Subglottotracheal Adenoid Cystic Carcinoma in a 16-Year-Old Female—A Case Report
Cystic adenoid carcinoma (ACC) is a rare malignant epithelial tumor arising from exocrine glands and accounts for only 1% of head and neck cancers. ACCs are common in the fifth and sixth decades of life, predominantly in women, and characterized by slow progression, local aggression, recurrence, and...
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| Format: | Article |
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MDPI AG
2023-06-01
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| Series: | Medicina |
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| Online Access: | https://www.mdpi.com/1648-9144/59/6/1140 |
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| author | Cristina Ștefania Dumitru Nicolae Constantin Balica |
| author_facet | Cristina Ștefania Dumitru Nicolae Constantin Balica |
| author_sort | Cristina Ștefania Dumitru |
| collection | DOAJ |
| description | Cystic adenoid carcinoma (ACC) is a rare malignant epithelial tumor arising from exocrine glands and accounts for only 1% of head and neck cancers. ACCs are common in the fifth and sixth decades of life, predominantly in women, and characterized by slow progression, local aggression, recurrence, and high metastasis. Subglottotracheal ACC is a rare tumor in the pediatric population, with only a few cases reported in the literature. We present a case of a 16-year-old female who was diagnosed with ACC in the subglottic and tracheal region. The patient presented with respiratory failure but without a history of dysphonia, dyspnea, stridor, or dysphagia. The diagnosis was confirmed by a biopsy, and subsequent imaging studies showed a large tumor involving the subglottic and tracheal region. The therapeutic management of this patient has been challenging due to the rarity of this tumor in the pediatric population and the potential long-term complications associated with tumor recurrence and psychological impact. This case highlights the diagnostic and therapeutic challenges in the management of subglottotracheal ACC in children and the importance of a multidisciplinary approach to optimize patient outcomes. |
| first_indexed | 2024-03-11T02:11:27Z |
| format | Article |
| id | doaj.art-8c3100cae7194b53858b255409e05ad4 |
| institution | Directory Open Access Journal |
| issn | 1010-660X 1648-9144 |
| language | English |
| last_indexed | 2024-03-11T02:11:27Z |
| publishDate | 2023-06-01 |
| publisher | MDPI AG |
| record_format | Article |
| series | Medicina |
| spelling | doaj.art-8c3100cae7194b53858b255409e05ad42023-11-18T11:32:04ZengMDPI AGMedicina1010-660X1648-91442023-06-01596114010.3390/medicina59061140Subglottotracheal Adenoid Cystic Carcinoma in a 16-Year-Old Female—A Case ReportCristina Ștefania Dumitru0Nicolae Constantin Balica1Department of Microscopic Morphology/Histology, Angiogenesis Research Center, “Victor Babes” University of Medicine and Pharmacy, Sq. EftimieMurgu No. 2, 300041 Timisoara, RomaniaDepartment of Ear-Nose-Throat, “Victor Babes” University of Medicine and Pharmacy, Eftimie Murgu Square 2, 300041 Timisoara, RomaniaCystic adenoid carcinoma (ACC) is a rare malignant epithelial tumor arising from exocrine glands and accounts for only 1% of head and neck cancers. ACCs are common in the fifth and sixth decades of life, predominantly in women, and characterized by slow progression, local aggression, recurrence, and high metastasis. Subglottotracheal ACC is a rare tumor in the pediatric population, with only a few cases reported in the literature. We present a case of a 16-year-old female who was diagnosed with ACC in the subglottic and tracheal region. The patient presented with respiratory failure but without a history of dysphonia, dyspnea, stridor, or dysphagia. The diagnosis was confirmed by a biopsy, and subsequent imaging studies showed a large tumor involving the subglottic and tracheal region. The therapeutic management of this patient has been challenging due to the rarity of this tumor in the pediatric population and the potential long-term complications associated with tumor recurrence and psychological impact. This case highlights the diagnostic and therapeutic challenges in the management of subglottotracheal ACC in children and the importance of a multidisciplinary approach to optimize patient outcomes.https://www.mdpi.com/1648-9144/59/6/1140adenoid cystic carcinomasubglottotrachealpediatric patientmanagement |
| spellingShingle | Cristina Ștefania Dumitru Nicolae Constantin Balica Subglottotracheal Adenoid Cystic Carcinoma in a 16-Year-Old Female—A Case Report Medicina adenoid cystic carcinoma subglottotracheal pediatric patient management |
| title | Subglottotracheal Adenoid Cystic Carcinoma in a 16-Year-Old Female—A Case Report |
| title_full | Subglottotracheal Adenoid Cystic Carcinoma in a 16-Year-Old Female—A Case Report |
| title_fullStr | Subglottotracheal Adenoid Cystic Carcinoma in a 16-Year-Old Female—A Case Report |
| title_full_unstemmed | Subglottotracheal Adenoid Cystic Carcinoma in a 16-Year-Old Female—A Case Report |
| title_short | Subglottotracheal Adenoid Cystic Carcinoma in a 16-Year-Old Female—A Case Report |
| title_sort | subglottotracheal adenoid cystic carcinoma in a 16 year old female a case report |
| topic | adenoid cystic carcinoma subglottotracheal pediatric patient management |
| url | https://www.mdpi.com/1648-9144/59/6/1140 |
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