Congenital Mitral Aortic Intervalvular Fibrosa Aneurysm with Submitral Aneurysm
Congenital aneurysm of the mitral aortic intervalvular fibrosa (MAIVF) is a relatively rare condition. It was initially described in the African population and subsequently reported in other racial groups. Many of the subaortic aneurysms arise from the MAIVF; association with submitral aneurysm (SMA...
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| Format: | Article |
| Language: | English |
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Wolters Kluwer Medknow Publications
2020-01-01
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| Series: | Journal of the Indian Academy of Echocardiography & Cardiovascular Imaging |
| Subjects: | |
| Online Access: | http://www.jiaecho.org/article.asp?issn=2543-1463;year=2020;volume=4;issue=3;spage=383;epage=386;aulast=Shah |
| _version_ | 1818611679852756992 |
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| author | Rajesh Krishnachandra Shah |
| author_facet | Rajesh Krishnachandra Shah |
| author_sort | Rajesh Krishnachandra Shah |
| collection | DOAJ |
| description | Congenital aneurysm of the mitral aortic intervalvular fibrosa (MAIVF) is a relatively rare condition. It was initially described in the African population and subsequently reported in other racial groups. Many of the subaortic aneurysms arise from the MAIVF; association with submitral aneurysm (SMA) is even rare. They more commonly occur as a pseudoaneurysm of the MAIVF-P, which is usually due to a complication of endocarditis or aortic valve surgery. Diagnosis is usually with echocardiography, and complete confirmation and anatomical assessment are done by computerised tomography and cardiac magnetic resonance imaging, which are useful for surgical evaluation. Surgery is the only treatment when it is large or symptomatic or has related complications, such as rupture, compression of adjacent structures, embolic events, mitral regurgitation, or heart failure. Here, case is presented of a congenital variety of MAIVF aneurysm with congenital SMA, in a 31-year-old female. She presented with breathlessness. She had mitral regurgitation, and had to undergo surgical repair and mitral valve replacement. This may be the first case reported of a congenital MAIVF aneurysm with a congenital SMA. |
| first_indexed | 2024-12-16T15:34:10Z |
| format | Article |
| id | doaj.art-92c9fb77b2d5423eafc8107cc6974e2e |
| institution | Directory Open Access Journal |
| issn | 2543-1463 2543-1471 |
| language | English |
| last_indexed | 2024-12-16T15:34:10Z |
| publishDate | 2020-01-01 |
| publisher | Wolters Kluwer Medknow Publications |
| record_format | Article |
| series | Journal of the Indian Academy of Echocardiography & Cardiovascular Imaging |
| spelling | doaj.art-92c9fb77b2d5423eafc8107cc6974e2e2022-12-21T22:26:16ZengWolters Kluwer Medknow PublicationsJournal of the Indian Academy of Echocardiography & Cardiovascular Imaging2543-14632543-14712020-01-014338338610.4103/jiae.jiae_1_20Congenital Mitral Aortic Intervalvular Fibrosa Aneurysm with Submitral AneurysmRajesh Krishnachandra ShahCongenital aneurysm of the mitral aortic intervalvular fibrosa (MAIVF) is a relatively rare condition. It was initially described in the African population and subsequently reported in other racial groups. Many of the subaortic aneurysms arise from the MAIVF; association with submitral aneurysm (SMA) is even rare. They more commonly occur as a pseudoaneurysm of the MAIVF-P, which is usually due to a complication of endocarditis or aortic valve surgery. Diagnosis is usually with echocardiography, and complete confirmation and anatomical assessment are done by computerised tomography and cardiac magnetic resonance imaging, which are useful for surgical evaluation. Surgery is the only treatment when it is large or symptomatic or has related complications, such as rupture, compression of adjacent structures, embolic events, mitral regurgitation, or heart failure. Here, case is presented of a congenital variety of MAIVF aneurysm with congenital SMA, in a 31-year-old female. She presented with breathlessness. She had mitral regurgitation, and had to undergo surgical repair and mitral valve replacement. This may be the first case reported of a congenital MAIVF aneurysm with a congenital SMA.http://www.jiaecho.org/article.asp?issn=2543-1463;year=2020;volume=4;issue=3;spage=383;epage=386;aulast=Shahmitral aortic intervalvular fibrosa aneurysmpseudoaneurysm of the mitral aortic intervalvular fibrosasubmitral aneurysm |
| spellingShingle | Rajesh Krishnachandra Shah Congenital Mitral Aortic Intervalvular Fibrosa Aneurysm with Submitral Aneurysm Journal of the Indian Academy of Echocardiography & Cardiovascular Imaging mitral aortic intervalvular fibrosa aneurysm pseudoaneurysm of the mitral aortic intervalvular fibrosa submitral aneurysm |
| title | Congenital Mitral Aortic Intervalvular Fibrosa Aneurysm with Submitral Aneurysm |
| title_full | Congenital Mitral Aortic Intervalvular Fibrosa Aneurysm with Submitral Aneurysm |
| title_fullStr | Congenital Mitral Aortic Intervalvular Fibrosa Aneurysm with Submitral Aneurysm |
| title_full_unstemmed | Congenital Mitral Aortic Intervalvular Fibrosa Aneurysm with Submitral Aneurysm |
| title_short | Congenital Mitral Aortic Intervalvular Fibrosa Aneurysm with Submitral Aneurysm |
| title_sort | congenital mitral aortic intervalvular fibrosa aneurysm with submitral aneurysm |
| topic | mitral aortic intervalvular fibrosa aneurysm pseudoaneurysm of the mitral aortic intervalvular fibrosa submitral aneurysm |
| url | http://www.jiaecho.org/article.asp?issn=2543-1463;year=2020;volume=4;issue=3;spage=383;epage=386;aulast=Shah |
| work_keys_str_mv | AT rajeshkrishnachandrashah congenitalmitralaorticintervalvularfibrosaaneurysmwithsubmitralaneurysm |