Peculiar type 1 congenital pyloric atresia: a case report

<p>Abstract</p> <p>Pyloric atresia (PA) is a very rare condition. Its incidence is approximately 1 in 100,000 newborns and constitutes about 1% of all intestinal atresias. We describe the neonatal course of a peculiar case of type 1 pyloric atresia, in which the pyloric membrane wa...

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Main Authors: Nanni Lorenzo, Pintus Claudio, Corsello Mirta, Zecca Enrico, Zecca Susanna
Format: Article
Language:English
Published: BMC 2010-01-01
Series:Italian Journal of Pediatrics
Online Access:http://www.ijponline.net/content/36/1/3
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author Nanni Lorenzo
Pintus Claudio
Corsello Mirta
Zecca Enrico
Zecca Susanna
author_facet Nanni Lorenzo
Pintus Claudio
Corsello Mirta
Zecca Enrico
Zecca Susanna
author_sort Nanni Lorenzo
collection DOAJ
description <p>Abstract</p> <p>Pyloric atresia (PA) is a very rare condition. Its incidence is approximately 1 in 100,000 newborns and constitutes about 1% of all intestinal atresias. We describe the neonatal course of a peculiar case of type 1 pyloric atresia, in which the pyloric membrane was connected to a second duodenal membrane through a virtual duodenal lumen in a premature newborn. The atypical variant required an unusual side to side gastroduodenostomy. We emphasize the importance of a prompt diagnosis to avoid potentially fatal complications and to warrant a good outcome even in the presence of a strange form of PA in the neonatal period.</p>
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spelling doaj.art-8d7460eb93a541e9925a85d6903cb99b2022-12-22T02:57:59ZengBMCItalian Journal of Pediatrics1720-84241824-72882010-01-01361310.1186/1824-7288-36-3Peculiar type 1 congenital pyloric atresia: a case reportNanni LorenzoPintus ClaudioCorsello MirtaZecca EnricoZecca Susanna<p>Abstract</p> <p>Pyloric atresia (PA) is a very rare condition. Its incidence is approximately 1 in 100,000 newborns and constitutes about 1% of all intestinal atresias. We describe the neonatal course of a peculiar case of type 1 pyloric atresia, in which the pyloric membrane was connected to a second duodenal membrane through a virtual duodenal lumen in a premature newborn. The atypical variant required an unusual side to side gastroduodenostomy. We emphasize the importance of a prompt diagnosis to avoid potentially fatal complications and to warrant a good outcome even in the presence of a strange form of PA in the neonatal period.</p>http://www.ijponline.net/content/36/1/3
spellingShingle Nanni Lorenzo
Pintus Claudio
Corsello Mirta
Zecca Enrico
Zecca Susanna
Peculiar type 1 congenital pyloric atresia: a case report
Italian Journal of Pediatrics
title Peculiar type 1 congenital pyloric atresia: a case report
title_full Peculiar type 1 congenital pyloric atresia: a case report
title_fullStr Peculiar type 1 congenital pyloric atresia: a case report
title_full_unstemmed Peculiar type 1 congenital pyloric atresia: a case report
title_short Peculiar type 1 congenital pyloric atresia: a case report
title_sort peculiar type 1 congenital pyloric atresia a case report
url http://www.ijponline.net/content/36/1/3
work_keys_str_mv AT nannilorenzo peculiartype1congenitalpyloricatresiaacasereport
AT pintusclaudio peculiartype1congenitalpyloricatresiaacasereport
AT corsellomirta peculiartype1congenitalpyloricatresiaacasereport
AT zeccaenrico peculiartype1congenitalpyloricatresiaacasereport
AT zeccasusanna peculiartype1congenitalpyloricatresiaacasereport