Large aortic aneurysm and dissection in a patient with Marfan's syndrome

Marfan’s syndrome is an autosomal dominant disorder of connective tissue affecting approximately1 in5000 people. In individuals with this syndrome, more than 90% of deaths from known causes result from cardiovascular complications, such as aortic dissection, aortic regurgitation, and congestive card...

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Main Authors: Fernando Pivatto Júnior, Leila Denise Cardoso Ramos, Murilo Foppa, Felipe Soares Torres
Format: Article
Language:English
Published: Hospital de Clinicas de Porto Alegre ; Universidade Federal do Rio Grande do Sul (UFRGS) 2015-04-01
Series:Clinical and Biomedical Research
Subjects:
Online Access:http://seer.ufrgs.br/hcpa/article/view/52524
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author Fernando Pivatto Júnior
Leila Denise Cardoso Ramos
Murilo Foppa
Felipe Soares Torres
author_facet Fernando Pivatto Júnior
Leila Denise Cardoso Ramos
Murilo Foppa
Felipe Soares Torres
author_sort Fernando Pivatto Júnior
collection DOAJ
description Marfan’s syndrome is an autosomal dominant disorder of connective tissue affecting approximately1 in5000 people. In individuals with this syndrome, more than 90% of deaths from known causes result from cardiovascular complications, such as aortic dissection, aortic regurgitation, and congestive cardiac failure. In this report, we present a patient with a large symptomatic aortic aneurysm and chronic dissection, severe aortic regurgitation and cardiomegaly, treated successfully with resection of the proximal aorta and placement of a mechanic aortic valved graft.
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spelling doaj.art-86d6b94e8f2749278741a59d6c36c4212022-12-22T03:11:49ZengHospital de Clinicas de Porto Alegre ; Universidade Federal do Rio Grande do Sul (UFRGS)Clinical and Biomedical Research0101-55752357-97302015-04-0135227226Large aortic aneurysm and dissection in a patient with Marfan's syndromeFernando Pivatto Júnior0Leila Denise Cardoso Ramos1Murilo Foppa2Felipe Soares Torres3Cardiology Division, Hospital de Clínicas de Porto Alegre, Porto Alegre, RS - Brazil Mailing address: Fernando Pivatto Júnior, MD Cardiology Division – Hospital de Clínicas de Porto Alegre Rua Ramiro Barcelos, 2350 Sala 2060 90035-903 – Porto Alegre, RS - Brazil E-mail: fpivatto@gmail.com Phone: +55 51 3359-8342Cardiology Division, Hospital de Clínicas de Porto Alegre, Porto Alegre, RS - BrazilCardiology Division, Hospital de Clínicas de Porto Alegre, Porto Alegre, RS - BrazilRadiology Department, Hospital de Clínicas de Porto Alegre, Porto Alegre, RS - BrazilMarfan’s syndrome is an autosomal dominant disorder of connective tissue affecting approximately1 in5000 people. In individuals with this syndrome, more than 90% of deaths from known causes result from cardiovascular complications, such as aortic dissection, aortic regurgitation, and congestive cardiac failure. In this report, we present a patient with a large symptomatic aortic aneurysm and chronic dissection, severe aortic regurgitation and cardiomegaly, treated successfully with resection of the proximal aorta and placement of a mechanic aortic valved graft.http://seer.ufrgs.br/hcpa/article/view/52524Marfan’s syndromeaortic aneurysmdissection
spellingShingle Fernando Pivatto Júnior
Leila Denise Cardoso Ramos
Murilo Foppa
Felipe Soares Torres
Large aortic aneurysm and dissection in a patient with Marfan's syndrome
Clinical and Biomedical Research
Marfan’s syndrome
aortic aneurysm
dissection
title Large aortic aneurysm and dissection in a patient with Marfan's syndrome
title_full Large aortic aneurysm and dissection in a patient with Marfan's syndrome
title_fullStr Large aortic aneurysm and dissection in a patient with Marfan's syndrome
title_full_unstemmed Large aortic aneurysm and dissection in a patient with Marfan's syndrome
title_short Large aortic aneurysm and dissection in a patient with Marfan's syndrome
title_sort large aortic aneurysm and dissection in a patient with marfan s syndrome
topic Marfan’s syndrome
aortic aneurysm
dissection
url http://seer.ufrgs.br/hcpa/article/view/52524
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AT felipesoarestorres largeaorticaneurysmanddissectioninapatientwithmarfanssyndrome