Iatrogenic distal aortic rupture in a patient with vascular Ehlers-Danlos syndrome

Vascular Ehlers-Danlos syndrome is a rare inherited connective tissue disorder that can result in significant morbidity and mortality. This report details an iatrogenic aortic rupture during an endovascular approach in the management of critical limb ischemia in a 27-year-old woman who presented wit...

Full description

Bibliographic Details
Main Authors: Mohammad M. Zagzoog, MD, Sean A. Crawford, MD, Thomas Le Houérou, MD, Antoine Gaudin, MD, Stéphan Haulon, MD, PhD, Dominique Fabre, MD, PhD
Format: Article
Language:English
Published: Elsevier 2023-06-01
Series:Journal of Vascular Surgery Cases and Innovative Techniques
Subjects:
Online Access:http://www.sciencedirect.com/science/article/pii/S2468428723000655
Description
Summary:Vascular Ehlers-Danlos syndrome is a rare inherited connective tissue disorder that can result in significant morbidity and mortality. This report details an iatrogenic aortic rupture during an endovascular approach in the management of critical limb ischemia in a 27-year-old woman who presented with acute onset of severe sensory deficit of the left leg. Conversion to open repair with a midline laparotomy and an aortic-left popliteal bypass was performed. In the endovascular era, we highlight that even minimally invasive therapeutic interventions can have devastating adverse events in patients with vascular Ehlers-Danlos syndrome.
ISSN:2468-4287