Left Ventricular Dysfunction in Arrhythmogenic Right Ventricular Cardiomyopathy (ARVC): Can We Separate ARVC From Other Arrhythmogenic Cardiomyopathies?

Abstract Arrhythmogenic right ventricular cardiomyopathy was first described as a right ventricular disease that is an important cause of death in young adults. However, with the advent of advanced imaging, arrhythmogenic right ventricular cardiomyopathy has been found to commonly have biventricular...

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Main Authors: Stephan Altmayer, Saman Nazarian, Yuchi Han
Format: Article
Language:English
Published: Wiley 2020-12-01
Series:Journal of the American Heart Association: Cardiovascular and Cerebrovascular Disease
Subjects:
Online Access:https://www.ahajournals.org/doi/10.1161/JAHA.120.018866
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author Stephan Altmayer
Saman Nazarian
Yuchi Han
author_facet Stephan Altmayer
Saman Nazarian
Yuchi Han
author_sort Stephan Altmayer
collection DOAJ
description Abstract Arrhythmogenic right ventricular cardiomyopathy was first described as a right ventricular disease that is an important cause of death in young adults. However, with the advent of advanced imaging, arrhythmogenic right ventricular cardiomyopathy has been found to commonly have biventricular involvement, and a small portion of patients have left ventricular–dominant forms. On the other hand, a number of primarily left ventricular disease such as sarcoid and myocarditis can be arrhythmogenic and have right ventricular involvement. A few recent publications on arrhythmogenic right ventricular cardiomyopathy cohorts have average left ventricular functions that are comparable to sarcoid or myocarditis cohorts. We review the current literature and compare these cohorts of patients, and call for left ventricular functional criteria for arrhythmogenic right ventricular cardiomyopathy as inherited arrhythmogenic cardiomyopathy.
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spelling doaj.art-8ff7a20839e545ecac9f36f076247d0c2022-12-21T18:11:28ZengWileyJournal of the American Heart Association: Cardiovascular and Cerebrovascular Disease2047-99802020-12-0192310.1161/JAHA.120.018866Left Ventricular Dysfunction in Arrhythmogenic Right Ventricular Cardiomyopathy (ARVC): Can We Separate ARVC From Other Arrhythmogenic Cardiomyopathies?Stephan Altmayer0Saman Nazarian1Yuchi Han2Department of Radiology Pontificia Universidade Catolica do Rio Grande do Sul Porto Alegre BrazilCardiovascular Division Department of Medicine University of Pennsylvania Philadelphia PACardiovascular Division Department of Medicine University of Pennsylvania Philadelphia PAAbstract Arrhythmogenic right ventricular cardiomyopathy was first described as a right ventricular disease that is an important cause of death in young adults. However, with the advent of advanced imaging, arrhythmogenic right ventricular cardiomyopathy has been found to commonly have biventricular involvement, and a small portion of patients have left ventricular–dominant forms. On the other hand, a number of primarily left ventricular disease such as sarcoid and myocarditis can be arrhythmogenic and have right ventricular involvement. A few recent publications on arrhythmogenic right ventricular cardiomyopathy cohorts have average left ventricular functions that are comparable to sarcoid or myocarditis cohorts. We review the current literature and compare these cohorts of patients, and call for left ventricular functional criteria for arrhythmogenic right ventricular cardiomyopathy as inherited arrhythmogenic cardiomyopathy.https://www.ahajournals.org/doi/10.1161/JAHA.120.018866arryhthmogenic cardiomyopathyarrhythmogenic right ventricular cardiomyopathyarrhythmogenic right ventricular dysplasia
spellingShingle Stephan Altmayer
Saman Nazarian
Yuchi Han
Left Ventricular Dysfunction in Arrhythmogenic Right Ventricular Cardiomyopathy (ARVC): Can We Separate ARVC From Other Arrhythmogenic Cardiomyopathies?
Journal of the American Heart Association: Cardiovascular and Cerebrovascular Disease
arryhthmogenic cardiomyopathy
arrhythmogenic right ventricular cardiomyopathy
arrhythmogenic right ventricular dysplasia
title Left Ventricular Dysfunction in Arrhythmogenic Right Ventricular Cardiomyopathy (ARVC): Can We Separate ARVC From Other Arrhythmogenic Cardiomyopathies?
title_full Left Ventricular Dysfunction in Arrhythmogenic Right Ventricular Cardiomyopathy (ARVC): Can We Separate ARVC From Other Arrhythmogenic Cardiomyopathies?
title_fullStr Left Ventricular Dysfunction in Arrhythmogenic Right Ventricular Cardiomyopathy (ARVC): Can We Separate ARVC From Other Arrhythmogenic Cardiomyopathies?
title_full_unstemmed Left Ventricular Dysfunction in Arrhythmogenic Right Ventricular Cardiomyopathy (ARVC): Can We Separate ARVC From Other Arrhythmogenic Cardiomyopathies?
title_short Left Ventricular Dysfunction in Arrhythmogenic Right Ventricular Cardiomyopathy (ARVC): Can We Separate ARVC From Other Arrhythmogenic Cardiomyopathies?
title_sort left ventricular dysfunction in arrhythmogenic right ventricular cardiomyopathy arvc can we separate arvc from other arrhythmogenic cardiomyopathies
topic arryhthmogenic cardiomyopathy
arrhythmogenic right ventricular cardiomyopathy
arrhythmogenic right ventricular dysplasia
url https://www.ahajournals.org/doi/10.1161/JAHA.120.018866
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