Iatrogenic distal aortic rupture in a patient with vascular Ehlers-Danlos syndrome
Vascular Ehlers-Danlos syndrome is a rare inherited connective tissue disorder that can result in significant morbidity and mortality. This report details an iatrogenic aortic rupture during an endovascular approach in the management of critical limb ischemia in a 27-year-old woman who presented wit...
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| Format: | Article |
| Language: | English |
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Elsevier
2023-06-01
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| Series: | Journal of Vascular Surgery Cases and Innovative Techniques |
| Subjects: | |
| Online Access: | http://www.sciencedirect.com/science/article/pii/S2468428723000655 |
| _version_ | 1797797135983312896 |
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| author | Mohammad M. Zagzoog, MD Sean A. Crawford, MD Thomas Le Houérou, MD Antoine Gaudin, MD Stéphan Haulon, MD, PhD Dominique Fabre, MD, PhD |
| author_facet | Mohammad M. Zagzoog, MD Sean A. Crawford, MD Thomas Le Houérou, MD Antoine Gaudin, MD Stéphan Haulon, MD, PhD Dominique Fabre, MD, PhD |
| author_sort | Mohammad M. Zagzoog, MD |
| collection | DOAJ |
| description | Vascular Ehlers-Danlos syndrome is a rare inherited connective tissue disorder that can result in significant morbidity and mortality. This report details an iatrogenic aortic rupture during an endovascular approach in the management of critical limb ischemia in a 27-year-old woman who presented with acute onset of severe sensory deficit of the left leg. Conversion to open repair with a midline laparotomy and an aortic-left popliteal bypass was performed. In the endovascular era, we highlight that even minimally invasive therapeutic interventions can have devastating adverse events in patients with vascular Ehlers-Danlos syndrome. |
| first_indexed | 2024-03-13T03:44:40Z |
| format | Article |
| id | doaj.art-7b9fddea651d4739a5f603ac7770510e |
| institution | Directory Open Access Journal |
| issn | 2468-4287 |
| language | English |
| last_indexed | 2024-03-13T03:44:40Z |
| publishDate | 2023-06-01 |
| publisher | Elsevier |
| record_format | Article |
| series | Journal of Vascular Surgery Cases and Innovative Techniques |
| spelling | doaj.art-7b9fddea651d4739a5f603ac7770510e2023-06-23T04:43:40ZengElsevierJournal of Vascular Surgery Cases and Innovative Techniques2468-42872023-06-0192101156Iatrogenic distal aortic rupture in a patient with vascular Ehlers-Danlos syndromeMohammad M. Zagzoog, MD0Sean A. Crawford, MD1Thomas Le Houérou, MD2Antoine Gaudin, MD3Stéphan Haulon, MD, PhD4Dominique Fabre, MD, PhD5Department of Vascular and Endovascular Surgery, Aortic Center, Marie Lannelongue Hospital, Groupe Hospitalier Paris Saint Joseph, Paris Saclay University, Paris, FrancePeter Munk Cardiac Centre, Toronto General Hospital, University Health Network, Toronto, ON, CanadaDepartment of Vascular and Endovascular Surgery, Aortic Center, Marie Lannelongue Hospital, Groupe Hospitalier Paris Saint Joseph, Paris Saclay University, Paris, FranceDepartment of Vascular and Endovascular Surgery, Aortic Center, Marie Lannelongue Hospital, Groupe Hospitalier Paris Saint Joseph, Paris Saclay University, Paris, FranceDepartment of Vascular and Endovascular Surgery, Aortic Center, Marie Lannelongue Hospital, Groupe Hospitalier Paris Saint Joseph, Paris Saclay University, Paris, FranceDepartment of Vascular and Endovascular Surgery, Aortic Center, Marie Lannelongue Hospital, Groupe Hospitalier Paris Saint Joseph, Paris Saclay University, Paris, France; Correspondence: Dominique Fabre, MD, PhD, Department of Vascular and Endovascular Surgery, Aortic Center, Marie Lannelongue Hospital, Groupe Hospitalier Paris Saint Joseph, Paris Saclay University, 133 Avenue de la Résistance, Le Plessis-Robinson, Paris 92350, FranceVascular Ehlers-Danlos syndrome is a rare inherited connective tissue disorder that can result in significant morbidity and mortality. This report details an iatrogenic aortic rupture during an endovascular approach in the management of critical limb ischemia in a 27-year-old woman who presented with acute onset of severe sensory deficit of the left leg. Conversion to open repair with a midline laparotomy and an aortic-left popliteal bypass was performed. In the endovascular era, we highlight that even minimally invasive therapeutic interventions can have devastating adverse events in patients with vascular Ehlers-Danlos syndrome.http://www.sciencedirect.com/science/article/pii/S2468428723000655Critical limb ischemiaEndovascular proceduresOpen proceduresSpontaneous dissectionVascular Ehlers-Danlos syndromeVascular graft |
| spellingShingle | Mohammad M. Zagzoog, MD Sean A. Crawford, MD Thomas Le Houérou, MD Antoine Gaudin, MD Stéphan Haulon, MD, PhD Dominique Fabre, MD, PhD Iatrogenic distal aortic rupture in a patient with vascular Ehlers-Danlos syndrome Journal of Vascular Surgery Cases and Innovative Techniques Critical limb ischemia Endovascular procedures Open procedures Spontaneous dissection Vascular Ehlers-Danlos syndrome Vascular graft |
| title | Iatrogenic distal aortic rupture in a patient with vascular Ehlers-Danlos syndrome |
| title_full | Iatrogenic distal aortic rupture in a patient with vascular Ehlers-Danlos syndrome |
| title_fullStr | Iatrogenic distal aortic rupture in a patient with vascular Ehlers-Danlos syndrome |
| title_full_unstemmed | Iatrogenic distal aortic rupture in a patient with vascular Ehlers-Danlos syndrome |
| title_short | Iatrogenic distal aortic rupture in a patient with vascular Ehlers-Danlos syndrome |
| title_sort | iatrogenic distal aortic rupture in a patient with vascular ehlers danlos syndrome |
| topic | Critical limb ischemia Endovascular procedures Open procedures Spontaneous dissection Vascular Ehlers-Danlos syndrome Vascular graft |
| url | http://www.sciencedirect.com/science/article/pii/S2468428723000655 |
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