Orbicularis oculi myectomy as a treatment for blepharospasm in a case of Schwartz Jampel syndrome

Purpose: To describe a patient with Schwartz Jampel vel Aberfeld syndrome (SJS) who underwent orbicularis oculi myectomy as a treatment for blepharospasm. Case Report: A 4-year-old child with SJS did not respond to an injection of a single dose of botulinum toxin after one month, so orbicularis myec...

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Main Authors: Bahram Eshraghi, Mahla Shadravan, Elham Aalami, Elias Khalili Pour
Format: Article
Language:English
Published: Knowledge E 2016-01-01
Series:Journal of Ophthalmic & Vision Research
Subjects:
Online Access:http://www.jovr.org/article.asp?issn=2008-322X;year=2016;volume=11;issue=3;spage=329;epage=332;aulast=Eshraghi
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author Bahram Eshraghi
Mahla Shadravan
Elham Aalami
Elias Khalili Pour
author_facet Bahram Eshraghi
Mahla Shadravan
Elham Aalami
Elias Khalili Pour
author_sort Bahram Eshraghi
collection DOAJ
description Purpose: To describe a patient with Schwartz Jampel vel Aberfeld syndrome (SJS) who underwent orbicularis oculi myectomy as a treatment for blepharospasm. Case Report: A 4-year-old child with SJS did not respond to an injection of a single dose of botulinum toxin after one month, so orbicularis myectomy was then performed under general anesthesia. During the procedure, orbicularis vermiform movements were a useful guide for the extent of myectomy that the patient needed. He responded very well to this procedure and experienced significant relief of blepharospasm documented in follow-up visits for up to 6 months. Conclusion: Blepharospasm in patients with SJS can be treated with orbicularis oculi myectomy as a good functional method with faster and durable response in comparison to botulinum toxin injection.
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spelling doaj.art-96403e07c2d7424b8dd8ed07ec6dbd8c2022-12-22T03:26:31ZengKnowledge EJournal of Ophthalmic & Vision Research2008-322X2016-01-0111332933210.4103/2008-322X.188401Orbicularis oculi myectomy as a treatment for blepharospasm in a case of Schwartz Jampel syndromeBahram EshraghiMahla ShadravanElham AalamiElias Khalili PourPurpose: To describe a patient with Schwartz Jampel vel Aberfeld syndrome (SJS) who underwent orbicularis oculi myectomy as a treatment for blepharospasm. Case Report: A 4-year-old child with SJS did not respond to an injection of a single dose of botulinum toxin after one month, so orbicularis myectomy was then performed under general anesthesia. During the procedure, orbicularis vermiform movements were a useful guide for the extent of myectomy that the patient needed. He responded very well to this procedure and experienced significant relief of blepharospasm documented in follow-up visits for up to 6 months. Conclusion: Blepharospasm in patients with SJS can be treated with orbicularis oculi myectomy as a good functional method with faster and durable response in comparison to botulinum toxin injection.http://www.jovr.org/article.asp?issn=2008-322X;year=2016;volume=11;issue=3;spage=329;epage=332;aulast=EshraghiBlepharospasm; Orbicularis Oculi Myectomy; Schwartz Jampel Syndrome
spellingShingle Bahram Eshraghi
Mahla Shadravan
Elham Aalami
Elias Khalili Pour
Orbicularis oculi myectomy as a treatment for blepharospasm in a case of Schwartz Jampel syndrome
Journal of Ophthalmic & Vision Research
Blepharospasm; Orbicularis Oculi Myectomy; Schwartz Jampel Syndrome
title Orbicularis oculi myectomy as a treatment for blepharospasm in a case of Schwartz Jampel syndrome
title_full Orbicularis oculi myectomy as a treatment for blepharospasm in a case of Schwartz Jampel syndrome
title_fullStr Orbicularis oculi myectomy as a treatment for blepharospasm in a case of Schwartz Jampel syndrome
title_full_unstemmed Orbicularis oculi myectomy as a treatment for blepharospasm in a case of Schwartz Jampel syndrome
title_short Orbicularis oculi myectomy as a treatment for blepharospasm in a case of Schwartz Jampel syndrome
title_sort orbicularis oculi myectomy as a treatment for blepharospasm in a case of schwartz jampel syndrome
topic Blepharospasm; Orbicularis Oculi Myectomy; Schwartz Jampel Syndrome
url http://www.jovr.org/article.asp?issn=2008-322X;year=2016;volume=11;issue=3;spage=329;epage=332;aulast=Eshraghi
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AT mahlashadravan orbicularisoculimyectomyasatreatmentforblepharospasminacaseofschwartzjampelsyndrome
AT elhamaalami orbicularisoculimyectomyasatreatmentforblepharospasminacaseofschwartzjampelsyndrome
AT eliaskhalilipour orbicularisoculimyectomyasatreatmentforblepharospasminacaseofschwartzjampelsyndrome