Appendicitis as a Leading Manifestation of Kawasaki Disease in Older Children

Kawasaki disease (KD) is a systematic inflammatory disease with multiple organ involvement. Timely diagnosis and prompt management are essential for successful treatment. KD, with an atypical presentation, remains a diagnostic challenge for physicians. We report a five-year-old boy who presented wit...

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Main Authors: Ya-Ning Huang, Lu-Hang Liu, Jeng-Jung Chen, Yu-Lin Tai, Yih-Cherng Duh, Chien-Yu Lin
Format: Article
Language:English
Published: MDPI AG 2022-02-01
Series:Children
Subjects:
Online Access:https://www.mdpi.com/2227-9067/9/2/193
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author Ya-Ning Huang
Lu-Hang Liu
Jeng-Jung Chen
Yu-Lin Tai
Yih-Cherng Duh
Chien-Yu Lin
author_facet Ya-Ning Huang
Lu-Hang Liu
Jeng-Jung Chen
Yu-Lin Tai
Yih-Cherng Duh
Chien-Yu Lin
author_sort Ya-Ning Huang
collection DOAJ
description Kawasaki disease (KD) is a systematic inflammatory disease with multiple organ involvement. Timely diagnosis and prompt management are essential for successful treatment. KD, with an atypical presentation, remains a diagnostic challenge for physicians. We report a five-year-old boy who presented with appendicitis. An appendectomy was performed; however, his fever persisted. The boy was diagnosed with KD and intravenous immunoglobulin was administered. His symptoms resolved, and he had an uneventful recovery. Furthermore, we performed a literature review with 13 cases identified in the literature. Most cases were male, and the average age was older than typical for KD. In conclusion, KD may present with abdominal complaints and appendicitis may be a rare initial presentation of KD. Multidisciplinary cooperation and high awareness are warranted for timely diagnosis, especially in older children experiencing persistent fever after an appendectomy.
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spelling doaj.art-8cec7bfb854c4b9789d9f21aa5c304822023-11-23T19:19:02ZengMDPI AGChildren2227-90672022-02-019219310.3390/children9020193Appendicitis as a Leading Manifestation of Kawasaki Disease in Older ChildrenYa-Ning Huang0Lu-Hang Liu1Jeng-Jung Chen2Yu-Lin Tai3Yih-Cherng Duh4Chien-Yu Lin5Department of Pediatrics, MacKay Children’s Hospital, Taipei 10449, TaiwanDepartment of Pediatrics, Hsinchu MacKay Memorial Hospital, Hsinchu City 30071, TaiwanDepartment of Pediatrics, Hsinchu MacKay Memorial Hospital, Hsinchu City 30071, TaiwanDepartment of Pediatrics, Hsinchu MacKay Memorial Hospital, Hsinchu City 30071, TaiwanDivision of Pediatric Surgery, Department of Surgery, Hsinchu MacKay Memorial Hospital, Hsinchu City 30071, TaiwanDepartment of Pediatrics, Hsinchu MacKay Memorial Hospital, Hsinchu City 30071, TaiwanKawasaki disease (KD) is a systematic inflammatory disease with multiple organ involvement. Timely diagnosis and prompt management are essential for successful treatment. KD, with an atypical presentation, remains a diagnostic challenge for physicians. We report a five-year-old boy who presented with appendicitis. An appendectomy was performed; however, his fever persisted. The boy was diagnosed with KD and intravenous immunoglobulin was administered. His symptoms resolved, and he had an uneventful recovery. Furthermore, we performed a literature review with 13 cases identified in the literature. Most cases were male, and the average age was older than typical for KD. In conclusion, KD may present with abdominal complaints and appendicitis may be a rare initial presentation of KD. Multidisciplinary cooperation and high awareness are warranted for timely diagnosis, especially in older children experiencing persistent fever after an appendectomy.https://www.mdpi.com/2227-9067/9/2/193Kawasaki diseaseappendicitisintravenous immunoglobulinacute abdomencoronary aneurysm
spellingShingle Ya-Ning Huang
Lu-Hang Liu
Jeng-Jung Chen
Yu-Lin Tai
Yih-Cherng Duh
Chien-Yu Lin
Appendicitis as a Leading Manifestation of Kawasaki Disease in Older Children
Children
Kawasaki disease
appendicitis
intravenous immunoglobulin
acute abdomen
coronary aneurysm
title Appendicitis as a Leading Manifestation of Kawasaki Disease in Older Children
title_full Appendicitis as a Leading Manifestation of Kawasaki Disease in Older Children
title_fullStr Appendicitis as a Leading Manifestation of Kawasaki Disease in Older Children
title_full_unstemmed Appendicitis as a Leading Manifestation of Kawasaki Disease in Older Children
title_short Appendicitis as a Leading Manifestation of Kawasaki Disease in Older Children
title_sort appendicitis as a leading manifestation of kawasaki disease in older children
topic Kawasaki disease
appendicitis
intravenous immunoglobulin
acute abdomen
coronary aneurysm
url https://www.mdpi.com/2227-9067/9/2/193
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