Doença de Moyamoya. Clínica, diagnóstico, novas terapêuticas.
Moyamoya disease is a chronic cerebral vasculopathy that leads to a slow progressive narrowing and occlusion of the principal arteries responsible for the anterior circulation of the brain. It causes a cerebrovascular insufficiency with the development of multiple anastomoses between internal and ex...
| Main Authors: | , |
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| Format: | Article |
| Language: | English |
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Ordem dos Médicos
1997-05-01
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| Series: | Acta Médica Portuguesa |
| Online Access: | https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/2425 |
| _version_ | 1817981305207390208 |
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| author | A L Gomes H Loreto |
| author_facet | A L Gomes H Loreto |
| author_sort | A L Gomes |
| collection | DOAJ |
| description | Moyamoya disease is a chronic cerebral vasculopathy that leads to a slow progressive narrowing and occlusion of the principal arteries responsible for the anterior circulation of the brain. It causes a cerebrovascular insufficiency with the development of multiple anastomoses between internal and external carotid arteries. The diagnosis is based on the peculiar appearance in angiography. Although rare, it is not possible to omit it in the differential diagnosis of ischemic vascular accidents in children. The authors describe a case of a eight year old female caucasian whose diagnosis was suspected by means of the non invasive technique of angiographic magnetic resonance imaging and confirmed by angiography. Based on this case, the main aspects of the disease are described, with particular emphasis on clinical features, diagnosis and treatment. |
| first_indexed | 2024-04-13T23:05:16Z |
| format | Article |
| id | doaj.art-782704deac95443281bc1df7cc86c7ba |
| institution | Directory Open Access Journal |
| issn | 0870-399X 1646-0758 |
| language | English |
| last_indexed | 2024-04-13T23:05:16Z |
| publishDate | 1997-05-01 |
| publisher | Ordem dos Médicos |
| record_format | Article |
| series | Acta Médica Portuguesa |
| spelling | doaj.art-782704deac95443281bc1df7cc86c7ba2022-12-22T02:25:43ZengOrdem dos MédicosActa Médica Portuguesa0870-399X1646-07581997-05-0110510.20344/amp.2425Doença de Moyamoya. Clínica, diagnóstico, novas terapêuticas.A L Gomes0H LoretoUnidade de Neurologia, Hospital Santa Maria, Lisboa.Moyamoya disease is a chronic cerebral vasculopathy that leads to a slow progressive narrowing and occlusion of the principal arteries responsible for the anterior circulation of the brain. It causes a cerebrovascular insufficiency with the development of multiple anastomoses between internal and external carotid arteries. The diagnosis is based on the peculiar appearance in angiography. Although rare, it is not possible to omit it in the differential diagnosis of ischemic vascular accidents in children. The authors describe a case of a eight year old female caucasian whose diagnosis was suspected by means of the non invasive technique of angiographic magnetic resonance imaging and confirmed by angiography. Based on this case, the main aspects of the disease are described, with particular emphasis on clinical features, diagnosis and treatment.https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/2425 |
| spellingShingle | A L Gomes H Loreto Doença de Moyamoya. Clínica, diagnóstico, novas terapêuticas. Acta Médica Portuguesa |
| title | Doença de Moyamoya. Clínica, diagnóstico, novas terapêuticas. |
| title_full | Doença de Moyamoya. Clínica, diagnóstico, novas terapêuticas. |
| title_fullStr | Doença de Moyamoya. Clínica, diagnóstico, novas terapêuticas. |
| title_full_unstemmed | Doença de Moyamoya. Clínica, diagnóstico, novas terapêuticas. |
| title_short | Doença de Moyamoya. Clínica, diagnóstico, novas terapêuticas. |
| title_sort | doenca de moyamoya clinica diagnostico novas terapeuticas |
| url | https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/2425 |
| work_keys_str_mv | AT algomes doencademoyamoyaclinicadiagnosticonovasterapeuticas AT hloreto doencademoyamoyaclinicadiagnosticonovasterapeuticas |