Large aortic aneurysm and dissection in a patient with Marfan's syndrome
Marfan’s syndrome is an autosomal dominant disorder of connective tissue affecting approximately1 in5000 people. In individuals with this syndrome, more than 90% of deaths from known causes result from cardiovascular complications, such as aortic dissection, aortic regurgitation, and congestive card...
Main Authors: | , , , |
---|---|
Format: | Article |
Language: | English |
Published: |
Hospital de Clinicas de Porto Alegre ; Universidade Federal do Rio Grande do Sul (UFRGS)
2015-04-01
|
Series: | Clinical and Biomedical Research |
Subjects: | |
Online Access: | http://seer.ufrgs.br/hcpa/article/view/52524 |
_version_ | 1811275970878898176 |
---|---|
author | Fernando Pivatto Júnior Leila Denise Cardoso Ramos Murilo Foppa Felipe Soares Torres |
author_facet | Fernando Pivatto Júnior Leila Denise Cardoso Ramos Murilo Foppa Felipe Soares Torres |
author_sort | Fernando Pivatto Júnior |
collection | DOAJ |
description | Marfan’s syndrome is an autosomal dominant disorder of connective tissue affecting approximately1 in5000 people. In individuals with this syndrome, more than 90% of deaths from known causes result from cardiovascular complications, such as aortic dissection, aortic regurgitation, and congestive cardiac failure. In this report, we present a patient with a large symptomatic aortic aneurysm and chronic dissection, severe aortic regurgitation and cardiomegaly, treated successfully with resection of the proximal aorta and placement of a mechanic aortic valved graft. |
first_indexed | 2024-04-12T23:48:13Z |
format | Article |
id | doaj.art-86d6b94e8f2749278741a59d6c36c421 |
institution | Directory Open Access Journal |
issn | 0101-5575 2357-9730 |
language | English |
last_indexed | 2024-04-12T23:48:13Z |
publishDate | 2015-04-01 |
publisher | Hospital de Clinicas de Porto Alegre ; Universidade Federal do Rio Grande do Sul (UFRGS) |
record_format | Article |
series | Clinical and Biomedical Research |
spelling | doaj.art-86d6b94e8f2749278741a59d6c36c4212022-12-22T03:11:49ZengHospital de Clinicas de Porto Alegre ; Universidade Federal do Rio Grande do Sul (UFRGS)Clinical and Biomedical Research0101-55752357-97302015-04-0135227226Large aortic aneurysm and dissection in a patient with Marfan's syndromeFernando Pivatto Júnior0Leila Denise Cardoso Ramos1Murilo Foppa2Felipe Soares Torres3Cardiology Division, Hospital de Clínicas de Porto Alegre, Porto Alegre, RS - Brazil Mailing address: Fernando Pivatto Júnior, MD Cardiology Division – Hospital de Clínicas de Porto Alegre Rua Ramiro Barcelos, 2350 Sala 2060 90035-903 – Porto Alegre, RS - Brazil E-mail: fpivatto@gmail.com Phone: +55 51 3359-8342Cardiology Division, Hospital de Clínicas de Porto Alegre, Porto Alegre, RS - BrazilCardiology Division, Hospital de Clínicas de Porto Alegre, Porto Alegre, RS - BrazilRadiology Department, Hospital de Clínicas de Porto Alegre, Porto Alegre, RS - BrazilMarfan’s syndrome is an autosomal dominant disorder of connective tissue affecting approximately1 in5000 people. In individuals with this syndrome, more than 90% of deaths from known causes result from cardiovascular complications, such as aortic dissection, aortic regurgitation, and congestive cardiac failure. In this report, we present a patient with a large symptomatic aortic aneurysm and chronic dissection, severe aortic regurgitation and cardiomegaly, treated successfully with resection of the proximal aorta and placement of a mechanic aortic valved graft.http://seer.ufrgs.br/hcpa/article/view/52524Marfan’s syndromeaortic aneurysmdissection |
spellingShingle | Fernando Pivatto Júnior Leila Denise Cardoso Ramos Murilo Foppa Felipe Soares Torres Large aortic aneurysm and dissection in a patient with Marfan's syndrome Clinical and Biomedical Research Marfan’s syndrome aortic aneurysm dissection |
title | Large aortic aneurysm and dissection in a patient with Marfan's syndrome |
title_full | Large aortic aneurysm and dissection in a patient with Marfan's syndrome |
title_fullStr | Large aortic aneurysm and dissection in a patient with Marfan's syndrome |
title_full_unstemmed | Large aortic aneurysm and dissection in a patient with Marfan's syndrome |
title_short | Large aortic aneurysm and dissection in a patient with Marfan's syndrome |
title_sort | large aortic aneurysm and dissection in a patient with marfan s syndrome |
topic | Marfan’s syndrome aortic aneurysm dissection |
url | http://seer.ufrgs.br/hcpa/article/view/52524 |
work_keys_str_mv | AT fernandopivattojunior largeaorticaneurysmanddissectioninapatientwithmarfanssyndrome AT leiladenisecardosoramos largeaorticaneurysmanddissectioninapatientwithmarfanssyndrome AT murilofoppa largeaorticaneurysmanddissectioninapatientwithmarfanssyndrome AT felipesoarestorres largeaorticaneurysmanddissectioninapatientwithmarfanssyndrome |