Cardiac Magnetic Resonance in Fabry Disease: Morphological, Functional, and Tissue Features

Cardiac Magnetic Resonance in Fabry Disease: Morphological, Functional, and Tissue Features

Fabry disease (FD) is an X-linked inheritable storage disease caused by a deficiency of alpha-galactosidase causing lysosomal overload of sphingolipids. FD cardiomyopathy is characterized by left ventricular (LV) hypertrophy and should be considered in differential diagnosis with all the other cause...

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Bibliographic Details
Main Authors:	Giovanni Donato Aquaro, Carmelo De Gori, Lorenzo Faggioni, Maria Luisa Parisella, Giacomo Aringhieri, Dania Cioni, Riccardo Lencioni, Emanuele Neri
Format:	Article
Language:	English
Published:	MDPI AG 2022-11-01
Series:	Diagnostics
Subjects:	Fabry disease cardiac magnetic resonance T1 mapping late gadolinium enhancement feature tracking
Online Access:	https://www.mdpi.com/2075-4418/12/11/2652

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