A Translocation Renal Cell Carcinoma with Skeletal Muscle Metastasis in a Child

Renal cell carcinoma is a tumor that is well known for a high rate of metastasis to several locations like the lung, liver and bones. Skeletal muscle is a rare location for dissemination of the disease. Herein, we describe a 7-year-old boy who presented with flank pain. On physical examination, an a...

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Main Authors: Gülen TÜYSÜZ, Nihal ÖZDEMİR, Haluk EMİR, Haydar DURAK, Sergülen DERVİŞOĞLU, İbrahim ADALETLİ, Hilmi APAK
Format: Article
Language:English
Published: Federation of Turkish Pathology Societies 2017-09-01
Series:Türk Patoloji Dergisi
Subjects:
Online Access:http://www.turkjpath.org/pdf.php3?id=1695
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author Gülen TÜYSÜZ
Nihal ÖZDEMİR
Haluk EMİR
Haydar DURAK
Sergülen DERVİŞOĞLU
İbrahim ADALETLİ
Hilmi APAK
author_facet Gülen TÜYSÜZ
Nihal ÖZDEMİR
Haluk EMİR
Haydar DURAK
Sergülen DERVİŞOĞLU
İbrahim ADALETLİ
Hilmi APAK
author_sort Gülen TÜYSÜZ
collection DOAJ
description Renal cell carcinoma is a tumor that is well known for a high rate of metastasis to several locations like the lung, liver and bones. Skeletal muscle is a rare location for dissemination of the disease. Herein, we describe a 7-year-old boy who presented with flank pain. On physical examination, an abdominal mass located on the left kidney as well as a solid palpable lesion on the left upper arm were detected. Total nephrectomy with subsequent excision of the arm mass was performed. Pathology examination revealed presence of translocation renal cell carcinoma. The patient received α-interferon followed by multikinase inhibitor (Sorafenib) treatment but was lost due to progressive disease. This is the first description of a pediatric patient with skeletal muscle metastases of translocation renal cell carcinoma in the literature.
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spelling doaj.art-94cfc35c89b049d394b2d3800892e04b2023-02-15T16:22:12ZengFederation of Turkish Pathology SocietiesTürk Patoloji Dergisi1018-56151309-57302017-09-01333248250A Translocation Renal Cell Carcinoma with Skeletal Muscle Metastasis in a ChildGülen TÜYSÜZNihal ÖZDEMİRHaluk EMİRHaydar DURAKSergülen DERVİŞOĞLUİbrahim ADALETLİHilmi APAKRenal cell carcinoma is a tumor that is well known for a high rate of metastasis to several locations like the lung, liver and bones. Skeletal muscle is a rare location for dissemination of the disease. Herein, we describe a 7-year-old boy who presented with flank pain. On physical examination, an abdominal mass located on the left kidney as well as a solid palpable lesion on the left upper arm were detected. Total nephrectomy with subsequent excision of the arm mass was performed. Pathology examination revealed presence of translocation renal cell carcinoma. The patient received α-interferon followed by multikinase inhibitor (Sorafenib) treatment but was lost due to progressive disease. This is the first description of a pediatric patient with skeletal muscle metastases of translocation renal cell carcinoma in the literature.http://www.turkjpath.org/pdf.php3?id=1695Translocation renal cell carcinomaPediatricSkeletal muscleMetastases
spellingShingle Gülen TÜYSÜZ
Nihal ÖZDEMİR
Haluk EMİR
Haydar DURAK
Sergülen DERVİŞOĞLU
İbrahim ADALETLİ
Hilmi APAK
A Translocation Renal Cell Carcinoma with Skeletal Muscle Metastasis in a Child
Türk Patoloji Dergisi
Translocation renal cell carcinoma
Pediatric
Skeletal muscle
Metastases
title A Translocation Renal Cell Carcinoma with Skeletal Muscle Metastasis in a Child
title_full A Translocation Renal Cell Carcinoma with Skeletal Muscle Metastasis in a Child
title_fullStr A Translocation Renal Cell Carcinoma with Skeletal Muscle Metastasis in a Child
title_full_unstemmed A Translocation Renal Cell Carcinoma with Skeletal Muscle Metastasis in a Child
title_short A Translocation Renal Cell Carcinoma with Skeletal Muscle Metastasis in a Child
title_sort translocation renal cell carcinoma with skeletal muscle metastasis in a child
topic Translocation renal cell carcinoma
Pediatric
Skeletal muscle
Metastases
url http://www.turkjpath.org/pdf.php3?id=1695
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