Hepatic perivascular epithelioid cell tumor: A case report

Perivascular epithelioid cell tumor (PEComa) of liver is extremely rare hepatic neoplasm with only 30 cases reported in the literature. These lesions are found mainly in young females and may present a potential pitfall in the characterisation of focal liver lesions. The biological behavior of PECom...

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Bibliographic Details
Main Authors: Rok Dežman, Dragan Mašulović, Peter Popovič
Format: Article
Language:English
Published: Elsevier 2018-01-01
Series:European Journal of Radiology Open
Online Access:http://www.sciencedirect.com/science/article/pii/S2352047718300807
Description
Summary:Perivascular epithelioid cell tumor (PEComa) of liver is extremely rare hepatic neoplasm with only 30 cases reported in the literature. These lesions are found mainly in young females and may present a potential pitfall in the characterisation of focal liver lesions. The biological behavior of PEComa varies from generally benign to rarely malignant and metastatic disease. We report a case of a patient with hepatic PEComa with the corresponding imaging findings on the ultrasound, contrast-enhanced ultrasound (CEUS) and hepatospecific MRI. After failed attempt to characterize the lesion by percutaneous biopsy, surgical resection was conducted and the final diagnosis was achieved. Keywords: Perivascular epithelioid tumor, PECOM, Focal liver lesion, CEUS, MRI
ISSN:2352-0477