Bilateral Vision Loss Secondary to Pachymeningitis in a Patient with IgG4-Related Disease

Bilateral Vision Loss Secondary to Pachymeningitis in a Patient with IgG4-Related Disease

IgG4-Related Disease is a recently recognized fibroinflammatory condition associated with disease in nearly every organ, including the meninges. A proportion of Idiopathic Hypertrophic Pachymeningitis cases may involve a component of meningeal IgG4-RD. We present a patient with severe bilateral visi...

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Bibliographic Details
Main Authors: Lucas eRamirez, Andrea eD'Auria, Adeel ePopalzai, Nerses eSanossian
Format: Article
Language:English
Published: Frontiers Media S.A. 2014-10-01
Series:Frontiers in Neurology
Subjects:
IgG4
Vision Loss
IgG4 Related Disease
Pachymeningitis
Dural Thickening
Online Access:http://journal.frontiersin.org/Journal/10.3389/fneur.2014.00192/full
Description
Summary:IgG4-Related Disease is a recently recognized fibroinflammatory condition associated with disease in nearly every organ, including the meninges. A proportion of Idiopathic Hypertrophic Pachymeningitis cases may involve a component of meningeal IgG4-RD. We present a patient with severe bilateral vision loss found to have thickening of the dura mater on MRI, and subsequently diagnosed with IgG4-RD after dural biopsy.
ISSN:1664-2295

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