Pulmonary valve spindle-cell lipoma: A case report
Primary cardiac tumours are rare and most of them are benign. Myxomas, fibroelastomas and lipomas are common in adults. Primary valvular cardiac tumours are even more rare and affect all four valves in a similar proportion. Valvular lipomas are very rare. In the pulmonary valve there is only one des...
| Main Authors: | , , , , , |
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| Format: | Article |
| Language: | English |
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SAGE Publishing
2023-11-01
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| Series: | SAGE Open Medical Case Reports |
| Online Access: | https://doi.org/10.1177/2050313X231216544 |
| _version_ | 1797447516122251264 |
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| author | Guadalupe Sauchelli-Faas Antonio Barragán-Acea Hugo Álvarez-Argüelles Javier Montoto-López Juan José Jiménez-Rivera Rafael Martínez-Sanz |
| author_facet | Guadalupe Sauchelli-Faas Antonio Barragán-Acea Hugo Álvarez-Argüelles Javier Montoto-López Juan José Jiménez-Rivera Rafael Martínez-Sanz |
| author_sort | Guadalupe Sauchelli-Faas |
| collection | DOAJ |
| description | Primary cardiac tumours are rare and most of them are benign. Myxomas, fibroelastomas and lipomas are common in adults. Primary valvular cardiac tumours are even more rare and affect all four valves in a similar proportion. Valvular lipomas are very rare. In the pulmonary valve there is only one described. Lipomas can be spindle-cell varieties. But of these, there is only one described in a valve, and it is placed in the aortic valve. Pulmonary valve lipomas can produce obstruction to the right ventricular outflow tract as well as pulmonary valve regurgitation, or pulmonary embolism. Symptoms may be dyspnoea, angina, arrhythmias, or syncope. We aim to illustrate with this case report how we came into this very rare pathology, so we present a 54-year-old woman with a giant spindle-cell lipoma located in the anterior pulmonary leaflet and severe dyspnoea. Total resection of the tumour was performed and restoration of valve function was obtained by means of bicuspidization of the remaining pulmonary leaflets. She had a good recovery after surgery and no complication during the postoperative evolution, being discharged from hospital after 7 days from surgery, with echocardiographic control showing good biventricular function, absence of tumour or obstruction, and minimal pulmonary valve regurgitation. |
| first_indexed | 2024-03-09T13:57:08Z |
| format | Article |
| id | doaj.art-7ec691c47d9645a8b12d34f0f0581cbe |
| institution | Directory Open Access Journal |
| issn | 2050-313X |
| language | English |
| last_indexed | 2024-03-09T13:57:08Z |
| publishDate | 2023-11-01 |
| publisher | SAGE Publishing |
| record_format | Article |
| series | SAGE Open Medical Case Reports |
| spelling | doaj.art-7ec691c47d9645a8b12d34f0f0581cbe2023-11-30T13:03:23ZengSAGE PublishingSAGE Open Medical Case Reports2050-313X2023-11-011110.1177/2050313X231216544Pulmonary valve spindle-cell lipoma: A case reportGuadalupe Sauchelli-Faas0Antonio Barragán-Acea1Hugo Álvarez-Argüelles2Javier Montoto-López3Juan José Jiménez-Rivera4Rafael Martínez-Sanz5Cardiovascular Surgery Department, Hospital Universitario de Canarias, Santa Cruz de Tenerife, SpainEchocardiography Unit, Cardiology Department, Hospital Universitario de Canarias, Santa Cruz de Tenerife, SpainPathology Department, Hospital Universitario de Canarias, Universidad de La Laguna, Santa Cruz de Tenerife, SpainCardiovascular Surgery Department, Hospital Universitario de Canarias, Santa Cruz de Tenerife, SpainIntensive Care Unit, Hospital universitario de Canarias, Santa Cruz de Tenerife, SpainCardiovascular Surgery Department, Hospital Universitario de Canarias, Santa Cruz de Tenerife, SpainPrimary cardiac tumours are rare and most of them are benign. Myxomas, fibroelastomas and lipomas are common in adults. Primary valvular cardiac tumours are even more rare and affect all four valves in a similar proportion. Valvular lipomas are very rare. In the pulmonary valve there is only one described. Lipomas can be spindle-cell varieties. But of these, there is only one described in a valve, and it is placed in the aortic valve. Pulmonary valve lipomas can produce obstruction to the right ventricular outflow tract as well as pulmonary valve regurgitation, or pulmonary embolism. Symptoms may be dyspnoea, angina, arrhythmias, or syncope. We aim to illustrate with this case report how we came into this very rare pathology, so we present a 54-year-old woman with a giant spindle-cell lipoma located in the anterior pulmonary leaflet and severe dyspnoea. Total resection of the tumour was performed and restoration of valve function was obtained by means of bicuspidization of the remaining pulmonary leaflets. She had a good recovery after surgery and no complication during the postoperative evolution, being discharged from hospital after 7 days from surgery, with echocardiographic control showing good biventricular function, absence of tumour or obstruction, and minimal pulmonary valve regurgitation.https://doi.org/10.1177/2050313X231216544 |
| spellingShingle | Guadalupe Sauchelli-Faas Antonio Barragán-Acea Hugo Álvarez-Argüelles Javier Montoto-López Juan José Jiménez-Rivera Rafael Martínez-Sanz Pulmonary valve spindle-cell lipoma: A case report SAGE Open Medical Case Reports |
| title | Pulmonary valve spindle-cell lipoma: A case report |
| title_full | Pulmonary valve spindle-cell lipoma: A case report |
| title_fullStr | Pulmonary valve spindle-cell lipoma: A case report |
| title_full_unstemmed | Pulmonary valve spindle-cell lipoma: A case report |
| title_short | Pulmonary valve spindle-cell lipoma: A case report |
| title_sort | pulmonary valve spindle cell lipoma a case report |
| url | https://doi.org/10.1177/2050313X231216544 |
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