Hepatic perivascular epithelioid cell tumor: A case report

Perivascular epithelioid cell tumor (PEComa) of liver is extremely rare hepatic neoplasm with only 30 cases reported in the literature. These lesions are found mainly in young females and may present a potential pitfall in the characterisation of focal liver lesions. The biological behavior of PECom...

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Main Authors: Rok Dežman, Dragan Mašulović, Peter Popovič
Format: Article
Language:English
Published: Elsevier 2018-01-01
Series:European Journal of Radiology Open
Online Access:http://www.sciencedirect.com/science/article/pii/S2352047718300807
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author Rok Dežman
Dragan Mašulović
Peter Popovič
author_facet Rok Dežman
Dragan Mašulović
Peter Popovič
author_sort Rok Dežman
collection DOAJ
description Perivascular epithelioid cell tumor (PEComa) of liver is extremely rare hepatic neoplasm with only 30 cases reported in the literature. These lesions are found mainly in young females and may present a potential pitfall in the characterisation of focal liver lesions. The biological behavior of PEComa varies from generally benign to rarely malignant and metastatic disease. We report a case of a patient with hepatic PEComa with the corresponding imaging findings on the ultrasound, contrast-enhanced ultrasound (CEUS) and hepatospecific MRI. After failed attempt to characterize the lesion by percutaneous biopsy, surgical resection was conducted and the final diagnosis was achieved. Keywords: Perivascular epithelioid tumor, PECOM, Focal liver lesion, CEUS, MRI
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spelling doaj.art-78f7ec577cb44ef9b9bf51d9859537382022-12-22T01:14:47ZengElsevierEuropean Journal of Radiology Open2352-04772018-01-015121125Hepatic perivascular epithelioid cell tumor: A case reportRok Dežman0Dragan Mašulović1Peter Popovič2University Medical Centre Ljubljana, Clinical Institute of Radiology, Ljubljana, Slovenia; Corresponding author at: University Medical Centre Ljubljana, Clinical Institute of Radiology, Zaloska cesta 7, 1525, Ljubljana, Slovenia.Clinical Centre of Serbia, Centre for Radiology and Magnetic Resonance Imaging, Belgrade, SerbiaUniversity Medical Centre Ljubljana, Clinical Institute of Radiology, Ljubljana, SloveniaPerivascular epithelioid cell tumor (PEComa) of liver is extremely rare hepatic neoplasm with only 30 cases reported in the literature. These lesions are found mainly in young females and may present a potential pitfall in the characterisation of focal liver lesions. The biological behavior of PEComa varies from generally benign to rarely malignant and metastatic disease. We report a case of a patient with hepatic PEComa with the corresponding imaging findings on the ultrasound, contrast-enhanced ultrasound (CEUS) and hepatospecific MRI. After failed attempt to characterize the lesion by percutaneous biopsy, surgical resection was conducted and the final diagnosis was achieved. Keywords: Perivascular epithelioid tumor, PECOM, Focal liver lesion, CEUS, MRIhttp://www.sciencedirect.com/science/article/pii/S2352047718300807
spellingShingle Rok Dežman
Dragan Mašulović
Peter Popovič
Hepatic perivascular epithelioid cell tumor: A case report
European Journal of Radiology Open
title Hepatic perivascular epithelioid cell tumor: A case report
title_full Hepatic perivascular epithelioid cell tumor: A case report
title_fullStr Hepatic perivascular epithelioid cell tumor: A case report
title_full_unstemmed Hepatic perivascular epithelioid cell tumor: A case report
title_short Hepatic perivascular epithelioid cell tumor: A case report
title_sort hepatic perivascular epithelioid cell tumor a case report
url http://www.sciencedirect.com/science/article/pii/S2352047718300807
work_keys_str_mv AT rokdezman hepaticperivascularepithelioidcelltumoracasereport
AT draganmasulovic hepaticperivascularepithelioidcelltumoracasereport
AT peterpopovic hepaticperivascularepithelioidcelltumoracasereport