Appendicitis as a Leading Manifestation of Kawasaki Disease in Older Children
Kawasaki disease (KD) is a systematic inflammatory disease with multiple organ involvement. Timely diagnosis and prompt management are essential for successful treatment. KD, with an atypical presentation, remains a diagnostic challenge for physicians. We report a five-year-old boy who presented wit...
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MDPI AG
2022-02-01
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Series: | Children |
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Online Access: | https://www.mdpi.com/2227-9067/9/2/193 |
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author | Ya-Ning Huang Lu-Hang Liu Jeng-Jung Chen Yu-Lin Tai Yih-Cherng Duh Chien-Yu Lin |
author_facet | Ya-Ning Huang Lu-Hang Liu Jeng-Jung Chen Yu-Lin Tai Yih-Cherng Duh Chien-Yu Lin |
author_sort | Ya-Ning Huang |
collection | DOAJ |
description | Kawasaki disease (KD) is a systematic inflammatory disease with multiple organ involvement. Timely diagnosis and prompt management are essential for successful treatment. KD, with an atypical presentation, remains a diagnostic challenge for physicians. We report a five-year-old boy who presented with appendicitis. An appendectomy was performed; however, his fever persisted. The boy was diagnosed with KD and intravenous immunoglobulin was administered. His symptoms resolved, and he had an uneventful recovery. Furthermore, we performed a literature review with 13 cases identified in the literature. Most cases were male, and the average age was older than typical for KD. In conclusion, KD may present with abdominal complaints and appendicitis may be a rare initial presentation of KD. Multidisciplinary cooperation and high awareness are warranted for timely diagnosis, especially in older children experiencing persistent fever after an appendectomy. |
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issn | 2227-9067 |
language | English |
last_indexed | 2024-03-09T22:18:21Z |
publishDate | 2022-02-01 |
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series | Children |
spelling | doaj.art-8cec7bfb854c4b9789d9f21aa5c304822023-11-23T19:19:02ZengMDPI AGChildren2227-90672022-02-019219310.3390/children9020193Appendicitis as a Leading Manifestation of Kawasaki Disease in Older ChildrenYa-Ning Huang0Lu-Hang Liu1Jeng-Jung Chen2Yu-Lin Tai3Yih-Cherng Duh4Chien-Yu Lin5Department of Pediatrics, MacKay Children’s Hospital, Taipei 10449, TaiwanDepartment of Pediatrics, Hsinchu MacKay Memorial Hospital, Hsinchu City 30071, TaiwanDepartment of Pediatrics, Hsinchu MacKay Memorial Hospital, Hsinchu City 30071, TaiwanDepartment of Pediatrics, Hsinchu MacKay Memorial Hospital, Hsinchu City 30071, TaiwanDivision of Pediatric Surgery, Department of Surgery, Hsinchu MacKay Memorial Hospital, Hsinchu City 30071, TaiwanDepartment of Pediatrics, Hsinchu MacKay Memorial Hospital, Hsinchu City 30071, TaiwanKawasaki disease (KD) is a systematic inflammatory disease with multiple organ involvement. Timely diagnosis and prompt management are essential for successful treatment. KD, with an atypical presentation, remains a diagnostic challenge for physicians. We report a five-year-old boy who presented with appendicitis. An appendectomy was performed; however, his fever persisted. The boy was diagnosed with KD and intravenous immunoglobulin was administered. His symptoms resolved, and he had an uneventful recovery. Furthermore, we performed a literature review with 13 cases identified in the literature. Most cases were male, and the average age was older than typical for KD. In conclusion, KD may present with abdominal complaints and appendicitis may be a rare initial presentation of KD. Multidisciplinary cooperation and high awareness are warranted for timely diagnosis, especially in older children experiencing persistent fever after an appendectomy.https://www.mdpi.com/2227-9067/9/2/193Kawasaki diseaseappendicitisintravenous immunoglobulinacute abdomencoronary aneurysm |
spellingShingle | Ya-Ning Huang Lu-Hang Liu Jeng-Jung Chen Yu-Lin Tai Yih-Cherng Duh Chien-Yu Lin Appendicitis as a Leading Manifestation of Kawasaki Disease in Older Children Children Kawasaki disease appendicitis intravenous immunoglobulin acute abdomen coronary aneurysm |
title | Appendicitis as a Leading Manifestation of Kawasaki Disease in Older Children |
title_full | Appendicitis as a Leading Manifestation of Kawasaki Disease in Older Children |
title_fullStr | Appendicitis as a Leading Manifestation of Kawasaki Disease in Older Children |
title_full_unstemmed | Appendicitis as a Leading Manifestation of Kawasaki Disease in Older Children |
title_short | Appendicitis as a Leading Manifestation of Kawasaki Disease in Older Children |
title_sort | appendicitis as a leading manifestation of kawasaki disease in older children |
topic | Kawasaki disease appendicitis intravenous immunoglobulin acute abdomen coronary aneurysm |
url | https://www.mdpi.com/2227-9067/9/2/193 |
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