presents a significant diagnostic challenge due to nonspecific imaging findings and its histologic similarities to alternate benign and malignant entities. Management requires complete local excision and clinical follow-up to monitor for recurrence. Here, we present the diagnosis, management, and two-year follow-up of a 13-month-old boy with a scrotal FHI in addition to a comprehensive literature review of this entity.http://www.sciencedirect.com/science/article/pii/S2214442022002303Fibrous hamartoma of infancyPediatric testicular tumorsParatesticular tumorsGenitourinary tract
spellingShingle Savannah Starr
Neil Mendhiratta
Paul J. Iskander
Huihui Ye
Renea Sturm
Scrotal fibrous hamartoma of infancy: A case report and literature review of a rare tumor of the genitourinary tract
Urology Case Reports
Fibrous hamartoma of infancy
Pediatric testicular tumors
Paratesticular tumors
Genitourinary tract
title Scrotal fibrous hamartoma of infancy: A case report and literature review of a rare tumor of the genitourinary tract
title_full Scrotal fibrous hamartoma of infancy: A case report and literature review of a rare tumor of the genitourinary tract
title_fullStr Scrotal fibrous hamartoma of infancy: A case report and literature review of a rare tumor of the genitourinary tract
title_full_unstemmed Scrotal fibrous hamartoma of infancy: A case report and literature review of a rare tumor of the genitourinary tract
title_short Scrotal fibrous hamartoma of infancy: A case report and literature review of a rare tumor of the genitourinary tract
title_sort scrotal fibrous hamartoma of infancy a case report and literature review of a rare tumor of the genitourinary tract
topic Fibrous hamartoma of infancy
Pediatric testicular tumors
Paratesticular tumors
Genitourinary tract
url http://www.sciencedirect.com/science/article/pii/S2214442022002303
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