Partial anomalous pulmonary venous return: A case series with management approach
Partial anomalous pulmonary venous return (PAPVR) is a rare congenital anomaly that results in a left-to-right shunt. Based on the shunt fraction, PAPVR has a wide spectrum of presentations. If a significant left-to-right shunt is left unrepaired, pulmonary vascular remodeling can occur resulting in...
| Main Authors: | , , , |
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| Format: | Article |
| Language: | English |
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Elsevier
2019-01-01
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| Series: | Respiratory Medicine Case Reports |
| Online Access: | http://www.sciencedirect.com/science/article/pii/S2213007119300139 |
| _version_ | 1818544898763128832 |
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| author | Karim El-Kersh Elie Homsy Curt J. Daniels J. Shaun Smith |
| author_facet | Karim El-Kersh Elie Homsy Curt J. Daniels J. Shaun Smith |
| author_sort | Karim El-Kersh |
| collection | DOAJ |
| description | Partial anomalous pulmonary venous return (PAPVR) is a rare congenital anomaly that results in a left-to-right shunt. Based on the shunt fraction, PAPVR has a wide spectrum of presentations. If a significant left-to-right shunt is left unrepaired, pulmonary vascular remodeling can occur resulting in the development of pulmonary arterial hypertension (PAH). Furthermore, if the condition is associated with an atrial septal defect (ASD), the patient can develop shunt reversal and Eisenmenger's syndrome in setting of severe PAH. Management plans include close observation, surgical repair, and treatment with pulmonary artery vasodilator therapies. Here, we present multiple cases of PAPVR to highlight the wide spectrum of presentations and the individualized treatment for each case. Keywords: PAPVR, PAH, CHD, ASD |
| first_indexed | 2024-12-11T22:54:28Z |
| format | Article |
| id | doaj.art-7dbff863ad6c411c9460674caebf087a |
| institution | Directory Open Access Journal |
| issn | 2213-0071 |
| language | English |
| last_indexed | 2024-12-11T22:54:28Z |
| publishDate | 2019-01-01 |
| publisher | Elsevier |
| record_format | Article |
| series | Respiratory Medicine Case Reports |
| spelling | doaj.art-7dbff863ad6c411c9460674caebf087a2022-12-22T00:47:18ZengElsevierRespiratory Medicine Case Reports2213-00712019-01-0127Partial anomalous pulmonary venous return: A case series with management approachKarim El-Kersh0Elie Homsy1Curt J. Daniels2J. Shaun Smith3Department of Internal Medicine, Division of Pulmonary, Critical Care and Sleep Disorders Medicine, University of Louisville, Louisville, KY, USA; Corresponding author. Department of Medicine, Division of Pulmonary, Critical Care and Sleep Disorders Medicine, Ambulatory Care Building, 550 S. Jackson Street, Louisville, KY, 40202, USA.Department of Internal Medicine, Division of Pulmonary, Critical Care & Sleep Medicine,The Ohio State University Wexner Medical Center, USADepartment of Internal Medicine, Division of Cardiovascular Medicine, The Ohio State University Wexner Medical Center, USA; Department of Pediatrics, Division of Cardiovascular Medicine, Nationwide Children's Hospital, USADepartment of Internal Medicine, Division of Pulmonary, Critical Care & Sleep Medicine,The Ohio State University Wexner Medical Center, USAPartial anomalous pulmonary venous return (PAPVR) is a rare congenital anomaly that results in a left-to-right shunt. Based on the shunt fraction, PAPVR has a wide spectrum of presentations. If a significant left-to-right shunt is left unrepaired, pulmonary vascular remodeling can occur resulting in the development of pulmonary arterial hypertension (PAH). Furthermore, if the condition is associated with an atrial septal defect (ASD), the patient can develop shunt reversal and Eisenmenger's syndrome in setting of severe PAH. Management plans include close observation, surgical repair, and treatment with pulmonary artery vasodilator therapies. Here, we present multiple cases of PAPVR to highlight the wide spectrum of presentations and the individualized treatment for each case. Keywords: PAPVR, PAH, CHD, ASDhttp://www.sciencedirect.com/science/article/pii/S2213007119300139 |
| spellingShingle | Karim El-Kersh Elie Homsy Curt J. Daniels J. Shaun Smith Partial anomalous pulmonary venous return: A case series with management approach Respiratory Medicine Case Reports |
| title | Partial anomalous pulmonary venous return: A case series with management approach |
| title_full | Partial anomalous pulmonary venous return: A case series with management approach |
| title_fullStr | Partial anomalous pulmonary venous return: A case series with management approach |
| title_full_unstemmed | Partial anomalous pulmonary venous return: A case series with management approach |
| title_short | Partial anomalous pulmonary venous return: A case series with management approach |
| title_sort | partial anomalous pulmonary venous return a case series with management approach |
| url | http://www.sciencedirect.com/science/article/pii/S2213007119300139 |
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