Diagnostic lacunae and implications of an automated implantable cardioverter defibrillator implantation in a child with type 3 Long QT (LQT3) syndrome
A diagnosis of congenital long QT interval syndrome based on history and electrocardiogram was made in a child in the absence of readily available genetic testing. A genotype 3 (LQT3) was suspected after exclusion of other variants as the child was non-responsive to beta-blocker and sodium channel b...
| Main Authors: | , , , |
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| Format: | Article |
| Language: | English |
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Wolters Kluwer Medknow Publications
2022-01-01
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| Series: | Annals of Cardiac Anaesthesia |
| Subjects: | |
| Online Access: | http://www.annals.in/article.asp?issn=0971-9784;year=2022;volume=25;issue=2;spage=210;epage=213;aulast=Maddali |
| _version_ | 1828364012257017856 |
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| author | Madan M Maddali Pranav S Kandachar Ismail A Al-Abri Mohammed I Al-Yamani |
| author_facet | Madan M Maddali Pranav S Kandachar Ismail A Al-Abri Mohammed I Al-Yamani |
| author_sort | Madan M Maddali |
| collection | DOAJ |
| description | A diagnosis of congenital long QT interval syndrome based on history and electrocardiogram was made in a child in the absence of readily available genetic testing. A genotype 3 (LQT3) was suspected after exclusion of other variants as the child was non-responsive to beta-blocker and sodium channel blocker medication. As the child continues to show episodic bradycardia, polymorphic ventricular ectopy, and T-wave alternans, a single-chamber automated implantable cardioverter-defibrillator implantation was done successfully. This report highlights how the diagnosis of LQT3 was arrived at as well as the anesthetic challenges in the management of patients with LQTS. |
| first_indexed | 2024-04-14T05:09:49Z |
| format | Article |
| id | doaj.art-780c471ebfce4a9384d2ae06fa539ccf |
| institution | Directory Open Access Journal |
| issn | 0971-9784 |
| language | English |
| last_indexed | 2024-04-14T05:09:49Z |
| publishDate | 2022-01-01 |
| publisher | Wolters Kluwer Medknow Publications |
| record_format | Article |
| series | Annals of Cardiac Anaesthesia |
| spelling | doaj.art-780c471ebfce4a9384d2ae06fa539ccf2022-12-22T02:10:36ZengWolters Kluwer Medknow PublicationsAnnals of Cardiac Anaesthesia0971-97842022-01-0125221021310.4103/aca.aca_13_21Diagnostic lacunae and implications of an automated implantable cardioverter defibrillator implantation in a child with type 3 Long QT (LQT3) syndromeMadan M MaddaliPranav S KandacharIsmail A Al-AbriMohammed I Al-YamaniA diagnosis of congenital long QT interval syndrome based on history and electrocardiogram was made in a child in the absence of readily available genetic testing. A genotype 3 (LQT3) was suspected after exclusion of other variants as the child was non-responsive to beta-blocker and sodium channel blocker medication. As the child continues to show episodic bradycardia, polymorphic ventricular ectopy, and T-wave alternans, a single-chamber automated implantable cardioverter-defibrillator implantation was done successfully. This report highlights how the diagnosis of LQT3 was arrived at as well as the anesthetic challenges in the management of patients with LQTS.http://www.annals.in/article.asp?issn=0971-9784;year=2022;volume=25;issue=2;spage=210;epage=213;aulast=Maddalianti-arrhythmia agents/administration and dosagedefibrillatorselectrocardiographyimplantablelong qt syndrome/diagnosislong qt syndrome/drug therapyvoltage-gated sodium channel blockers/administration and dosage |
| spellingShingle | Madan M Maddali Pranav S Kandachar Ismail A Al-Abri Mohammed I Al-Yamani Diagnostic lacunae and implications of an automated implantable cardioverter defibrillator implantation in a child with type 3 Long QT (LQT3) syndrome Annals of Cardiac Anaesthesia anti-arrhythmia agents/administration and dosage defibrillators electrocardiography implantable long qt syndrome/diagnosis long qt syndrome/drug therapy voltage-gated sodium channel blockers/administration and dosage |
| title | Diagnostic lacunae and implications of an automated implantable cardioverter defibrillator implantation in a child with type 3 Long QT (LQT3) syndrome |
| title_full | Diagnostic lacunae and implications of an automated implantable cardioverter defibrillator implantation in a child with type 3 Long QT (LQT3) syndrome |
| title_fullStr | Diagnostic lacunae and implications of an automated implantable cardioverter defibrillator implantation in a child with type 3 Long QT (LQT3) syndrome |
| title_full_unstemmed | Diagnostic lacunae and implications of an automated implantable cardioverter defibrillator implantation in a child with type 3 Long QT (LQT3) syndrome |
| title_short | Diagnostic lacunae and implications of an automated implantable cardioverter defibrillator implantation in a child with type 3 Long QT (LQT3) syndrome |
| title_sort | diagnostic lacunae and implications of an automated implantable cardioverter defibrillator implantation in a child with type 3 long qt lqt3 syndrome |
| topic | anti-arrhythmia agents/administration and dosage defibrillators electrocardiography implantable long qt syndrome/diagnosis long qt syndrome/drug therapy voltage-gated sodium channel blockers/administration and dosage |
| url | http://www.annals.in/article.asp?issn=0971-9784;year=2022;volume=25;issue=2;spage=210;epage=213;aulast=Maddali |
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