Carpal Tunnel Syndrome Associated with Klippel-Trénaunay Syndrome: A Case Report
Background and Importance: Klippel-Trénaunay syndrome is a rare congenital condition that rarely affects peripheral nerves. Median nerve involvement at the carpal tunnel level has only been reported on four occasions of this syndrome in the medical literature. Case Presentation: A 61-year-old Caucas...
| Main Author: | |
|---|---|
| Format: | Article |
| Language: | English |
| Published: |
Guilan University of Medical Sciences
2020-07-01
|
| Series: | Iranian Journal of Neurosurgery |
| Subjects: | |
| Online Access: | http://irjns.org/article-1-204-en.pdf |
| _version_ | 1797778247623114752 |
|---|---|
| author | Joan Arenas-Prat |
| author_facet | Joan Arenas-Prat |
| author_sort | Joan Arenas-Prat |
| collection | DOAJ |
| description | Background and Importance: Klippel-Trénaunay syndrome is a rare congenital condition that rarely affects peripheral nerves. Median nerve involvement at the carpal tunnel level has only been reported on four occasions of this syndrome in the medical literature.
Case Presentation: A 61-year-old Caucasian female patient with Klippel-Trénaunay syndrome presented with a 10-month history of paraesthesia and numbness affecting the median nerve distribution area of her left hand. The clinical and neurophysiological examination confirmed a moderately severe carpal tunnel syndrome that required surgical decompression.
Conclusion: Pre-operative findings demonstrated diffuse vascular infiltration and engorgement of the median nerve. Flexor tendons had a normal appearance. The patient had a satisfactory post-operative period with full resolution of her symptoms 4 weeks after the procedure. Although peripheral nerves are rarely affected in patients with Klippel-Trénaunay syndrome, neurological symptoms could indicate nerve involvement and magnetic resonance imaging (MRI) examination should be considered to further assess the extension of the lesion. |
| first_indexed | 2024-03-12T23:14:34Z |
| format | Article |
| id | doaj.art-8b7298fc8efd4cdeb59a7d2f27023fb7 |
| institution | Directory Open Access Journal |
| issn | 2423-6497 2423-6829 |
| language | English |
| last_indexed | 2024-03-12T23:14:34Z |
| publishDate | 2020-07-01 |
| publisher | Guilan University of Medical Sciences |
| record_format | Article |
| series | Iranian Journal of Neurosurgery |
| spelling | doaj.art-8b7298fc8efd4cdeb59a7d2f27023fb72023-07-17T13:29:15ZengGuilan University of Medical SciencesIranian Journal of Neurosurgery2423-64972423-68292020-07-0163161164Carpal Tunnel Syndrome Associated with Klippel-Trénaunay Syndrome: A Case ReportJoan Arenas-Prat0 Serveis Mèdics Penedès, Department of Orthopedics, Barcelona, Catalonia, Spain. Background and Importance: Klippel-Trénaunay syndrome is a rare congenital condition that rarely affects peripheral nerves. Median nerve involvement at the carpal tunnel level has only been reported on four occasions of this syndrome in the medical literature. Case Presentation: A 61-year-old Caucasian female patient with Klippel-Trénaunay syndrome presented with a 10-month history of paraesthesia and numbness affecting the median nerve distribution area of her left hand. The clinical and neurophysiological examination confirmed a moderately severe carpal tunnel syndrome that required surgical decompression. Conclusion: Pre-operative findings demonstrated diffuse vascular infiltration and engorgement of the median nerve. Flexor tendons had a normal appearance. The patient had a satisfactory post-operative period with full resolution of her symptoms 4 weeks after the procedure. Although peripheral nerves are rarely affected in patients with Klippel-Trénaunay syndrome, neurological symptoms could indicate nerve involvement and magnetic resonance imaging (MRI) examination should be considered to further assess the extension of the lesion.http://irjns.org/article-1-204-en.pdfklippel-trénaunay syndromecarpal tunnel syndromemedian nerve |
| spellingShingle | Joan Arenas-Prat Carpal Tunnel Syndrome Associated with Klippel-Trénaunay Syndrome: A Case Report Iranian Journal of Neurosurgery klippel-trénaunay syndrome carpal tunnel syndrome median nerve |
| title | Carpal Tunnel Syndrome Associated with Klippel-Trénaunay Syndrome: A Case Report |
| title_full | Carpal Tunnel Syndrome Associated with Klippel-Trénaunay Syndrome: A Case Report |
| title_fullStr | Carpal Tunnel Syndrome Associated with Klippel-Trénaunay Syndrome: A Case Report |
| title_full_unstemmed | Carpal Tunnel Syndrome Associated with Klippel-Trénaunay Syndrome: A Case Report |
| title_short | Carpal Tunnel Syndrome Associated with Klippel-Trénaunay Syndrome: A Case Report |
| title_sort | carpal tunnel syndrome associated with klippel trenaunay syndrome a case report |
| topic | klippel-trénaunay syndrome carpal tunnel syndrome median nerve |
| url | http://irjns.org/article-1-204-en.pdf |
| work_keys_str_mv | AT joanarenasprat carpaltunnelsyndromeassociatedwithklippeltrenaunaysyndromeacasereport |