Herlyn-Werner-Wunderlich Syndrome: A Case Report
Herlyn-Werner-Wunderlich syndrome is a rare congenital malformation of the Mullerian ducts characterized by uterine didelphys with obstructed hemivagina and ipsilateral renal agenesis. Commonly, such patients present with pelvic pain, dysmenorrhea following menarche, and an abdominal mass secondary...
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| Format: | Article |
| Language: | English |
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Nepal Medical Association
2023-12-01
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| Series: | Journal of Nepal Medical Association |
| Subjects: | |
| Online Access: | https://www.jnma.com.np/jnma/index.php/jnma/article/view/8376 |
| _version_ | 1797422710236643328 |
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| author | Deepak Lamichhane Anshu Sutihar Gubeanthrey Janakyraman Rudish Jaz Shrestha Mahbubur Rahman Razeeb |
| author_facet | Deepak Lamichhane Anshu Sutihar Gubeanthrey Janakyraman Rudish Jaz Shrestha Mahbubur Rahman Razeeb |
| author_sort | Deepak Lamichhane |
| collection | DOAJ |
| description |
Herlyn-Werner-Wunderlich syndrome is a rare congenital malformation of the Mullerian ducts characterized by uterine didelphys with obstructed hemivagina and ipsilateral renal agenesis. Commonly, such patients present with pelvic pain, dysmenorrhea following menarche, and an abdominal mass secondary to hematometrocolpos. In this report, a case of a 14-year-old female presented with abdominal pain, back pain and acute urinary retention. She attained menarche at the age of 10 years; however, symptoms of dysmenorrhea only appeared 4 years later. She was eventually diagnosed with the help of ultrasound and computed tomography urogram. She was managed conservatively with an incision and drainage procedure and was also advised for resection of vaginal septum. The nonspecific nature of symptoms such as regular menstruation with cyclical abdominal pain impedes the diagnosis which can lead to an array of complications. Awareness of this syndrome can help avoid misdiagnosis and allow for early surgical intervention.
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| first_indexed | 2024-03-09T07:36:19Z |
| format | Article |
| id | doaj.art-785cde1044fe4eab85d5e8fe2d16c97f |
| institution | Directory Open Access Journal |
| issn | 0028-2715 1815-672X |
| language | English |
| last_indexed | 2024-03-09T07:36:19Z |
| publishDate | 2023-12-01 |
| publisher | Nepal Medical Association |
| record_format | Article |
| series | Journal of Nepal Medical Association |
| spelling | doaj.art-785cde1044fe4eab85d5e8fe2d16c97f2023-12-03T05:37:02ZengNepal Medical AssociationJournal of Nepal Medical Association0028-27151815-672X2023-12-016126810.31729/jnma.8376Herlyn-Werner-Wunderlich Syndrome: A Case ReportDeepak Lamichhane0Anshu Sutihar1Gubeanthrey Janakyraman2Rudish Jaz Shrestha3Mahbubur Rahman Razeeb4Dhaka Medical College, Bakshi Bazar, Dhaka, BangladeshDhaka Medical College, Bakshi Bazar, Dhaka, Bangladesh Dhaka Medical College, Bakshi Bazar, Dhaka, BangladeshDhaka Medical College, Bakshi Bazar, Dhaka, BangladeshDepartment of Obstetrics and Gynaecology, Dhaka Medical College, Bakshi Bazar, Dhaka, Bangladesh Herlyn-Werner-Wunderlich syndrome is a rare congenital malformation of the Mullerian ducts characterized by uterine didelphys with obstructed hemivagina and ipsilateral renal agenesis. Commonly, such patients present with pelvic pain, dysmenorrhea following menarche, and an abdominal mass secondary to hematometrocolpos. In this report, a case of a 14-year-old female presented with abdominal pain, back pain and acute urinary retention. She attained menarche at the age of 10 years; however, symptoms of dysmenorrhea only appeared 4 years later. She was eventually diagnosed with the help of ultrasound and computed tomography urogram. She was managed conservatively with an incision and drainage procedure and was also advised for resection of vaginal septum. The nonspecific nature of symptoms such as regular menstruation with cyclical abdominal pain impedes the diagnosis which can lead to an array of complications. Awareness of this syndrome can help avoid misdiagnosis and allow for early surgical intervention. https://www.jnma.com.np/jnma/index.php/jnma/article/view/8376case reportsdysmenorrheauterine didelphys |
| spellingShingle | Deepak Lamichhane Anshu Sutihar Gubeanthrey Janakyraman Rudish Jaz Shrestha Mahbubur Rahman Razeeb Herlyn-Werner-Wunderlich Syndrome: A Case Report Journal of Nepal Medical Association case reports dysmenorrhea uterine didelphys |
| title | Herlyn-Werner-Wunderlich Syndrome: A Case Report |
| title_full | Herlyn-Werner-Wunderlich Syndrome: A Case Report |
| title_fullStr | Herlyn-Werner-Wunderlich Syndrome: A Case Report |
| title_full_unstemmed | Herlyn-Werner-Wunderlich Syndrome: A Case Report |
| title_short | Herlyn-Werner-Wunderlich Syndrome: A Case Report |
| title_sort | herlyn werner wunderlich syndrome a case report |
| topic | case reports dysmenorrhea uterine didelphys |
| url | https://www.jnma.com.np/jnma/index.php/jnma/article/view/8376 |
| work_keys_str_mv | AT deepaklamichhane herlynwernerwunderlichsyndromeacasereport AT anshusutihar herlynwernerwunderlichsyndromeacasereport AT gubeanthreyjanakyraman herlynwernerwunderlichsyndromeacasereport AT rudishjazshrestha herlynwernerwunderlichsyndromeacasereport AT mahbuburrahmanrazeeb herlynwernerwunderlichsyndromeacasereport |