Bullous mastocytosis in a 3-month-old infant
Mastocytosis is a rare myeloid neoplasm characterized by abnormal proliferation and accumulation of mast cells in one or more organ systems including the skin, bone marrow, liver, spleen, lymph nodes and gastrointestinal tract. An infant presenting with bullous lesions is an even rarer clinical pres...
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Format: | Article |
Language: | English |
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Wolters Kluwer Medknow Publications
2014-01-01
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Series: | Indian Dermatology Online Journal |
Subjects: | |
Online Access: | http://www.idoj.in/article.asp?issn=2229-5178;year=2014;volume=5;issue=4;spage=497;epage=500;aulast=Asati |
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author | Dinesh Prasad Asati Anurag Tiwari |
author_facet | Dinesh Prasad Asati Anurag Tiwari |
author_sort | Dinesh Prasad Asati |
collection | DOAJ |
description | Mastocytosis is a rare myeloid neoplasm characterized by abnormal proliferation and accumulation of mast cells in one or more organ systems including the skin, bone marrow, liver, spleen, lymph nodes and gastrointestinal tract. An infant presenting with bullous lesions is an even rarer clinical presentation of cutaneous mastocytosis. The symptoms and complications are mostly in proportion to the mast cell degranulation in tissues. Management is focused on preventing and treating this event. We report a three-month-old infant with bullous mastocytosis to enhance awareness about this rare diagnosis. |
first_indexed | 2024-12-23T05:54:19Z |
format | Article |
id | doaj.art-82cb12addd124b878ecafc97463d0648 |
institution | Directory Open Access Journal |
issn | 2229-5178 |
language | English |
last_indexed | 2024-12-23T05:54:19Z |
publishDate | 2014-01-01 |
publisher | Wolters Kluwer Medknow Publications |
record_format | Article |
series | Indian Dermatology Online Journal |
spelling | doaj.art-82cb12addd124b878ecafc97463d06482022-12-21T17:57:51ZengWolters Kluwer Medknow PublicationsIndian Dermatology Online Journal2229-51782014-01-015449750010.4103/2229-5178.142520Bullous mastocytosis in a 3-month-old infantDinesh Prasad AsatiAnurag TiwariMastocytosis is a rare myeloid neoplasm characterized by abnormal proliferation and accumulation of mast cells in one or more organ systems including the skin, bone marrow, liver, spleen, lymph nodes and gastrointestinal tract. An infant presenting with bullous lesions is an even rarer clinical presentation of cutaneous mastocytosis. The symptoms and complications are mostly in proportion to the mast cell degranulation in tissues. Management is focused on preventing and treating this event. We report a three-month-old infant with bullous mastocytosis to enhance awareness about this rare diagnosis.http://www.idoj.in/article.asp?issn=2229-5178;year=2014;volume=5;issue=4;spage=497;epage=500;aulast=AsatiInfantile bullous mastocytosismast cellsurticaria pigmentosa |
spellingShingle | Dinesh Prasad Asati Anurag Tiwari Bullous mastocytosis in a 3-month-old infant Indian Dermatology Online Journal Infantile bullous mastocytosis mast cells urticaria pigmentosa |
title | Bullous mastocytosis in a 3-month-old infant |
title_full | Bullous mastocytosis in a 3-month-old infant |
title_fullStr | Bullous mastocytosis in a 3-month-old infant |
title_full_unstemmed | Bullous mastocytosis in a 3-month-old infant |
title_short | Bullous mastocytosis in a 3-month-old infant |
title_sort | bullous mastocytosis in a 3 month old infant |
topic | Infantile bullous mastocytosis mast cells urticaria pigmentosa |
url | http://www.idoj.in/article.asp?issn=2229-5178;year=2014;volume=5;issue=4;spage=497;epage=500;aulast=Asati |
work_keys_str_mv | AT dineshprasadasati bullousmastocytosisina3montholdinfant AT anuragtiwari bullousmastocytosisina3montholdinfant |