Hematopoietic Stem Cell Transplantation for DNA Double Strand Breakage Repair Disorders
The ubiquitous presence of enzymes required for repair of DNA double strand breaks renders patients with defects in these pathways susceptible to immunodeficiency, an increased risk of infection, autoimmunity, bone marrow failure and malignancies, which are commonly associated with Epstein Barr viru...
Auteurs principaux: | Beata Wolska-Kuśnierz, Andrew R. Gennery |
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Format: | Article |
Langue: | English |
Publié: |
Frontiers Media S.A.
2020-01-01
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Collection: | Frontiers in Pediatrics |
Sujets: | |
Accès en ligne: | https://www.frontiersin.org/article/10.3389/fped.2019.00557/full |
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