Scrotal fibrous hamartoma of infancy: A case report and literature review of a rare tumor of the genitourinary tract
Fibrous hamartoma of infancy (FHI) is a rare, benign soft tissue lesion observed in infants characterized histologically by triphasic appearance of bland fibroblastic fascicles, mature adipose tissue, and nodules of primitive myxoid mesenchyme. Preoperative and intraoperative recognition of FHI pres...
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Format: | Article |
Language: | English |
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Elsevier
2022-11-01
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Series: | Urology Case Reports |
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Online Access: | http://www.sciencedirect.com/science/article/pii/S2214442022002303 |
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author | Savannah Starr Neil Mendhiratta Paul J. Iskander Huihui Ye Renea Sturm |
author_facet | Savannah Starr Neil Mendhiratta Paul J. Iskander Huihui Ye Renea Sturm |
author_sort | Savannah Starr |
collection | DOAJ |
description | Fibrous hamartoma of infancy (FHI) is a rare, benign soft tissue lesion observed in infants characterized histologically by triphasic appearance of bland fibroblastic fascicles, mature adipose tissue, and nodules of primitive myxoid mesenchyme. Preoperative and intraoperative recognition of FHI presents a significant diagnostic challenge due to nonspecific imaging findings and its histologic similarities to alternate benign and malignant entities. Management requires complete local excision and clinical follow-up to monitor for recurrence. Here, we present the diagnosis, management, and two-year follow-up of a 13-month-old boy with a scrotal FHI in addition to a comprehensive literature review of this entity. |
first_indexed | 2024-04-13T11:24:26Z |
format | Article |
id | doaj.art-755893a5142849078b26ee39f71b37f8 |
institution | Directory Open Access Journal |
issn | 2214-4420 |
language | English |
last_indexed | 2024-04-13T11:24:26Z |
publishDate | 2022-11-01 |
publisher | Elsevier |
record_format | Article |
series | Urology Case Reports |
spelling | doaj.art-755893a5142849078b26ee39f71b37f82022-12-22T02:48:44ZengElsevierUrology Case Reports2214-44202022-11-0145102218Scrotal fibrous hamartoma of infancy: A case report and literature review of a rare tumor of the genitourinary tractSavannah Starr0Neil Mendhiratta1Paul J. Iskander2Huihui Ye3Renea Sturm4Department of Urology, University of California Los Angeles, USADepartment of Urology, University of California Los Angeles, USADepartment of Radiology, University of California Los Angeles, USADepartment of Pathology, University of California Los Angeles, USADepartment of Urology, University of California Los Angeles, USA; Corresponding author. Department of Urology, Division of Pediatric Urology, 200 Westwood Plaza, #140, Los Angeles, CA, 90095, USA.Fibrous hamartoma of infancy (FHI) is a rare, benign soft tissue lesion observed in infants characterized histologically by triphasic appearance of bland fibroblastic fascicles, mature adipose tissue, and nodules of primitive myxoid mesenchyme. Preoperative and intraoperative recognition of FHI presents a significant diagnostic challenge due to nonspecific imaging findings and its histologic similarities to alternate benign and malignant entities. Management requires complete local excision and clinical follow-up to monitor for recurrence. Here, we present the diagnosis, management, and two-year follow-up of a 13-month-old boy with a scrotal FHI in addition to a comprehensive literature review of this entity.http://www.sciencedirect.com/science/article/pii/S2214442022002303Fibrous hamartoma of infancyPediatric testicular tumorsParatesticular tumorsGenitourinary tract |
spellingShingle | Savannah Starr Neil Mendhiratta Paul J. Iskander Huihui Ye Renea Sturm Scrotal fibrous hamartoma of infancy: A case report and literature review of a rare tumor of the genitourinary tract Urology Case Reports Fibrous hamartoma of infancy Pediatric testicular tumors Paratesticular tumors Genitourinary tract |
title | Scrotal fibrous hamartoma of infancy: A case report and literature review of a rare tumor of the genitourinary tract |
title_full | Scrotal fibrous hamartoma of infancy: A case report and literature review of a rare tumor of the genitourinary tract |
title_fullStr | Scrotal fibrous hamartoma of infancy: A case report and literature review of a rare tumor of the genitourinary tract |
title_full_unstemmed | Scrotal fibrous hamartoma of infancy: A case report and literature review of a rare tumor of the genitourinary tract |
title_short | Scrotal fibrous hamartoma of infancy: A case report and literature review of a rare tumor of the genitourinary tract |
title_sort | scrotal fibrous hamartoma of infancy a case report and literature review of a rare tumor of the genitourinary tract |
topic | Fibrous hamartoma of infancy Pediatric testicular tumors Paratesticular tumors Genitourinary tract |
url | http://www.sciencedirect.com/science/article/pii/S2214442022002303 |
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