Aggressive progressive pleuroparenchymal fibroelastosis developed long after allogenic hematopoietic stem cell transplantation
Key Clinical Message The typical pleuroparenchymal fibroelastosis (PPFE) after hematopoietic stem cell transplantation (HSCT) is characterized by late‐onset progressive pulmonary complication within 5 years. PPFE shows a poor prognosis without definitive standard care other than lung transplantation...
| Main Authors: | , |
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| Format: | Article |
| Language: | English |
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Wiley
2024-01-01
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| Series: | Clinical Case Reports |
| Subjects: | |
| Online Access: | https://doi.org/10.1002/ccr3.8415 |
| _version_ | 1797335004646211584 |
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| author | Osamu Imataki Makiko Uemura |
| author_facet | Osamu Imataki Makiko Uemura |
| author_sort | Osamu Imataki |
| collection | DOAJ |
| description | Key Clinical Message The typical pleuroparenchymal fibroelastosis (PPFE) after hematopoietic stem cell transplantation (HSCT) is characterized by late‐onset progressive pulmonary complication within 5 years. PPFE shows a poor prognosis without definitive standard care other than lung transplantation. Our case indicated an over 20 years late‐onset and aggressively exacerbating PPFE. |
| first_indexed | 2024-03-08T08:30:33Z |
| format | Article |
| id | doaj.art-80a118e5389c44f2b38305d78509380c |
| institution | Directory Open Access Journal |
| issn | 2050-0904 |
| language | English |
| last_indexed | 2024-03-08T08:30:33Z |
| publishDate | 2024-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Clinical Case Reports |
| spelling | doaj.art-80a118e5389c44f2b38305d78509380c2024-02-02T03:36:31ZengWileyClinical Case Reports2050-09042024-01-01121n/an/a10.1002/ccr3.8415Aggressive progressive pleuroparenchymal fibroelastosis developed long after allogenic hematopoietic stem cell transplantationOsamu Imataki0Makiko Uemura1Division of Hematology, Department of Internal Medicine, Faculty of Medicine Kagawa University Takamatsu JapanDivision of Hematology, Department of Internal Medicine, Faculty of Medicine Kagawa University Takamatsu JapanKey Clinical Message The typical pleuroparenchymal fibroelastosis (PPFE) after hematopoietic stem cell transplantation (HSCT) is characterized by late‐onset progressive pulmonary complication within 5 years. PPFE shows a poor prognosis without definitive standard care other than lung transplantation. Our case indicated an over 20 years late‐onset and aggressively exacerbating PPFE.https://doi.org/10.1002/ccr3.8415hematopoietic stem cell transplantation (HSCT)late‐onset noninfectious pulmonary complication (LONIPC)pleuroparenchymal fibroelastosis (PPFE) |
| spellingShingle | Osamu Imataki Makiko Uemura Aggressive progressive pleuroparenchymal fibroelastosis developed long after allogenic hematopoietic stem cell transplantation Clinical Case Reports hematopoietic stem cell transplantation (HSCT) late‐onset noninfectious pulmonary complication (LONIPC) pleuroparenchymal fibroelastosis (PPFE) |
| title | Aggressive progressive pleuroparenchymal fibroelastosis developed long after allogenic hematopoietic stem cell transplantation |
| title_full | Aggressive progressive pleuroparenchymal fibroelastosis developed long after allogenic hematopoietic stem cell transplantation |
| title_fullStr | Aggressive progressive pleuroparenchymal fibroelastosis developed long after allogenic hematopoietic stem cell transplantation |
| title_full_unstemmed | Aggressive progressive pleuroparenchymal fibroelastosis developed long after allogenic hematopoietic stem cell transplantation |
| title_short | Aggressive progressive pleuroparenchymal fibroelastosis developed long after allogenic hematopoietic stem cell transplantation |
| title_sort | aggressive progressive pleuroparenchymal fibroelastosis developed long after allogenic hematopoietic stem cell transplantation |
| topic | hematopoietic stem cell transplantation (HSCT) late‐onset noninfectious pulmonary complication (LONIPC) pleuroparenchymal fibroelastosis (PPFE) |
| url | https://doi.org/10.1002/ccr3.8415 |
| work_keys_str_mv | AT osamuimataki aggressiveprogressivepleuroparenchymalfibroelastosisdevelopedlongafterallogenichematopoieticstemcelltransplantation AT makikouemura aggressiveprogressivepleuroparenchymalfibroelastosisdevelopedlongafterallogenichematopoieticstemcelltransplantation |