Congenital Afibrinogenemia: Anaesthetic Implications of a Rare Inherited Coagulation Disorder
Congenital afibrinogenemia is a very rare inherited bleeding disorder that results from fibrinogen deficiency and is associated with bleeding manifestations of varying severity. A 21 Year-old, diagnosed case of congenital afibrinogenemia, was admitted to the hospital with blunt injury to both the ey...
| Main Authors: | , |
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| Format: | Article |
| Language: | English |
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Wolters Kluwer Medknow Publications
2015-10-01
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| Series: | The Indian Anaesthetists' Forum |
| Subjects: | |
| Online Access: | http://theiaforum.org/article/Congenital Afibrinogenemia: Anaesthetic Implications of a Rare Inherited Coagulation Disorder |
| _version_ | 1818421147734114304 |
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| author | Archana Kalaichelvam Jui Lagoo |
| author_facet | Archana Kalaichelvam Jui Lagoo |
| author_sort | Archana Kalaichelvam |
| collection | DOAJ |
| description | Congenital afibrinogenemia is a very rare inherited bleeding disorder that results from fibrinogen deficiency and is associated with bleeding manifestations of varying severity. A 21 Year-old, diagnosed case of congenital afibrinogenemia, was admitted to the hospital with blunt injury to both the eyes. He was posted for right eye enucleation. Main modality of treatment during bleeding episodes is transfusion of fibrinogen. Alternatively, cryoprecipitate can also be used for minor bleeding episodes or to maintain a base line fibrinogen level. Team work involving haematologists, surgeons and anaesthetist is needed for good pre-operative preparation, to form a protocol for intraoperative management and for optimum post-operative care. It is mandatory to arrange blood and blood products even for minor surgeries in view of the possibility of excessive blood loss. |
| first_indexed | 2024-12-14T13:05:44Z |
| format | Article |
| id | doaj.art-77141ff39c204173bf6a375fec51a691 |
| institution | Directory Open Access Journal |
| issn | 0973-0311 |
| language | English |
| last_indexed | 2024-12-14T13:05:44Z |
| publishDate | 2015-10-01 |
| publisher | Wolters Kluwer Medknow Publications |
| record_format | Article |
| series | The Indian Anaesthetists' Forum |
| spelling | doaj.art-77141ff39c204173bf6a375fec51a6912022-12-21T23:00:19ZengWolters Kluwer Medknow PublicationsThe Indian Anaesthetists' Forum0973-03112015-10-01162014Congenital Afibrinogenemia: Anaesthetic Implications of a Rare Inherited Coagulation DisorderArchana Kalaichelvam0Jui Lagoo1St. John’s Medical College and Hospital BengaluruSt. John’s Medical College and Hospital BengaluruCongenital afibrinogenemia is a very rare inherited bleeding disorder that results from fibrinogen deficiency and is associated with bleeding manifestations of varying severity. A 21 Year-old, diagnosed case of congenital afibrinogenemia, was admitted to the hospital with blunt injury to both the eyes. He was posted for right eye enucleation. Main modality of treatment during bleeding episodes is transfusion of fibrinogen. Alternatively, cryoprecipitate can also be used for minor bleeding episodes or to maintain a base line fibrinogen level. Team work involving haematologists, surgeons and anaesthetist is needed for good pre-operative preparation, to form a protocol for intraoperative management and for optimum post-operative care. It is mandatory to arrange blood and blood products even for minor surgeries in view of the possibility of excessive blood loss.http://theiaforum.org/article/Congenital Afibrinogenemia: Anaesthetic Implications of a Rare Inherited Coagulation Disordercongenital afibrinogenemiafibrinogencryoprecipitateanesthesia |
| spellingShingle | Archana Kalaichelvam Jui Lagoo Congenital Afibrinogenemia: Anaesthetic Implications of a Rare Inherited Coagulation Disorder The Indian Anaesthetists' Forum congenital afibrinogenemia fibrinogen cryoprecipitate anesthesia |
| title | Congenital Afibrinogenemia: Anaesthetic Implications of a Rare Inherited Coagulation Disorder |
| title_full | Congenital Afibrinogenemia: Anaesthetic Implications of a Rare Inherited Coagulation Disorder |
| title_fullStr | Congenital Afibrinogenemia: Anaesthetic Implications of a Rare Inherited Coagulation Disorder |
| title_full_unstemmed | Congenital Afibrinogenemia: Anaesthetic Implications of a Rare Inherited Coagulation Disorder |
| title_short | Congenital Afibrinogenemia: Anaesthetic Implications of a Rare Inherited Coagulation Disorder |
| title_sort | congenital afibrinogenemia anaesthetic implications of a rare inherited coagulation disorder |
| topic | congenital afibrinogenemia fibrinogen cryoprecipitate anesthesia |
| url | http://theiaforum.org/article/Congenital Afibrinogenemia: Anaesthetic Implications of a Rare Inherited Coagulation Disorder |
| work_keys_str_mv | AT archanakalaichelvam congenitalafibrinogenemiaanaestheticimplicationsofarareinheritedcoagulationdisorder AT juilagoo congenitalafibrinogenemiaanaestheticimplicationsofarareinheritedcoagulationdisorder |