Pancreatic Plasmacytoma Misdiagnosed as Neuroendocrine Tumour: A Pathologist’s Dilemma

Extramedullary plasmacytomas are rare, constituting to about 5% of plasma cell neoplasms. Pancreatic involvement is uncommon constituting to about 2.3%. Localised solitary plasmacytomas has a good response to radiation. When they are associated with pre-existing multiple myeloma, their prognosis is...

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Main Authors: Sakthisankari Shanmugasundaram, Umamaheswari Gurusamy, Prasanna N Kumar, Biku Joseph John
Format: Article
Language:English
Published: JCDR Research and Publications Private Limited 2020-02-01
Series:Journal of Clinical and Diagnostic Research
Subjects:
Online Access:https://jcdr.net/articles/PDF/13534/43083_CE[Ra1]_F(KM)_PF1(AG_SHU)_PN(SL).pdf
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author Sakthisankari Shanmugasundaram
Umamaheswari Gurusamy
Prasanna N Kumar
Biku Joseph John
author_facet Sakthisankari Shanmugasundaram
Umamaheswari Gurusamy
Prasanna N Kumar
Biku Joseph John
author_sort Sakthisankari Shanmugasundaram
collection DOAJ
description Extramedullary plasmacytomas are rare, constituting to about 5% of plasma cell neoplasms. Pancreatic involvement is uncommon constituting to about 2.3%. Localised solitary plasmacytomas has a good response to radiation. When they are associated with pre-existing multiple myeloma, their prognosis is poor. A case of plasmacytoma of pancreas presenting with obstructive jaundice preceding plasma cell leukaemia is presented here. The lesion was misdiagnosed by fine needle aspiration cytology as neuroendocrine neoplasm. The patient did not present with symptoms of myeloma initially. The present case highlights the significance of considering other causes of pancreatic mass than primary carcinomas.
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spelling doaj.art-82a4bae1969b4950ba3f46c9aa6620622022-12-22T03:44:30ZengJCDR Research and Publications Private LimitedJournal of Clinical and Diagnostic Research2249-782X0973-709X2020-02-01142ED10ED1210.7860/JCDR/2020/43083.13534Pancreatic Plasmacytoma Misdiagnosed as Neuroendocrine Tumour: A Pathologist’s DilemmaSakthisankari Shanmugasundaram0Umamaheswari Gurusamy1Prasanna N Kumar2Biku Joseph John3Assistant Professor, Department of Pathology, PSG Institute of Medical Sciences and Research, Coimbatore, Tamil Nadu, India.Associate Professor, Department of Pathology, PSG Institute of Medical Sciences and Research, Coimbatore, Tamil Nadu, India.Professor, Department of Pathology, PSG Institute of Medical Sciences and Research, Coimbatore, Tamil Nadu, India.Professor, Department of Hepatobiliary and Pancreatic Surgery, PSG Institute of Medical Sciences and Research, Coimbatore, Tamil Nadu, India.Extramedullary plasmacytomas are rare, constituting to about 5% of plasma cell neoplasms. Pancreatic involvement is uncommon constituting to about 2.3%. Localised solitary plasmacytomas has a good response to radiation. When they are associated with pre-existing multiple myeloma, their prognosis is poor. A case of plasmacytoma of pancreas presenting with obstructive jaundice preceding plasma cell leukaemia is presented here. The lesion was misdiagnosed by fine needle aspiration cytology as neuroendocrine neoplasm. The patient did not present with symptoms of myeloma initially. The present case highlights the significance of considering other causes of pancreatic mass than primary carcinomas.https://jcdr.net/articles/PDF/13534/43083_CE[Ra1]_F(KM)_PF1(AG_SHU)_PN(SL).pdfextramedullary plasmacytomapancreatic neoplasmplasma cell leukaemia
spellingShingle Sakthisankari Shanmugasundaram
Umamaheswari Gurusamy
Prasanna N Kumar
Biku Joseph John
Pancreatic Plasmacytoma Misdiagnosed as Neuroendocrine Tumour: A Pathologist’s Dilemma
Journal of Clinical and Diagnostic Research
extramedullary plasmacytoma
pancreatic neoplasm
plasma cell leukaemia
title Pancreatic Plasmacytoma Misdiagnosed as Neuroendocrine Tumour: A Pathologist’s Dilemma
title_full Pancreatic Plasmacytoma Misdiagnosed as Neuroendocrine Tumour: A Pathologist’s Dilemma
title_fullStr Pancreatic Plasmacytoma Misdiagnosed as Neuroendocrine Tumour: A Pathologist’s Dilemma
title_full_unstemmed Pancreatic Plasmacytoma Misdiagnosed as Neuroendocrine Tumour: A Pathologist’s Dilemma
title_short Pancreatic Plasmacytoma Misdiagnosed as Neuroendocrine Tumour: A Pathologist’s Dilemma
title_sort pancreatic plasmacytoma misdiagnosed as neuroendocrine tumour a pathologist s dilemma
topic extramedullary plasmacytoma
pancreatic neoplasm
plasma cell leukaemia
url https://jcdr.net/articles/PDF/13534/43083_CE[Ra1]_F(KM)_PF1(AG_SHU)_PN(SL).pdf
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