Surgical correction of subaxial kyphosis in a child with type I neurofibromatosis: rare clinical case and literature review

The paper presents a case of rapidly developing severe cervical kyphosis in a 5-year-old child which was the first clinical manifestation of type I neurofibromatosis (NF1). Surgical correction was carried out in two stages with preliminary hardware halo-traction and subsequent reconstruction of...

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Bibliographic Details
Main Authors: Denis B. Malamashin, Mikhail M. Shchelkunov, Maksim A. Krasnikov, Aleksandr Yu. Mushkin
Format: Article
Language:English
Published: Ministry of Health of Russian Federation, Federal State Budgetary Institution "Novosibirsk Research Institute of Traumatology and Orthopaedics n.a. Ya.L. Tsivyan" 2018-06-01
Series:Хирургия позвоночника
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Online Access:https://www.spinesurgery.ru/jour/article/view/1464/1411
Description
Summary:The paper presents a case of rapidly developing severe cervical kyphosis in a 5-year-old child which was the first clinical manifestation of type I neurofibromatosis (NF1). Surgical correction was carried out in two stages with preliminary hardware halo-traction and subsequent reconstruction of the spine using titanium mesh cage with bone autograft and posterior instrumentation. The deformity was corrected from the magnitude of 79° to the restoration of physiological lordosis. Long-term results were followed-up for 2.5 years with full mainte- nance of the achieved deformity correction. A 15-year literature review on the cervical spine lesions in NF1 is presented.
ISSN:1810-8997
2313-1497