A 40 years old woman with monolobar Caroli’s syndrome treated by left hepatic lobectomy
Caroli’s disease (CD) is a rare congenital abnormality characterized by dilatation of intra hepatic bile ducts, which causes stone formation, recurrent cholangitis and higher risk for biliary malignancy. Association of this anomaly with congenital hepatic fibrosis is named Caroli&a...
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| Format: | Article |
| Language: | English |
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Wolters Kluwer Medknow Publications
2007-12-01
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| Series: | Journal of Research in Medical Sciences |
| Subjects: | |
| Online Access: | http://journals.mui.ac.ir/jrms/article/view/1008 |
| _version_ | 1818533571454828544 |
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| author | Hamid Tavakkoli Abbas Tabatabaei Amir Hosein Davarpanah Jazi Mahshid Haghighi Diana Taheri Mahbobeh Tavakkoli |
| author_facet | Hamid Tavakkoli Abbas Tabatabaei Amir Hosein Davarpanah Jazi Mahshid Haghighi Diana Taheri Mahbobeh Tavakkoli |
| author_sort | Hamid Tavakkoli |
| collection | DOAJ |
| description | Caroli&rsquo;s disease (CD) is a rare congenital abnormality characterized by dilatation of intra hepatic bile ducts, which causes stone formation, recurrent cholangitis and higher risk for biliary malignancy. Association of this anomaly with congenital hepatic fibrosis is named Caroli&rsquo;s syndrome (CS). The monolobar involvement of CS is a very rare condition, curable by partial hepatectomy. We report a 40-year-old woman with recurrent epigastric pain without icterus with<br /> normal AST, ALT and alkaline phosphates for 5 years due to left lobe Caroli syndrome which was diagnosed by CT scan and MRCP. Then, the patient underwent successful operation (left hepatic resection). After 8 months follow up, she was symptom free. Because the presentation of unilobar CS may be as late as middle age, this congenital anomaly should be considered in differential diagnosis of patients with recurrent epigastric pain without icterus in this age group and MRCP is a useful diagnostic tool.<br /> <strong>KEY WORDS</strong>: Caroli&rsquo;s disease, Caroli&rsquo;s syndrome, congenital hepatic fibrosis, magnetic resonance cholangiopancreatography.<br /> |
| first_indexed | 2024-12-11T18:00:29Z |
| format | Article |
| id | doaj.art-96761e4e7c23489b9c1d2a64bbdf40d6 |
| institution | Directory Open Access Journal |
| issn | 1735-1995 1735-7136 |
| language | English |
| last_indexed | 2024-12-11T18:00:29Z |
| publishDate | 2007-12-01 |
| publisher | Wolters Kluwer Medknow Publications |
| record_format | Article |
| series | Journal of Research in Medical Sciences |
| spelling | doaj.art-96761e4e7c23489b9c1d2a64bbdf40d62022-12-22T00:55:54ZengWolters Kluwer Medknow PublicationsJournal of Research in Medical Sciences1735-19951735-71362007-12-01126320325A 40 years old woman with monolobar Caroli’s syndrome treated by left hepatic lobectomyHamid TavakkoliAbbas TabatabaeiAmir Hosein Davarpanah JaziMahshid HaghighiDiana TaheriMahbobeh TavakkoliCaroli&rsquo;s disease (CD) is a rare congenital abnormality characterized by dilatation of intra hepatic bile ducts, which causes stone formation, recurrent cholangitis and higher risk for biliary malignancy. Association of this anomaly with congenital hepatic fibrosis is named Caroli&rsquo;s syndrome (CS). The monolobar involvement of CS is a very rare condition, curable by partial hepatectomy. We report a 40-year-old woman with recurrent epigastric pain without icterus with<br /> normal AST, ALT and alkaline phosphates for 5 years due to left lobe Caroli syndrome which was diagnosed by CT scan and MRCP. Then, the patient underwent successful operation (left hepatic resection). After 8 months follow up, she was symptom free. Because the presentation of unilobar CS may be as late as middle age, this congenital anomaly should be considered in differential diagnosis of patients with recurrent epigastric pain without icterus in this age group and MRCP is a useful diagnostic tool.<br /> <strong>KEY WORDS</strong>: Caroli&rsquo;s disease, Caroli&rsquo;s syndrome, congenital hepatic fibrosis, magnetic resonance cholangiopancreatography.<br />http://journals.mui.ac.ir/jrms/article/view/1008Caroli’s disease, Caroli’s syndrome, congenital hepatic fibrosis, magnetic resonance cholangiopancreatography. |
| spellingShingle | Hamid Tavakkoli Abbas Tabatabaei Amir Hosein Davarpanah Jazi Mahshid Haghighi Diana Taheri Mahbobeh Tavakkoli A 40 years old woman with monolobar Caroli’s syndrome treated by left hepatic lobectomy Journal of Research in Medical Sciences Caroli’s disease, Caroli’s syndrome, congenital hepatic fibrosis, magnetic resonance cholangiopancreatography. |
| title | A 40 years old woman with monolobar Caroli’s syndrome treated by left hepatic lobectomy |
| title_full | A 40 years old woman with monolobar Caroli’s syndrome treated by left hepatic lobectomy |
| title_fullStr | A 40 years old woman with monolobar Caroli’s syndrome treated by left hepatic lobectomy |
| title_full_unstemmed | A 40 years old woman with monolobar Caroli’s syndrome treated by left hepatic lobectomy |
| title_short | A 40 years old woman with monolobar Caroli’s syndrome treated by left hepatic lobectomy |
| title_sort | 40 years old woman with monolobar caroli s syndrome treated by left hepatic lobectomy |
| topic | Caroli’s disease, Caroli’s syndrome, congenital hepatic fibrosis, magnetic resonance cholangiopancreatography. |
| url | http://journals.mui.ac.ir/jrms/article/view/1008 |
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