Prosthetic rehabilitation of an adolescent with hypohidrotic ectodermal dysplasia with partial anodontia: Case report
Ectodermal dysplasia is a hereditary syndrome characterized by dysplasia of tissues of ectodermal origin (hair, skin, nails, and teeth) and occasionally, dysplasia of mesodermally derived tissues. The triad of nail dystrophy (onychodysplasia), alopecia, or hypotrichosis (scanty, fine, light hair on...
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| Format: | Article |
| Language: | English |
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Wolters Kluwer Medknow Publications
2008-01-01
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| Series: | Journal of Indian Society of Pedodontics and Preventive Dentistry |
| Subjects: | |
| Online Access: | http://www.jisppd.com/article.asp?issn=0970-4388;year=2008;volume=26;issue=4;spage=177;epage=181;aulast=Kaul |
| _version_ | 1818063727915696128 |
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| author | Kaul S Reddy R |
| author_facet | Kaul S Reddy R |
| author_sort | Kaul S |
| collection | DOAJ |
| description | Ectodermal dysplasia is a hereditary syndrome characterized by dysplasia of tissues of ectodermal origin (hair, skin, nails, and teeth) and occasionally, dysplasia of mesodermally derived tissues. The triad of nail dystrophy (onychodysplasia), alopecia, or hypotrichosis (scanty, fine, light hair on the scalp and eyebrows) and palmoplantar hypohidrosis is usually accompanied by lack of sweat glands and partial or complete absence of primary and permanent dentition. Hypohidrotic ectodermal dysplasia usually has an X-linked inheritance and affects only males severely, while female heterozygotes show only minor defects. The clinical management of children with ectodermal dysplasia provides a unique opportunity for cooperative effort between the pedodontist and the prosthodontist. The following case report discusses the management of a young boy with hypohidrotic ectodermal dysplasia. Removable prostheses were employed in the treatment. The aim was to rehabilitate the adolescent prosthodontically and boost him psychologically. |
| first_indexed | 2024-12-10T14:24:42Z |
| format | Article |
| id | doaj.art-77a540c1774d4df0800a52bbf21984c1 |
| institution | Directory Open Access Journal |
| issn | 0970-4388 |
| language | English |
| last_indexed | 2024-12-10T14:24:42Z |
| publishDate | 2008-01-01 |
| publisher | Wolters Kluwer Medknow Publications |
| record_format | Article |
| series | Journal of Indian Society of Pedodontics and Preventive Dentistry |
| spelling | doaj.art-77a540c1774d4df0800a52bbf21984c12022-12-22T01:45:06ZengWolters Kluwer Medknow PublicationsJournal of Indian Society of Pedodontics and Preventive Dentistry0970-43882008-01-01264177181Prosthetic rehabilitation of an adolescent with hypohidrotic ectodermal dysplasia with partial anodontia: Case reportKaul SReddy REctodermal dysplasia is a hereditary syndrome characterized by dysplasia of tissues of ectodermal origin (hair, skin, nails, and teeth) and occasionally, dysplasia of mesodermally derived tissues. The triad of nail dystrophy (onychodysplasia), alopecia, or hypotrichosis (scanty, fine, light hair on the scalp and eyebrows) and palmoplantar hypohidrosis is usually accompanied by lack of sweat glands and partial or complete absence of primary and permanent dentition. Hypohidrotic ectodermal dysplasia usually has an X-linked inheritance and affects only males severely, while female heterozygotes show only minor defects. The clinical management of children with ectodermal dysplasia provides a unique opportunity for cooperative effort between the pedodontist and the prosthodontist. The following case report discusses the management of a young boy with hypohidrotic ectodermal dysplasia. Removable prostheses were employed in the treatment. The aim was to rehabilitate the adolescent prosthodontically and boost him psychologically.http://www.jisppd.com/article.asp?issn=0970-4388;year=2008;volume=26;issue=4;spage=177;epage=181;aulast=KaulHypohidrotic ectodermal dysplasiapartial anodontiaprosthetic therapy |
| spellingShingle | Kaul S Reddy R Prosthetic rehabilitation of an adolescent with hypohidrotic ectodermal dysplasia with partial anodontia: Case report Journal of Indian Society of Pedodontics and Preventive Dentistry Hypohidrotic ectodermal dysplasia partial anodontia prosthetic therapy |
| title | Prosthetic rehabilitation of an adolescent with hypohidrotic ectodermal dysplasia with partial anodontia: Case report |
| title_full | Prosthetic rehabilitation of an adolescent with hypohidrotic ectodermal dysplasia with partial anodontia: Case report |
| title_fullStr | Prosthetic rehabilitation of an adolescent with hypohidrotic ectodermal dysplasia with partial anodontia: Case report |
| title_full_unstemmed | Prosthetic rehabilitation of an adolescent with hypohidrotic ectodermal dysplasia with partial anodontia: Case report |
| title_short | Prosthetic rehabilitation of an adolescent with hypohidrotic ectodermal dysplasia with partial anodontia: Case report |
| title_sort | prosthetic rehabilitation of an adolescent with hypohidrotic ectodermal dysplasia with partial anodontia case report |
| topic | Hypohidrotic ectodermal dysplasia partial anodontia prosthetic therapy |
| url | http://www.jisppd.com/article.asp?issn=0970-4388;year=2008;volume=26;issue=4;spage=177;epage=181;aulast=Kaul |
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