Difficult management of an extremely rare case of giant pigmented epithelioid melanocytoma
Pigmented epithelioid melanocytoma (PEM), a heavily pigmented and highly uncommon melanocytic lesion, is extremely rare. It comes under several forms and names. We report the case of a three-year-old boy born with an isolated right lumbopelvic and femoral giant PEM. The boy was unable to walk due to...
| Main Authors: | , , , , , |
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| Format: | Article |
| Language: | English |
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Elsevier
2017-06-01
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| Series: | Journal of Pediatric Surgery Case Reports |
| Subjects: | |
| Online Access: | http://www.sciencedirect.com/science/article/pii/S2213576617300167 |
| _version_ | 1828468446402183168 |
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| author | Mengu Ma Tooh Oumama El Ezzi Samuel Rotman Mirko Dolci Raymond Bossou Anthony de Buys Roessingh, MD, PhD |
| author_facet | Mengu Ma Tooh Oumama El Ezzi Samuel Rotman Mirko Dolci Raymond Bossou Anthony de Buys Roessingh, MD, PhD |
| author_sort | Mengu Ma Tooh |
| collection | DOAJ |
| description | Pigmented epithelioid melanocytoma (PEM), a heavily pigmented and highly uncommon melanocytic lesion, is extremely rare. It comes under several forms and names. We report the case of a three-year-old boy born with an isolated right lumbopelvic and femoral giant PEM. The boy was unable to walk due to the size and the shape of the lesion. He underwent two stages of intra lesional resections, one in Benin and the second in Switzerland. The first surgery was followed by hypothetic hypovolemic and anaphylactic shocks, and the second surgery by a continuous lymphatic leakage from the wounds for months. The strategic management approach, the surgery and follow-up of this case of giant PEM presented a real challenge. |
| first_indexed | 2024-12-11T04:23:21Z |
| format | Article |
| id | doaj.art-7cce64ecb9ad4d19961bfeb7e3abfe52 |
| institution | Directory Open Access Journal |
| issn | 2213-5766 |
| language | English |
| last_indexed | 2024-12-11T04:23:21Z |
| publishDate | 2017-06-01 |
| publisher | Elsevier |
| record_format | Article |
| series | Journal of Pediatric Surgery Case Reports |
| spelling | doaj.art-7cce64ecb9ad4d19961bfeb7e3abfe522022-12-22T01:21:03ZengElsevierJournal of Pediatric Surgery Case Reports2213-57662017-06-0121C192110.1016/j.epsc.2017.04.003Difficult management of an extremely rare case of giant pigmented epithelioid melanocytomaMengu Ma Tooh0Oumama El Ezzi1Samuel Rotman2Mirko Dolci3Raymond Bossou4Anthony de Buys Roessingh, MD, PhD5Department of Pediatric Surgery, University Hospital of Lausanne (CHUV), 1011 Lausanne, SwitzerlandDepartment of Pediatric Surgery, University Hospital of Lausanne (CHUV), 1011 Lausanne, SwitzerlandDepartment of Pathology, CHUV, 1011 Lausanne, SwitzerlandDepartment of Anesthesiology, CHUV, 1011 Lausanne, SwitzerlandDepartment of Pediatrics, Department of Zou and Colline, Abomey, BeninDepartment of Pediatric Surgery, University Hospital of Lausanne (CHUV), 1011 Lausanne, SwitzerlandPigmented epithelioid melanocytoma (PEM), a heavily pigmented and highly uncommon melanocytic lesion, is extremely rare. It comes under several forms and names. We report the case of a three-year-old boy born with an isolated right lumbopelvic and femoral giant PEM. The boy was unable to walk due to the size and the shape of the lesion. He underwent two stages of intra lesional resections, one in Benin and the second in Switzerland. The first surgery was followed by hypothetic hypovolemic and anaphylactic shocks, and the second surgery by a continuous lymphatic leakage from the wounds for months. The strategic management approach, the surgery and follow-up of this case of giant PEM presented a real challenge.http://www.sciencedirect.com/science/article/pii/S2213576617300167Pigmented epithelioid melanocytomaLymphatic leakage |
| spellingShingle | Mengu Ma Tooh Oumama El Ezzi Samuel Rotman Mirko Dolci Raymond Bossou Anthony de Buys Roessingh, MD, PhD Difficult management of an extremely rare case of giant pigmented epithelioid melanocytoma Journal of Pediatric Surgery Case Reports Pigmented epithelioid melanocytoma Lymphatic leakage |
| title | Difficult management of an extremely rare case of giant pigmented epithelioid melanocytoma |
| title_full | Difficult management of an extremely rare case of giant pigmented epithelioid melanocytoma |
| title_fullStr | Difficult management of an extremely rare case of giant pigmented epithelioid melanocytoma |
| title_full_unstemmed | Difficult management of an extremely rare case of giant pigmented epithelioid melanocytoma |
| title_short | Difficult management of an extremely rare case of giant pigmented epithelioid melanocytoma |
| title_sort | difficult management of an extremely rare case of giant pigmented epithelioid melanocytoma |
| topic | Pigmented epithelioid melanocytoma Lymphatic leakage |
| url | http://www.sciencedirect.com/science/article/pii/S2213576617300167 |
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