Pulmonary Arteriovenous Malformations in a 18-months-old Child: A Case Report
Pulmonary Arteriovenous Malformation (PAVM) is a cardiovascular anomaly in which an anatomic communication between the pulmonary artery and pulmonary vein is formed, resulting in an additional cardiac shunt from right to left side. PAVM is a rare disease, reported more in females, but in newborn...
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JCDR Research and Publications Private Limited
2022-08-01
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| Series: | Journal of Clinical and Diagnostic Research |
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| Online Access: | https://www.jcdr.net/articles/PDF/16772/55333_CE(AD)_F(KR)_PF1(SC_KM)_PN(KM).pdf |
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| author | Hesham Mohamad Fayad Fatema Chowdhury Godfred Antony Menezes Shria Sadhu Samiha Anjum Hossain |
| author_facet | Hesham Mohamad Fayad Fatema Chowdhury Godfred Antony Menezes Shria Sadhu Samiha Anjum Hossain |
| author_sort | Hesham Mohamad Fayad |
| collection | DOAJ |
| description | Pulmonary Arteriovenous Malformation (PAVM) is a cardiovascular anomaly in which an anatomic communication between the
pulmonary artery and pulmonary vein is formed, resulting in an additional cardiac shunt from right to left side. PAVM is a rare disease,
reported more in females, but in newborns comparatively higher in males. Cases can vary from asymptomatic to symptomatic such
as having dyspnoea, hypoxia, cyanosis, neurological symptoms. They are mostly congenital having association with Hereditary
Haemorrhagic Telangiectasia (HHT). Herby, author present a case of 18-months-old female admitted with peripheral cyanosis in the
Paediatric Department. Her saturation level was 76%, after admission she received three doses of salbutamol nebulisation and was
kept on 3 litre oxygen until her saturation increased to around 95%. On auscultation, a murmur of grade 2/6 heard in the left axilla
with clear lung fields. Chest X-ray detected a prominent lobulated opacity in the left sided lung adjacent to the heart border. An
echocardiogram was done which turned out normal. Thoracic Computed Tomography (CT) scan with contrast showed a vascular
malformation in the apical region of the left lower lobe. Pulmonary angiography showed multiple vascular lesions in the peripheries
which was consistent with arteriovenous malformation. The child was diagnosed with PAVM. A transcatheter embolisation and coil
closure of AVM was performed and postprocedure the child was stable. |
| first_indexed | 2024-04-10T09:20:58Z |
| format | Article |
| id | doaj.art-8547ac12f19642b18c895552d41c10ab |
| institution | Directory Open Access Journal |
| issn | 2249-782X 0973-709X |
| language | English |
| last_indexed | 2024-04-10T09:20:58Z |
| publishDate | 2022-08-01 |
| publisher | JCDR Research and Publications Private Limited |
| record_format | Article |
| series | Journal of Clinical and Diagnostic Research |
| spelling | doaj.art-8547ac12f19642b18c895552d41c10ab2023-02-20T11:43:15ZengJCDR Research and Publications Private LimitedJournal of Clinical and Diagnostic Research2249-782X0973-709X2022-08-01168SD01SD0310.7860/JCDR/2022/55333.16772Pulmonary Arteriovenous Malformations in a 18-months-old Child: A Case ReportHesham Mohamad Fayad0Fatema Chowdhury1Godfred Antony Menezes2Shria Sadhu3Samiha Anjum Hossain4Consultant, Department of Paediatrics, Saqr Hospital, Al Juwais, Ras Al-Khaimah, United Arab Emirates.Teaching Assistant, Department of Obstetrics and Gynaecology, RAK College of Medical Sciences, RAK Medical and Health Sciences University, Ras Al-Khaimah, United Arab Emirates.Associate Professor and Clinical Microbiologist, Department of Microbiology, RAK College of Medical Sciences, RAK Medical and Health Sciences University, Ras Al-Khaimah, United Arab Emirates.Teaching Assistant, Department of Paediatrics, Al Qassimi Hospital, Wasit St, Mughaidir Suburb-Al Khezamia, Sharjah, United Arab Emirates.Teaching Assistant, Department of Paediatrics, RAK College of Medical Sciences, RAK Medical and Health Sciences University, Ras Al-Khaimah, United Arab Emirates.Pulmonary Arteriovenous Malformation (PAVM) is a cardiovascular anomaly in which an anatomic communication between the pulmonary artery and pulmonary vein is formed, resulting in an additional cardiac shunt from right to left side. PAVM is a rare disease, reported more in females, but in newborns comparatively higher in males. Cases can vary from asymptomatic to symptomatic such as having dyspnoea, hypoxia, cyanosis, neurological symptoms. They are mostly congenital having association with Hereditary Haemorrhagic Telangiectasia (HHT). Herby, author present a case of 18-months-old female admitted with peripheral cyanosis in the Paediatric Department. Her saturation level was 76%, after admission she received three doses of salbutamol nebulisation and was kept on 3 litre oxygen until her saturation increased to around 95%. On auscultation, a murmur of grade 2/6 heard in the left axilla with clear lung fields. Chest X-ray detected a prominent lobulated opacity in the left sided lung adjacent to the heart border. An echocardiogram was done which turned out normal. Thoracic Computed Tomography (CT) scan with contrast showed a vascular malformation in the apical region of the left lower lobe. Pulmonary angiography showed multiple vascular lesions in the peripheries which was consistent with arteriovenous malformation. The child was diagnosed with PAVM. A transcatheter embolisation and coil closure of AVM was performed and postprocedure the child was stable.https://www.jcdr.net/articles/PDF/16772/55333_CE(AD)_F(KR)_PF1(SC_KM)_PN(KM).pdfcardiovascular anomalyhereditary haemorrhagic telangiectasiapulmonary angiographyperipheral cyanosis |
| spellingShingle | Hesham Mohamad Fayad Fatema Chowdhury Godfred Antony Menezes Shria Sadhu Samiha Anjum Hossain Pulmonary Arteriovenous Malformations in a 18-months-old Child: A Case Report Journal of Clinical and Diagnostic Research cardiovascular anomaly hereditary haemorrhagic telangiectasia pulmonary angiography peripheral cyanosis |
| title | Pulmonary Arteriovenous Malformations in a 18-months-old Child: A Case Report |
| title_full | Pulmonary Arteriovenous Malformations in a 18-months-old Child: A Case Report |
| title_fullStr | Pulmonary Arteriovenous Malformations in a 18-months-old Child: A Case Report |
| title_full_unstemmed | Pulmonary Arteriovenous Malformations in a 18-months-old Child: A Case Report |
| title_short | Pulmonary Arteriovenous Malformations in a 18-months-old Child: A Case Report |
| title_sort | pulmonary arteriovenous malformations in a 18 months old child a case report |
| topic | cardiovascular anomaly hereditary haemorrhagic telangiectasia pulmonary angiography peripheral cyanosis |
| url | https://www.jcdr.net/articles/PDF/16772/55333_CE(AD)_F(KR)_PF1(SC_KM)_PN(KM).pdf |
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