A Translocation Renal Cell Carcinoma with Skeletal Muscle Metastasis in a Child
Renal cell carcinoma is a tumor that is well known for a high rate of metastasis to several locations like the lung, liver and bones. Skeletal muscle is a rare location for dissemination of the disease. Herein, we describe a 7-year-old boy who presented with flank pain. On physical examination, an a...
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Format: | Article |
Language: | English |
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Federation of Turkish Pathology Societies
2017-09-01
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Series: | Türk Patoloji Dergisi |
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Online Access: | http://www.turkjpath.org/pdf.php3?id=1695 |
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author | Gülen TÜYSÜZ Nihal ÖZDEMİR Haluk EMİR Haydar DURAK Sergülen DERVİŞOĞLU İbrahim ADALETLİ Hilmi APAK |
author_facet | Gülen TÜYSÜZ Nihal ÖZDEMİR Haluk EMİR Haydar DURAK Sergülen DERVİŞOĞLU İbrahim ADALETLİ Hilmi APAK |
author_sort | Gülen TÜYSÜZ |
collection | DOAJ |
description | Renal cell carcinoma is a tumor that is well known for a high rate of metastasis to several locations like the lung, liver and bones. Skeletal muscle is a rare location for dissemination of the disease. Herein, we describe a 7-year-old boy who presented with flank pain. On physical examination, an abdominal mass located on the left kidney as well as a solid palpable lesion on the left upper arm were detected. Total nephrectomy with subsequent excision of the arm mass was performed. Pathology examination revealed presence of translocation renal cell carcinoma. The patient received α-interferon followed by multikinase inhibitor (Sorafenib) treatment but was lost due to progressive disease. This is the first description of a pediatric patient with skeletal muscle metastases of translocation renal cell carcinoma in the literature. |
first_indexed | 2024-04-10T10:10:21Z |
format | Article |
id | doaj.art-94cfc35c89b049d394b2d3800892e04b |
institution | Directory Open Access Journal |
issn | 1018-5615 1309-5730 |
language | English |
last_indexed | 2024-04-10T10:10:21Z |
publishDate | 2017-09-01 |
publisher | Federation of Turkish Pathology Societies |
record_format | Article |
series | Türk Patoloji Dergisi |
spelling | doaj.art-94cfc35c89b049d394b2d3800892e04b2023-02-15T16:22:12ZengFederation of Turkish Pathology SocietiesTürk Patoloji Dergisi1018-56151309-57302017-09-01333248250A Translocation Renal Cell Carcinoma with Skeletal Muscle Metastasis in a ChildGülen TÜYSÜZNihal ÖZDEMİRHaluk EMİRHaydar DURAKSergülen DERVİŞOĞLUİbrahim ADALETLİHilmi APAKRenal cell carcinoma is a tumor that is well known for a high rate of metastasis to several locations like the lung, liver and bones. Skeletal muscle is a rare location for dissemination of the disease. Herein, we describe a 7-year-old boy who presented with flank pain. On physical examination, an abdominal mass located on the left kidney as well as a solid palpable lesion on the left upper arm were detected. Total nephrectomy with subsequent excision of the arm mass was performed. Pathology examination revealed presence of translocation renal cell carcinoma. The patient received α-interferon followed by multikinase inhibitor (Sorafenib) treatment but was lost due to progressive disease. This is the first description of a pediatric patient with skeletal muscle metastases of translocation renal cell carcinoma in the literature.http://www.turkjpath.org/pdf.php3?id=1695Translocation renal cell carcinomaPediatricSkeletal muscleMetastases |
spellingShingle | Gülen TÜYSÜZ Nihal ÖZDEMİR Haluk EMİR Haydar DURAK Sergülen DERVİŞOĞLU İbrahim ADALETLİ Hilmi APAK A Translocation Renal Cell Carcinoma with Skeletal Muscle Metastasis in a Child Türk Patoloji Dergisi Translocation renal cell carcinoma Pediatric Skeletal muscle Metastases |
title | A Translocation Renal Cell Carcinoma with Skeletal Muscle Metastasis in a Child |
title_full | A Translocation Renal Cell Carcinoma with Skeletal Muscle Metastasis in a Child |
title_fullStr | A Translocation Renal Cell Carcinoma with Skeletal Muscle Metastasis in a Child |
title_full_unstemmed | A Translocation Renal Cell Carcinoma with Skeletal Muscle Metastasis in a Child |
title_short | A Translocation Renal Cell Carcinoma with Skeletal Muscle Metastasis in a Child |
title_sort | translocation renal cell carcinoma with skeletal muscle metastasis in a child |
topic | Translocation renal cell carcinoma Pediatric Skeletal muscle Metastases |
url | http://www.turkjpath.org/pdf.php3?id=1695 |
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