Lymphangioleiomyomatosis in a Young Male
Lymphangioleiomyomatosis (LAM) is a rare multisystem disorder, predominantly affecting females in the reproductive age group, characterised by multiple cysts in lungs. A 15-year-old male was admitted in our institute for right sided renal mass for which he underwent right nephrectomy and was referre...
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| Format: | Article |
| Language: | English |
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JCDR Research and Publications Private Limited
2020-01-01
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| Series: | Journal of Clinical and Diagnostic Research |
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| Online Access: | https://jcdr.net/articles/PDF/13424/43159_CE[Ra1]_F(SL)_PF1(AG_SHU)_PFA(SHU)_PB(AG_SHU)_PN(SL).pdf |
| _version_ | 1818580042410622976 |
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| author | Vishwanath Pujari Sanchit Mohan Priti Meshram Rohit Hegde |
| author_facet | Vishwanath Pujari Sanchit Mohan Priti Meshram Rohit Hegde |
| author_sort | Vishwanath Pujari |
| collection | DOAJ |
| description | Lymphangioleiomyomatosis (LAM) is a rare multisystem disorder, predominantly affecting females in the reproductive age group, characterised by multiple cysts in lungs. A 15-year-old male was admitted in our institute for right sided renal mass for which he underwent right nephrectomy and was referred to our department for bilateral spontaneous pneumothoraces. CT thorax was done which showed bilateral pneumothoraces with multiple thin walled cysts and subtle ground glass opacities in both lung fields suggestive of changes of LAM. LAM is rarely seen in males, however if present ER/PR status can help in modifying the management. This is the youngest case of LAM reported in a male worldwide. |
| first_indexed | 2024-12-16T07:11:18Z |
| format | Article |
| id | doaj.art-8944b6e7b3c145fc878c26ce7d99ce76 |
| institution | Directory Open Access Journal |
| issn | 2249-782X 0973-709X |
| language | English |
| last_indexed | 2024-12-16T07:11:18Z |
| publishDate | 2020-01-01 |
| publisher | JCDR Research and Publications Private Limited |
| record_format | Article |
| series | Journal of Clinical and Diagnostic Research |
| spelling | doaj.art-8944b6e7b3c145fc878c26ce7d99ce762022-12-21T22:39:53ZengJCDR Research and Publications Private LimitedJournal of Clinical and Diagnostic Research2249-782X0973-709X2020-01-01141OD03OD0510.7860/JCDR/2020/43159.13424Lymphangioleiomyomatosis in a Young MaleVishwanath Pujari0Sanchit Mohan1Priti Meshram2Rohit Hegde3Associate Professor, Department of Pulmonary Medicine, Grant Government Medical College, Mumbai, Maharashtra, India.Junior Resident, Department of Pulmonary Medicine, Grant Government Medical College, Mumbai, Maharashtra, India.Head, Department of Pulmonary Medicine, Grant Government Medical College, Mumbai, Maharashtra, India.Associate Professor, Department of Pulmonary Medicine, Grant Government Medical College, Mumbai, Maharashtra, India.Lymphangioleiomyomatosis (LAM) is a rare multisystem disorder, predominantly affecting females in the reproductive age group, characterised by multiple cysts in lungs. A 15-year-old male was admitted in our institute for right sided renal mass for which he underwent right nephrectomy and was referred to our department for bilateral spontaneous pneumothoraces. CT thorax was done which showed bilateral pneumothoraces with multiple thin walled cysts and subtle ground glass opacities in both lung fields suggestive of changes of LAM. LAM is rarely seen in males, however if present ER/PR status can help in modifying the management. This is the youngest case of LAM reported in a male worldwide.https://jcdr.net/articles/PDF/13424/43159_CE[Ra1]_F(SL)_PF1(AG_SHU)_PFA(SHU)_PB(AG_SHU)_PN(SL).pdflungsnephrectomypneumothorax |
| spellingShingle | Vishwanath Pujari Sanchit Mohan Priti Meshram Rohit Hegde Lymphangioleiomyomatosis in a Young Male Journal of Clinical and Diagnostic Research lungs nephrectomy pneumothorax |
| title | Lymphangioleiomyomatosis in a Young Male |
| title_full | Lymphangioleiomyomatosis in a Young Male |
| title_fullStr | Lymphangioleiomyomatosis in a Young Male |
| title_full_unstemmed | Lymphangioleiomyomatosis in a Young Male |
| title_short | Lymphangioleiomyomatosis in a Young Male |
| title_sort | lymphangioleiomyomatosis in a young male |
| topic | lungs nephrectomy pneumothorax |
| url | https://jcdr.net/articles/PDF/13424/43159_CE[Ra1]_F(SL)_PF1(AG_SHU)_PFA(SHU)_PB(AG_SHU)_PN(SL).pdf |
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