Patient with Rosai-Dorfman-Destombes disease: 18F-FDG-PET/CT scan as a diagnostic tool

Rosai-Dorfman-Destombes disease (RDD) is a rare non-Langerhans cell histiocytosis, with sinus involvement and massive lymphadenopathy. RDD is usually self-limited; it can appear alone or related to other diseases. We present a 9-year-old male with biopsy of that lesion was taken, giving as result a...

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Main Author: Luis C. Araujo Cachay
Format: Article
Language:English
Published: Colegio Médico del Perú 2023-01-01
Series:Acta Médica Peruana
Subjects:
Online Access:https://amp.cmp.org.pe/index.php/AMP/article/view/2334
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author Luis C. Araujo Cachay
author_facet Luis C. Araujo Cachay
author_sort Luis C. Araujo Cachay
collection DOAJ
description Rosai-Dorfman-Destombes disease (RDD) is a rare non-Langerhans cell histiocytosis, with sinus involvement and massive lymphadenopathy. RDD is usually self-limited; it can appear alone or related to other diseases. We present a 9-year-old male with biopsy of that lesion was taken, giving as result a benign histiocytosis, compatible with RDD. The patient was scanned with full body 18F-FDG PET/CT, the results of the study showed hypermetabolic focal lesions in the sphenoid sinus, ethmoid sinus, and bilateral nasal involvement with hypermetabolic focal injury in the middle third of the left tibia, findings in relation to high-grade expansive injury. The study of 18F-FDG PET/CT demonstrated avid FDG lesions at nodal and extranodal sites, and it also can be used in monitoring and/or evaluating response to treatment.
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spelling doaj.art-7d3fcbdabffd4b04890c1bb0101be1332023-05-09T23:26:39ZengColegio Médico del PerúActa Médica Peruana1018-88001728-59172023-01-0139410.35663/amp.2022.394.23342334Patient with Rosai-Dorfman-Destombes disease: 18F-FDG-PET/CT scan as a diagnostic toolLuis C. Araujo Cachay0Departamento de Medicina Nuclear, Instituto Nacional de Enfermedades Neoplásicas (INEN), Lima-Perú; Facultad de Medicina, Universidad Ricardo Palma, Lima-Perú.Rosai-Dorfman-Destombes disease (RDD) is a rare non-Langerhans cell histiocytosis, with sinus involvement and massive lymphadenopathy. RDD is usually self-limited; it can appear alone or related to other diseases. We present a 9-year-old male with biopsy of that lesion was taken, giving as result a benign histiocytosis, compatible with RDD. The patient was scanned with full body 18F-FDG PET/CT, the results of the study showed hypermetabolic focal lesions in the sphenoid sinus, ethmoid sinus, and bilateral nasal involvement with hypermetabolic focal injury in the middle third of the left tibia, findings in relation to high-grade expansive injury. The study of 18F-FDG PET/CT demonstrated avid FDG lesions at nodal and extranodal sites, and it also can be used in monitoring and/or evaluating response to treatment.https://amp.cmp.org.pe/index.php/AMP/article/view/2334rosai-dorfman diseasepositron emission tomography computed tomographyperu
spellingShingle Luis C. Araujo Cachay
Patient with Rosai-Dorfman-Destombes disease: 18F-FDG-PET/CT scan as a diagnostic tool
Acta Médica Peruana
rosai-dorfman disease
positron emission tomography computed tomography
peru
title Patient with Rosai-Dorfman-Destombes disease: 18F-FDG-PET/CT scan as a diagnostic tool
title_full Patient with Rosai-Dorfman-Destombes disease: 18F-FDG-PET/CT scan as a diagnostic tool
title_fullStr Patient with Rosai-Dorfman-Destombes disease: 18F-FDG-PET/CT scan as a diagnostic tool
title_full_unstemmed Patient with Rosai-Dorfman-Destombes disease: 18F-FDG-PET/CT scan as a diagnostic tool
title_short Patient with Rosai-Dorfman-Destombes disease: 18F-FDG-PET/CT scan as a diagnostic tool
title_sort patient with rosai dorfman destombes disease 18f fdg pet ct scan as a diagnostic tool
topic rosai-dorfman disease
positron emission tomography computed tomography
peru
url https://amp.cmp.org.pe/index.php/AMP/article/view/2334
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