Malignant Peripheral Nerve Sheath Tumors—A Comprehensive Review of Pathophysiology, Diagnosis, and Multidisciplinary Management

Malignant Peripheral Nerve Sheath Tumors—A Comprehensive Review of Pathophysiology, Diagnosis, and Multidisciplinary Management

Malignant peripheral nerve sheath tumors (MPNSTs) are aggressive soft tissue sarcomas (STS) with nerve sheath differentiation and a tendency to metastasize. Although occurring at an incidence of 0.001% in the general population, they are relatively common in individuals with neurofibromatosis type 1...

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Bibliographic Details
Main Authors: Samantha W. E. Knight, Tristan E. Knight, Teresa Santiago, Andrew J. Murphy, Abdelhafeez H. Abdelhafeez
Format: Article
Language:English
Published: MDPI AG 2022-01-01
Series:Children
Subjects:
malignant peripheral nerve sheath tumor
MEK inhibitor
multi-disciplinary management
neurofibroma
neurofibromatosis type 1
Online Access:https://www.mdpi.com/2227-9067/9/1/38

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