Aorto-ventricular tunnel: Aortic regurgitation and noncompaction cardiomyopathy – Common late associations after repair

Aorto-ventricular tunnels are rare, congenital extracardiac connections arising from the tubular ascending aorta, above the sinotubular junction, which communicate directly with the ventricular cavity. We present long-term follow-up in a series of five adults undergoing pediatric repair and describe...

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Bibliographic Details
Main Authors: Irene Martin de Miguel, Alexander C. Egbe, Heidi M. Connolly, Patrick W. O'Leary, William R. Miranda
Format: Article
Language:English
Published: Elsevier 2022-06-01
Series:International Journal of Cardiology Congenital Heart Disease
Subjects:
Online Access:http://www.sciencedirect.com/science/article/pii/S2666668522000507
Description
Summary:Aorto-ventricular tunnels are rare, congenital extracardiac connections arising from the tubular ascending aorta, above the sinotubular junction, which communicate directly with the ventricular cavity. We present long-term follow-up in a series of five adults undergoing pediatric repair and describe the cardiovascular features and outcomes. Significant aortic regurgitation, ascending aortic aneurysm and left ventricular noncompaction were found to be highly prevalent, emphasizing the need for ongoing surveillance following repair of this anomaly.
ISSN:2666-6685