Neurofibroma of the external genitalia, extreme enlargement of the clitoris
Neurofibromatosis of the genitourinary tract is rare, with a prevalence of 0.65%, and it is exceedingly rare to involve the external genitalia. Involvement of the clitoris, labia majora, and prepuce was reported with clitoromegaly being the most frequently occurring. Herein, we are reporting the cas...
| Main Authors: | , , , , , |
|---|---|
| Format: | Article |
| Language: | English |
| Published: |
Wolters Kluwer Medknow Publications
2023-01-01
|
| Series: | Urology Annals |
| Subjects: | |
| Online Access: | http://www.urologyannals.com/article.asp?issn=0974-7796;year=2023;volume=15;issue=3;spage=328;epage=330;aulast=Almesned |
| _version_ | 1797738469954420736 |
|---|---|
| author | Razan Almesned Mohamed Alhagbani Mohammed Sultan Mohammed Alshayie Naif Alqarni Ahmed Alshammari |
| author_facet | Razan Almesned Mohamed Alhagbani Mohammed Sultan Mohammed Alshayie Naif Alqarni Ahmed Alshammari |
| author_sort | Razan Almesned |
| collection | DOAJ |
| description | Neurofibromatosis of the genitourinary tract is rare, with a prevalence of 0.65%, and it is exceedingly rare to involve the external genitalia. Involvement of the clitoris, labia majora, and prepuce was reported with clitoromegaly being the most frequently occurring. Herein, we are reporting the case of a 6-year-old girl who was diagnosed with a neurofibroma of the clitoris; measuring 9.4 cm in its largest dimension. To the best of our knowledge, this is the largest clitoral neurofibroma reported in the literature. Due to the rarity of such cases and reports limitations in the literature, the diagnosis of neurofibroma of the external genitalia requires a high index of suspicion by health-care providers. Surgical excision and postoperative follow-up for possible recurrence remain the gold standard of management. |
| first_indexed | 2024-03-12T13:43:17Z |
| format | Article |
| id | doaj.art-94ab0b67f4fd47dfb419bba6f4c61352 |
| institution | Directory Open Access Journal |
| issn | 0974-7796 0974-7834 |
| language | English |
| last_indexed | 2024-03-12T13:43:17Z |
| publishDate | 2023-01-01 |
| publisher | Wolters Kluwer Medknow Publications |
| record_format | Article |
| series | Urology Annals |
| spelling | doaj.art-94ab0b67f4fd47dfb419bba6f4c613522023-08-23T09:47:47ZengWolters Kluwer Medknow PublicationsUrology Annals0974-77960974-78342023-01-0115332833010.4103/ua.ua_86_22Neurofibroma of the external genitalia, extreme enlargement of the clitorisRazan AlmesnedMohamed AlhagbaniMohammed SultanMohammed AlshayieNaif AlqarniAhmed AlshammariNeurofibromatosis of the genitourinary tract is rare, with a prevalence of 0.65%, and it is exceedingly rare to involve the external genitalia. Involvement of the clitoris, labia majora, and prepuce was reported with clitoromegaly being the most frequently occurring. Herein, we are reporting the case of a 6-year-old girl who was diagnosed with a neurofibroma of the clitoris; measuring 9.4 cm in its largest dimension. To the best of our knowledge, this is the largest clitoral neurofibroma reported in the literature. Due to the rarity of such cases and reports limitations in the literature, the diagnosis of neurofibroma of the external genitalia requires a high index of suspicion by health-care providers. Surgical excision and postoperative follow-up for possible recurrence remain the gold standard of management.http://www.urologyannals.com/article.asp?issn=0974-7796;year=2023;volume=15;issue=3;spage=328;epage=330;aulast=Almesnedclitorisneurofibromatosisplexiform neurofibroma |
| spellingShingle | Razan Almesned Mohamed Alhagbani Mohammed Sultan Mohammed Alshayie Naif Alqarni Ahmed Alshammari Neurofibroma of the external genitalia, extreme enlargement of the clitoris Urology Annals clitoris neurofibromatosis plexiform neurofibroma |
| title | Neurofibroma of the external genitalia, extreme enlargement of the clitoris |
| title_full | Neurofibroma of the external genitalia, extreme enlargement of the clitoris |
| title_fullStr | Neurofibroma of the external genitalia, extreme enlargement of the clitoris |
| title_full_unstemmed | Neurofibroma of the external genitalia, extreme enlargement of the clitoris |
| title_short | Neurofibroma of the external genitalia, extreme enlargement of the clitoris |
| title_sort | neurofibroma of the external genitalia extreme enlargement of the clitoris |
| topic | clitoris neurofibromatosis plexiform neurofibroma |
| url | http://www.urologyannals.com/article.asp?issn=0974-7796;year=2023;volume=15;issue=3;spage=328;epage=330;aulast=Almesned |
| work_keys_str_mv | AT razanalmesned neurofibromaoftheexternalgenitaliaextremeenlargementoftheclitoris AT mohamedalhagbani neurofibromaoftheexternalgenitaliaextremeenlargementoftheclitoris AT mohammedsultan neurofibromaoftheexternalgenitaliaextremeenlargementoftheclitoris AT mohammedalshayie neurofibromaoftheexternalgenitaliaextremeenlargementoftheclitoris AT naifalqarni neurofibromaoftheexternalgenitaliaextremeenlargementoftheclitoris AT ahmedalshammari neurofibromaoftheexternalgenitaliaextremeenlargementoftheclitoris |