Probable sporadic Creutzfeldt–Jakob disease mimicking focal epilepsy
Creutzfeldt–Jakob disease (CJD) presents with seizures as an early symptom in only approximately 3% of cases. These seizures often present as nonconvulsive status epilepticus (NCSE) or epilepsia partialis continua (EPC). Here, we describe a case of probable sporadic CJD (sCJD) in an 83-year-old man...
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Format: | Article |
Language: | English |
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Elsevier
2019-01-01
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Series: | Epilepsy and Behavior Case Reports |
Online Access: | http://www.sciencedirect.com/science/article/pii/S2213323218301579 |
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author | Pei-Shan Hsiao Yuan-Ming Lee Fu-Sin Chu Chao-Lin Lee Fang-Chun Liu Ping-Huang Tsai |
author_facet | Pei-Shan Hsiao Yuan-Ming Lee Fu-Sin Chu Chao-Lin Lee Fang-Chun Liu Ping-Huang Tsai |
author_sort | Pei-Shan Hsiao |
collection | DOAJ |
description | Creutzfeldt–Jakob disease (CJD) presents with seizures as an early symptom in only approximately 3% of cases. These seizures often present as nonconvulsive status epilepticus (NCSE) or epilepsia partialis continua (EPC). Here, we describe a case of probable sporadic CJD (sCJD) in an 83-year-old man whose manifest an unusual presentation of left-hand tonic seizures without evolution to EPC, as well as brain MRI findings interpreted as peri-ictal changes, which led to an initial misdiagnosis of focal epilepsy. Keywords: Creutzfeldt–Jakob disease, Seizure, EEG, MRI |
first_indexed | 2024-12-13T02:14:48Z |
format | Article |
id | doaj.art-968cd179dbff4741bf6a71bd32b2fd0e |
institution | Directory Open Access Journal |
issn | 2213-3232 |
language | English |
last_indexed | 2024-12-13T02:14:48Z |
publishDate | 2019-01-01 |
publisher | Elsevier |
record_format | Article |
series | Epilepsy and Behavior Case Reports |
spelling | doaj.art-968cd179dbff4741bf6a71bd32b2fd0e2022-12-22T00:02:56ZengElsevierEpilepsy and Behavior Case Reports2213-32322019-01-01117780Probable sporadic Creutzfeldt–Jakob disease mimicking focal epilepsyPei-Shan Hsiao0Yuan-Ming Lee1Fu-Sin Chu2Chao-Lin Lee3Fang-Chun Liu4Ping-Huang Tsai5Department of Laboratory Medicine, National Yang-Ming University Hospital, No.169, Siaoshe Rd., Yilan City, Yilan County 26058, Taiwan; Division of Neurology, Department of Internal Medicine, National Yang-Ming University Hospital, No.169, Siaoshe Rd., Yilan City, Yilan County 26058, TaiwanDepartment of Laboratory Medicine, National Yang-Ming University Hospital, No.169, Siaoshe Rd., Yilan City, Yilan County 26058, TaiwanDivision of Neurology, Department of Internal Medicine, National Yang-Ming University Hospital, No.169, Siaoshe Rd., Yilan City, Yilan County 26058, Taiwan; Center for Dementia Care and Evolution, National Yang-Ming University Hospital, No.169, Siaoshe Rd., Yilan City, Yilan County 26058, TaiwanDivision of Neurology, Department of Internal Medicine, National Yang-Ming University Hospital, No.169, Siaoshe Rd., Yilan City, Yilan County 26058, Taiwan; Center for Dementia Care and Evolution, National Yang-Ming University Hospital, No.169, Siaoshe Rd., Yilan City, Yilan County 26058, TaiwanDivision of Neurology, Department of Internal Medicine, National Yang-Ming University Hospital, No.169, Siaoshe Rd., Yilan City, Yilan County 26058, Taiwan; Center for Dementia Care and Evolution, National Yang-Ming University Hospital, No.169, Siaoshe Rd., Yilan City, Yilan County 26058, TaiwanDivision of Neurology, Department of Internal Medicine, National Yang-Ming University Hospital, No.169, Siaoshe Rd., Yilan City, Yilan County 26058, Taiwan; Center for Dementia Care and Evolution, National Yang-Ming University Hospital, No.169, Siaoshe Rd., Yilan City, Yilan County 26058, Taiwan; Department of Neurology, School of Medicine, National Yang-Ming University, No.155, Sec.2, Linong Street, Taipei 112, Taiwan; Corresponding author at: Division of Neurology, Department of Internal Medicine, National Yang-Ming University Hospital, No.169, Siaoshe Rd., Yilan City, Yilan County 26058, Taiwan.Creutzfeldt–Jakob disease (CJD) presents with seizures as an early symptom in only approximately 3% of cases. These seizures often present as nonconvulsive status epilepticus (NCSE) or epilepsia partialis continua (EPC). Here, we describe a case of probable sporadic CJD (sCJD) in an 83-year-old man whose manifest an unusual presentation of left-hand tonic seizures without evolution to EPC, as well as brain MRI findings interpreted as peri-ictal changes, which led to an initial misdiagnosis of focal epilepsy. Keywords: Creutzfeldt–Jakob disease, Seizure, EEG, MRIhttp://www.sciencedirect.com/science/article/pii/S2213323218301579 |
spellingShingle | Pei-Shan Hsiao Yuan-Ming Lee Fu-Sin Chu Chao-Lin Lee Fang-Chun Liu Ping-Huang Tsai Probable sporadic Creutzfeldt–Jakob disease mimicking focal epilepsy Epilepsy and Behavior Case Reports |
title | Probable sporadic Creutzfeldt–Jakob disease mimicking focal epilepsy |
title_full | Probable sporadic Creutzfeldt–Jakob disease mimicking focal epilepsy |
title_fullStr | Probable sporadic Creutzfeldt–Jakob disease mimicking focal epilepsy |
title_full_unstemmed | Probable sporadic Creutzfeldt–Jakob disease mimicking focal epilepsy |
title_short | Probable sporadic Creutzfeldt–Jakob disease mimicking focal epilepsy |
title_sort | probable sporadic creutzfeldt jakob disease mimicking focal epilepsy |
url | http://www.sciencedirect.com/science/article/pii/S2213323218301579 |
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