Distinct phenotypes in zebrafish models of human startle disease

Distinct phenotypes in zebrafish models of human startle disease

Startle disease is an inherited neurological disorder that causes affected individuals to suffer noise- or touch-induced non-epileptic seizures, excessive muscle stiffness and neonatal apnea episodes. Mutations known to cause startle disease have been identified in glycine receptor subunit (GLRA1 an...

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Bibliographic Details
Main Authors:	Lisa R. Ganser, Qing Yan, Victoria M. James, Robert Kozol, Maya Topf, Robert J. Harvey, Julia E. Dallman
Format:	Article
Language:	English
Published:	Elsevier 2013-12-01
Series:	Neurobiology of Disease
Subjects:	glra1 glrb Glycine receptor Startle disease Hyperekplexia Zebrafish
Online Access:	http://www.sciencedirect.com/science/article/pii/S0969996113002386

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