EXOTIC CONGENITAL SCOLIOSIS – THE EFFECTS OF EARLY ARTHRODESIS

Aim. The article presents the difficulties encountered in the treatment of exotic scoliosis and the optimal treatment options for this pathology. Material and method. The case presentation of an exotic scoliosis with T6-T11 vertebral block with hemivertebrae, rib fusions and rib agenesis on the co...

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Main Authors: R.A. Tutunaru, S.T. Gavriliu, S.A. Hamei, C. Simion, D. Vieru, Gh. Popescu
Format: Article
Language:English
Published: Amaltea Medical Publishing House 2018-03-01
Series:Romanian Medical Journal
Subjects:
Online Access:https://revistemedicale.amaltea.ro/Romanian_MEDICAL_Journal/Revista_MEDICALA_ROMANA-2018-Nr.1/RMJ_2018_1_Art-08.pdf
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author R.A. Tutunaru
S.T. Gavriliu
S.A. Hamei
C. Simion
D. Vieru
Gh. Popescu
author_facet R.A. Tutunaru
S.T. Gavriliu
S.A. Hamei
C. Simion
D. Vieru
Gh. Popescu
author_sort R.A. Tutunaru
collection DOAJ
description Aim. The article presents the difficulties encountered in the treatment of exotic scoliosis and the optimal treatment options for this pathology. Material and method. The case presentation of an exotic scoliosis with T6-T11 vertebral block with hemivertebrae, rib fusions and rib agenesis on the concave side, L1-T12 butterfly vertebrae, L2 hemivertebra and lumbar rachischizis, associated with a diastematomyelic bony spur at T12-L1 level, previous operated, requiring surgical reintervention. Results. Surgical decisions not optimized for each patient may lead to worsening of evolution and raise difficulties in later treatment. Discussions. The resection of the hemivertebra and spinal fusion limited to 2 levels is the optimal treatment for congenital scoliosis that corrects the scoliosis curve and stops progression. The VEPTR device is the most effective choice to ensure pulmonary development compatible with life in patients with thoracic insufficiency syndrome. Conclusions. Exotic scoliosis is a challenging pathology that requires prognosis of development in order to be able to choose the optimal treatment to ensure the growth and development of the thoracic cavity, the pulmonary system and the spinal cords.
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spelling doaj.art-79ce1214638a4e5e8eb99b468916ff8e2024-02-02T09:29:47ZengAmaltea Medical Publishing HouseRomanian Medical Journal1220-54782069-606X2018-03-01651454910.37897/RMJ.2018.1.8EXOTIC CONGENITAL SCOLIOSIS – THE EFFECTS OF EARLY ARTHRODESISR.A. Tutunaru0S.T. Gavriliu1S.A. Hamei2C. Simion3D. Vieru4Gh. Popescu5Facultatea de Medicină, Universitatea de Medicină şi Farmacie „Carol Davila“, BucureştiFacultatea de Medicină, Universitatea de Medicină şi Farmacie „Carol Davila“, Bucureşti; Secţia de Ortopedie Pediatrică, Spitalul Clinic de Urgenţă pentru Copii „M.S. Curie“, BucureştiSecţia de Ortopedie Pediatrică, Spitalul Clinic de Urgenţă pentru Copii „M.S. Curie“, BucureştiSecţia de Ortopedie Pediatrică, Spitalul Clinic de Urgenţă pentru Copii „M.S. Curie“, BucureştiSecţia de Ortopedie Pediatrică, Spitalul Clinic de Urgenţă pentru Copii „M.S. Curie“, BucureştiFacultatea de Medicină, Universitatea de Medicină şi Farmacie „Carol Davila“, Bucureşti; Spitalul Clinic de Urgenţă „Floreasca“, BucureştiAim. The article presents the difficulties encountered in the treatment of exotic scoliosis and the optimal treatment options for this pathology. Material and method. The case presentation of an exotic scoliosis with T6-T11 vertebral block with hemivertebrae, rib fusions and rib agenesis on the concave side, L1-T12 butterfly vertebrae, L2 hemivertebra and lumbar rachischizis, associated with a diastematomyelic bony spur at T12-L1 level, previous operated, requiring surgical reintervention. Results. Surgical decisions not optimized for each patient may lead to worsening of evolution and raise difficulties in later treatment. Discussions. The resection of the hemivertebra and spinal fusion limited to 2 levels is the optimal treatment for congenital scoliosis that corrects the scoliosis curve and stops progression. The VEPTR device is the most effective choice to ensure pulmonary development compatible with life in patients with thoracic insufficiency syndrome. Conclusions. Exotic scoliosis is a challenging pathology that requires prognosis of development in order to be able to choose the optimal treatment to ensure the growth and development of the thoracic cavity, the pulmonary system and the spinal cords.https://revistemedicale.amaltea.ro/Romanian_MEDICAL_Journal/Revista_MEDICALA_ROMANA-2018-Nr.1/RMJ_2018_1_Art-08.pdfexotic scoliosishemivertebraediastematomyeliaveptr
spellingShingle R.A. Tutunaru
S.T. Gavriliu
S.A. Hamei
C. Simion
D. Vieru
Gh. Popescu
EXOTIC CONGENITAL SCOLIOSIS – THE EFFECTS OF EARLY ARTHRODESIS
Romanian Medical Journal
exotic scoliosis
hemivertebrae
diastematomyelia
veptr
title EXOTIC CONGENITAL SCOLIOSIS – THE EFFECTS OF EARLY ARTHRODESIS
title_full EXOTIC CONGENITAL SCOLIOSIS – THE EFFECTS OF EARLY ARTHRODESIS
title_fullStr EXOTIC CONGENITAL SCOLIOSIS – THE EFFECTS OF EARLY ARTHRODESIS
title_full_unstemmed EXOTIC CONGENITAL SCOLIOSIS – THE EFFECTS OF EARLY ARTHRODESIS
title_short EXOTIC CONGENITAL SCOLIOSIS – THE EFFECTS OF EARLY ARTHRODESIS
title_sort exotic congenital scoliosis the effects of early arthrodesis
topic exotic scoliosis
hemivertebrae
diastematomyelia
veptr
url https://revistemedicale.amaltea.ro/Romanian_MEDICAL_Journal/Revista_MEDICALA_ROMANA-2018-Nr.1/RMJ_2018_1_Art-08.pdf
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AT sahamei exoticcongenitalscoliosistheeffectsofearlyarthrodesis
AT csimion exoticcongenitalscoliosistheeffectsofearlyarthrodesis
AT dvieru exoticcongenitalscoliosistheeffectsofearlyarthrodesis
AT ghpopescu exoticcongenitalscoliosistheeffectsofearlyarthrodesis