Cor pulmonale in a case of infantile Gaucher′s disease
Infantile Gaucher′s disease presenting as cor pulmonale is rarely reported in pediatric literature. We report a 3.3 year old boy with infantile Gaucher′s disease who presented to us as interstitial lung disease, pulmonary hypertension along with features of cor pulmonale. The high resolution CT find...
| Main Authors: | , , , , , |
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| Format: | Article |
| Language: | English |
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Wolters Kluwer Medknow Publications
2011-01-01
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| Series: | Indian Journal of Endocrinology and Metabolism |
| Subjects: | |
| Online Access: | http://www.ijem.in/article.asp?issn=2230-8210;year=2011;volume=15;issue=2;spage=134;epage=136;aulast=Patra |
| _version_ | 1819230949976571904 |
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| author | Soumya Patra Sayan Chatterjee Shilpi Singhla Bijoy Patra Anu Maheswari Anju Seth |
| author_facet | Soumya Patra Sayan Chatterjee Shilpi Singhla Bijoy Patra Anu Maheswari Anju Seth |
| author_sort | Soumya Patra |
| collection | DOAJ |
| description | Infantile Gaucher′s disease presenting as cor pulmonale is rarely reported in pediatric literature. We report a 3.3 year old boy with infantile Gaucher′s disease who presented to us as interstitial lung disease, pulmonary hypertension along with features of cor pulmonale. The high resolution CT findings were typical of interstitial and airspace disease. Cor pulmonale in this patient was a result of severe pulmonary hypertension. |
| first_indexed | 2024-12-23T11:37:12Z |
| format | Article |
| id | doaj.art-89d81de97ae6442298be99761a426bb5 |
| institution | Directory Open Access Journal |
| issn | 2230-8210 2230-9500 |
| language | English |
| last_indexed | 2024-12-23T11:37:12Z |
| publishDate | 2011-01-01 |
| publisher | Wolters Kluwer Medknow Publications |
| record_format | Article |
| series | Indian Journal of Endocrinology and Metabolism |
| spelling | doaj.art-89d81de97ae6442298be99761a426bb52022-12-21T17:48:36ZengWolters Kluwer Medknow PublicationsIndian Journal of Endocrinology and Metabolism2230-82102230-95002011-01-0115213413610.4103/2230-8210.81948Cor pulmonale in a case of infantile Gaucher′s diseaseSoumya PatraSayan ChatterjeeShilpi SinghlaBijoy PatraAnu MaheswariAnju SethInfantile Gaucher′s disease presenting as cor pulmonale is rarely reported in pediatric literature. We report a 3.3 year old boy with infantile Gaucher′s disease who presented to us as interstitial lung disease, pulmonary hypertension along with features of cor pulmonale. The high resolution CT findings were typical of interstitial and airspace disease. Cor pulmonale in this patient was a result of severe pulmonary hypertension.http://www.ijem.in/article.asp?issn=2230-8210;year=2011;volume=15;issue=2;spage=134;epage=136;aulast=PatraCor-pulmonaleGaucher′s diseaseinfant |
| spellingShingle | Soumya Patra Sayan Chatterjee Shilpi Singhla Bijoy Patra Anu Maheswari Anju Seth Cor pulmonale in a case of infantile Gaucher′s disease Indian Journal of Endocrinology and Metabolism Cor-pulmonale Gaucher′s disease infant |
| title | Cor pulmonale in a case of infantile Gaucher′s disease |
| title_full | Cor pulmonale in a case of infantile Gaucher′s disease |
| title_fullStr | Cor pulmonale in a case of infantile Gaucher′s disease |
| title_full_unstemmed | Cor pulmonale in a case of infantile Gaucher′s disease |
| title_short | Cor pulmonale in a case of infantile Gaucher′s disease |
| title_sort | cor pulmonale in a case of infantile gaucher s disease |
| topic | Cor-pulmonale Gaucher′s disease infant |
| url | http://www.ijem.in/article.asp?issn=2230-8210;year=2011;volume=15;issue=2;spage=134;epage=136;aulast=Patra |
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