Craniofacial polyossal fibrous dysplasia

Fibrous dysplasia is a rare anomaly of bone tissue development, in which it is replaced by fibrocystic tissue. A clinical case of a patient with a craniofacial polyossal form of fibrous dysplasia is presented. At the age of 13, a child had a constant intense headache, which was accompanied by dizzin...

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Bibliographic Details
Main Authors: G. A. Kulakova, N. A. Solovyeva, E. A. Kurmaeva, S. Ya. Volgina, E. V. Nikiforova, G. I. Davletshina, D. O. Kuptsova
Format: Article
Language:Russian
Published: Ltd. “The National Academy of Pediatric Science and Innovation” 2022-11-01
Series:Rossijskij Vestnik Perinatologii i Pediatrii
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Online Access:https://www.ped-perinatology.ru/jour/article/view/1724
Description
Summary:Fibrous dysplasia is a rare anomaly of bone tissue development, in which it is replaced by fibrocystic tissue. A clinical case of a patient with a craniofacial polyossal form of fibrous dysplasia is presented. At the age of 13, a child had a constant intense headache, which was accompanied by dizziness, tinnitus, cognitive impairment, deformity of the frontal region and lower jaw on the right, local pigmentation in the neck and face (coffee-and-milk-like stains). Brain tomography and osteoscintigraphy visualized a volumetric formation in the right half of the skull bones, in which fibrotic dysplasia was revealed during histological examination.Conclusion. To establish this diagnosis, a combination of pain syndrome with deformation of the facial part of the skull and histological examination is important.
ISSN:1027-4065
2500-2228