Indirect revascularization surgery for moyamoya disease in children and its special considerations

Moyamoya disease (MMD) is the most common pediatric cerebrovascular disease in Far Eastern countries. In children, MMD frequently manifests as ischemic symptomatology. Cerebral perfusion gradually decreases as the disease progresses, which often leads to cerebral infarction. The benefits of revascul...

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Main Authors: Kyu-Chang Wang, Ji Hoon Phi, Ji Yeoun Lee, Seung-Ki Kim, Byung-Kyu Cho
Format: Article
Language:English
Published: Korean Pediatric Society 2012-11-01
Series:Korean Journal of Pediatrics
Subjects:
Online Access:http://kjp.or.kr/upload/pdf/kjped-55-408.pdf
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author Kyu-Chang Wang
Ji Hoon Phi
Ji Yeoun Lee
Seung-Ki Kim
Byung-Kyu Cho
author_facet Kyu-Chang Wang
Ji Hoon Phi
Ji Yeoun Lee
Seung-Ki Kim
Byung-Kyu Cho
author_sort Kyu-Chang Wang
collection DOAJ
description Moyamoya disease (MMD) is the most common pediatric cerebrovascular disease in Far Eastern countries. In children, MMD frequently manifests as ischemic symptomatology. Cerebral perfusion gradually decreases as the disease progresses, which often leads to cerebral infarction. The benefits of revascularization surgery, whether direct or indirect, have been well established in MMD patients with ischemic symptoms. In adults, the increase in cerebral blood flow achieved with indirect revascularization is often unsatisfactory, and direct revascularization is usually feasible. In children, however, direct revascularization is frequently technically not feasible, whereas the response to indirect revascularization is excellent, although 1 or 2 weeks are required for stabilization of symptoms. The authors describe surgical procedures and perioperative care in indirect revascularization for MMD. In addition, special considerations with regard to very young patients, patients with recent cerebral infarction, and patients with hyperthyroidism are discussed.
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spelling doaj.art-7941035baac84d2f83dead6d5c6716622022-12-22T01:56:48ZengKorean Pediatric SocietyKorean Journal of Pediatrics1738-10612092-72582012-11-01551140841310.3345/kjp.2012.55.11.4082012600034Indirect revascularization surgery for moyamoya disease in children and its special considerationsKyu-Chang Wang0Ji Hoon Phi1Ji Yeoun Lee2Seung-Ki Kim3Byung-Kyu Cho4Division of Pediatric Neurosurgery, Department of Neurosurgery, Seoul National University Children's Hospital, Seoul, Korea.Division of Pediatric Neurosurgery, Department of Neurosurgery, Seoul National University Children's Hospital, Seoul, Korea.Division of Pediatric Neurosurgery, Department of Neurosurgery, Seoul National University Children's Hospital, Seoul, Korea.Division of Pediatric Neurosurgery, Department of Neurosurgery, Seoul National University Children's Hospital, Seoul, Korea.Division of Pediatric Neurosurgery, Department of Neurosurgery, Seoul National University Children's Hospital, Seoul, Korea.Moyamoya disease (MMD) is the most common pediatric cerebrovascular disease in Far Eastern countries. In children, MMD frequently manifests as ischemic symptomatology. Cerebral perfusion gradually decreases as the disease progresses, which often leads to cerebral infarction. The benefits of revascularization surgery, whether direct or indirect, have been well established in MMD patients with ischemic symptoms. In adults, the increase in cerebral blood flow achieved with indirect revascularization is often unsatisfactory, and direct revascularization is usually feasible. In children, however, direct revascularization is frequently technically not feasible, whereas the response to indirect revascularization is excellent, although 1 or 2 weeks are required for stabilization of symptoms. The authors describe surgical procedures and perioperative care in indirect revascularization for MMD. In addition, special considerations with regard to very young patients, patients with recent cerebral infarction, and patients with hyperthyroidism are discussed.http://kjp.or.kr/upload/pdf/kjped-55-408.pdfMoyamoya diseaseChildSurgery
spellingShingle Kyu-Chang Wang
Ji Hoon Phi
Ji Yeoun Lee
Seung-Ki Kim
Byung-Kyu Cho
Indirect revascularization surgery for moyamoya disease in children and its special considerations
Korean Journal of Pediatrics
Moyamoya disease
Child
Surgery
title Indirect revascularization surgery for moyamoya disease in children and its special considerations
title_full Indirect revascularization surgery for moyamoya disease in children and its special considerations
title_fullStr Indirect revascularization surgery for moyamoya disease in children and its special considerations
title_full_unstemmed Indirect revascularization surgery for moyamoya disease in children and its special considerations
title_short Indirect revascularization surgery for moyamoya disease in children and its special considerations
title_sort indirect revascularization surgery for moyamoya disease in children and its special considerations
topic Moyamoya disease
Child
Surgery
url http://kjp.or.kr/upload/pdf/kjped-55-408.pdf
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