Modified underlying cardiac disease severity in twin-twin transfusion syndrome

Twin-twin transfusion syndrome or related conditions affect fetal loading. We report monochorionic-diamniotic twins. Twin 1 had Ebstein anomaly with mild tricuspid regurgitation (TR) and slightly thickened tricuspid valve leaflets with plastering. Twin 2 had tricuspid valve dysplasia (with abnormal...

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Main Authors: Hirotaka Ishido, Satoshi Masutani, Yukiko Mikami, Kazunori Baba, Michitaka Fuse, Keiko Mizuta, Risa Tanaka, Kenji Sugamoto, Yoichi Iwamoto, Hideaki Senzaki
Format: Article
Language:English
Published: Wolters Kluwer Medknow Publications 2019-01-01
Series:Annals of Pediatric Cardiology
Subjects:
Online Access:http://www.annalspc.com/article.asp?issn=0974-2069;year=2019;volume=12;issue=3;spage=336;epage=338;aulast=
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author Hirotaka Ishido
Satoshi Masutani
Yukiko Mikami
Kazunori Baba
Michitaka Fuse
Keiko Mizuta
Risa Tanaka
Kenji Sugamoto
Yoichi Iwamoto
Hideaki Senzaki
author_facet Hirotaka Ishido
Satoshi Masutani
Yukiko Mikami
Kazunori Baba
Michitaka Fuse
Keiko Mizuta
Risa Tanaka
Kenji Sugamoto
Yoichi Iwamoto
Hideaki Senzaki
author_sort Hirotaka Ishido
collection DOAJ
description Twin-twin transfusion syndrome or related conditions affect fetal loading. We report monochorionic-diamniotic twins. Twin 1 had Ebstein anomaly with mild tricuspid regurgitation (TR) and slightly thickened tricuspid valve leaflets with plastering. Twin 2 had tricuspid valve dysplasia (with abnormal thickening but without plastering) with moderate TR and mild right atrial dilatation. After birth, the severity of TR was greatly reduced in the recipient but increased in the donor. Therefore, intravascular volume change which was due to twin-twin transfusion syndrome seemed to affect the severity of the valvar disease in fetuses. This case suggests that the intrinsic severity of fetal tricuspid valvular disease may be overestimated in the recipient and underestimated in the donor twin. These factors need to be taken into consideration in clinical decision-making.
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spelling doaj.art-7ba8268a10e043718e643c9dc720aab62022-12-21T17:57:30ZengWolters Kluwer Medknow PublicationsAnnals of Pediatric Cardiology0974-20692019-01-0112333633810.4103/apc.APC_112_18Modified underlying cardiac disease severity in twin-twin transfusion syndromeHirotaka IshidoSatoshi MasutaniYukiko MikamiKazunori BabaMichitaka FuseKeiko MizutaRisa TanakaKenji SugamotoYoichi IwamotoHideaki SenzakiTwin-twin transfusion syndrome or related conditions affect fetal loading. We report monochorionic-diamniotic twins. Twin 1 had Ebstein anomaly with mild tricuspid regurgitation (TR) and slightly thickened tricuspid valve leaflets with plastering. Twin 2 had tricuspid valve dysplasia (with abnormal thickening but without plastering) with moderate TR and mild right atrial dilatation. After birth, the severity of TR was greatly reduced in the recipient but increased in the donor. Therefore, intravascular volume change which was due to twin-twin transfusion syndrome seemed to affect the severity of the valvar disease in fetuses. This case suggests that the intrinsic severity of fetal tricuspid valvular disease may be overestimated in the recipient and underestimated in the donor twin. These factors need to be taken into consideration in clinical decision-making.http://www.annalspc.com/article.asp?issn=0974-2069;year=2019;volume=12;issue=3;spage=336;epage=338;aulast=Fetal echocardiographytricuspid insufficiencytwin amniotic fluid discordancetwin-twin transfusion syndrome
spellingShingle Hirotaka Ishido
Satoshi Masutani
Yukiko Mikami
Kazunori Baba
Michitaka Fuse
Keiko Mizuta
Risa Tanaka
Kenji Sugamoto
Yoichi Iwamoto
Hideaki Senzaki
Modified underlying cardiac disease severity in twin-twin transfusion syndrome
Annals of Pediatric Cardiology
Fetal echocardiography
tricuspid insufficiency
twin amniotic fluid discordance
twin-twin transfusion syndrome
title Modified underlying cardiac disease severity in twin-twin transfusion syndrome
title_full Modified underlying cardiac disease severity in twin-twin transfusion syndrome
title_fullStr Modified underlying cardiac disease severity in twin-twin transfusion syndrome
title_full_unstemmed Modified underlying cardiac disease severity in twin-twin transfusion syndrome
title_short Modified underlying cardiac disease severity in twin-twin transfusion syndrome
title_sort modified underlying cardiac disease severity in twin twin transfusion syndrome
topic Fetal echocardiography
tricuspid insufficiency
twin amniotic fluid discordance
twin-twin transfusion syndrome
url http://www.annalspc.com/article.asp?issn=0974-2069;year=2019;volume=12;issue=3;spage=336;epage=338;aulast=
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