Unilateral pigmented paravenous retinochoroidal atrophy with acute angle-closure glaucoma: a case report
Abstract Background Pigmented paravenous retinochoroidal atrophy (PPRCA) is an uncommon fundus disease characterized by perivenous aggregations of pigment clumps and retinochoroidal atrophy distributed along the retinal veins. We report a Chinese female case of unilateral PPRCA with acute angle-clos...
| Main Authors: | , , , , , |
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| Format: | Article |
| Language: | English |
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BMC
2023-05-01
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| Series: | BMC Ophthalmology |
| Subjects: | |
| Online Access: | https://doi.org/10.1186/s12886-023-02922-4 |
| _version_ | 1797827653440372736 |
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| author | Kun Lv Zhiqiao Liang Kangyi Yang Xuanzhu Chen Yao Ma Huijuan Wu |
| author_facet | Kun Lv Zhiqiao Liang Kangyi Yang Xuanzhu Chen Yao Ma Huijuan Wu |
| author_sort | Kun Lv |
| collection | DOAJ |
| description | Abstract Background Pigmented paravenous retinochoroidal atrophy (PPRCA) is an uncommon fundus disease characterized by perivenous aggregations of pigment clumps and retinochoroidal atrophy distributed along the retinal veins. We report a Chinese female case of unilateral PPRCA with acute angle-closure glaucoma (AACG). Case presentation A 50-year-old Chinese female presented with vision loss and elevated intraocular pressure (IOP) in the right eye and then underwent trabeculectomy. She referred to our clinic for further evaluation and treatment. The funduscopic examination revealed grayish retinochoroidal atrophy and osteocyte-like pigment clumping lesions along the retinal veins and peripapillary preretinal hemorrhage in the right eye. The patient also presented with AACG in the same eye on the basis of past medical history of acute attack, shallow anterior chamber depth (ACD), narrow angle showed by ultrasound biomicroscopy (UBM) and glaucomatous neuropathy identified by optical coherence tomography (OCT). Other examinations like fluorescein fundus angiography (FFA), electroretinogram (ERG) and electrooculography (EOG) all confirmed the aforementioned diagnose. Conclusion PPRCA is a rare disease, uncommon in females and symmetrical in both eyes. We present a rare case of unilateral PPRCA accompanied with AACG. |
| first_indexed | 2024-04-09T12:51:48Z |
| format | Article |
| id | doaj.art-8cb009458cd543c9a84029130b536e78 |
| institution | Directory Open Access Journal |
| issn | 1471-2415 |
| language | English |
| last_indexed | 2024-04-09T12:51:48Z |
| publishDate | 2023-05-01 |
| publisher | BMC |
| record_format | Article |
| series | BMC Ophthalmology |
| spelling | doaj.art-8cb009458cd543c9a84029130b536e782023-05-14T11:11:53ZengBMCBMC Ophthalmology1471-24152023-05-012311610.1186/s12886-023-02922-4Unilateral pigmented paravenous retinochoroidal atrophy with acute angle-closure glaucoma: a case reportKun Lv0Zhiqiao Liang1Kangyi Yang2Xuanzhu Chen3Yao Ma4Huijuan Wu5Department of Ophthalmology, Peking University People’s HospitalDepartment of Ophthalmology, Peking University People’s HospitalDepartment of Ophthalmology, Peking University People’s HospitalDepartment of Ophthalmology, Peking University People’s HospitalDepartment of Ophthalmology, Peking University People’s HospitalDepartment of Ophthalmology, Peking University People’s HospitalAbstract Background Pigmented paravenous retinochoroidal atrophy (PPRCA) is an uncommon fundus disease characterized by perivenous aggregations of pigment clumps and retinochoroidal atrophy distributed along the retinal veins. We report a Chinese female case of unilateral PPRCA with acute angle-closure glaucoma (AACG). Case presentation A 50-year-old Chinese female presented with vision loss and elevated intraocular pressure (IOP) in the right eye and then underwent trabeculectomy. She referred to our clinic for further evaluation and treatment. The funduscopic examination revealed grayish retinochoroidal atrophy and osteocyte-like pigment clumping lesions along the retinal veins and peripapillary preretinal hemorrhage in the right eye. The patient also presented with AACG in the same eye on the basis of past medical history of acute attack, shallow anterior chamber depth (ACD), narrow angle showed by ultrasound biomicroscopy (UBM) and glaucomatous neuropathy identified by optical coherence tomography (OCT). Other examinations like fluorescein fundus angiography (FFA), electroretinogram (ERG) and electrooculography (EOG) all confirmed the aforementioned diagnose. Conclusion PPRCA is a rare disease, uncommon in females and symmetrical in both eyes. We present a rare case of unilateral PPRCA accompanied with AACG.https://doi.org/10.1186/s12886-023-02922-4Pigmented paravenous retinochoroidal atrophyAcute angle-closure glaucomaUnilateral |
| spellingShingle | Kun Lv Zhiqiao Liang Kangyi Yang Xuanzhu Chen Yao Ma Huijuan Wu Unilateral pigmented paravenous retinochoroidal atrophy with acute angle-closure glaucoma: a case report BMC Ophthalmology Pigmented paravenous retinochoroidal atrophy Acute angle-closure glaucoma Unilateral |
| title | Unilateral pigmented paravenous retinochoroidal atrophy with acute angle-closure glaucoma: a case report |
| title_full | Unilateral pigmented paravenous retinochoroidal atrophy with acute angle-closure glaucoma: a case report |
| title_fullStr | Unilateral pigmented paravenous retinochoroidal atrophy with acute angle-closure glaucoma: a case report |
| title_full_unstemmed | Unilateral pigmented paravenous retinochoroidal atrophy with acute angle-closure glaucoma: a case report |
| title_short | Unilateral pigmented paravenous retinochoroidal atrophy with acute angle-closure glaucoma: a case report |
| title_sort | unilateral pigmented paravenous retinochoroidal atrophy with acute angle closure glaucoma a case report |
| topic | Pigmented paravenous retinochoroidal atrophy Acute angle-closure glaucoma Unilateral |
| url | https://doi.org/10.1186/s12886-023-02922-4 |
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