Primary Perivascular Epithelioid Cell Tumor of the Lung: A Case Report

Perivascular epithelioid cell tumors (PEComas) are very rare mesenchymal neoplasms, composed of histologically and immunohistochemically distinctive cells that form a sheetlike appearance around vessel lumens. Although most are benign, a malignant subset does exist, complicating clinical diagnost...

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Bibliographic Details
Main Authors: Hye Rim Na, Jong Hui Suh, Jiyun Lee
Format: Article
Language:English
Published: Korean Society for Thoracic & Cardiovascular Surgery 2023-09-01
Series:Journal of Chest Surgery
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Description
Summary:Perivascular epithelioid cell tumors (PEComas) are very rare mesenchymal neoplasms, composed of histologically and immunohistochemically distinctive cells that form a sheetlike appearance around vessel lumens. Although most are benign, a malignant subset does exist, complicating clinical diagnostic efforts. Proper evaluation and management are thus essential for long-term patient survival. Herein, we present a rare case of a benign pulmonary PEComa that was diagnosed postoperatively in a 45-year-old woman.
ISSN:2765-1606
2765-1614