Probable sporadic Creutzfeldt–Jakob disease mimicking focal epilepsy

Creutzfeldt–Jakob disease (CJD) presents with seizures as an early symptom in only approximately 3% of cases. These seizures often present as nonconvulsive status epilepticus (NCSE) or epilepsia partialis continua (EPC). Here, we describe a case of probable sporadic CJD (sCJD) in an 83-year-old man...

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Main Authors: Pei-Shan Hsiao, Yuan-Ming Lee, Fu-Sin Chu, Chao-Lin Lee, Fang-Chun Liu, Ping-Huang Tsai
Format: Article
Language:English
Published: Elsevier 2019-01-01
Series:Epilepsy and Behavior Case Reports
Online Access:http://www.sciencedirect.com/science/article/pii/S2213323218301579
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author Pei-Shan Hsiao
Yuan-Ming Lee
Fu-Sin Chu
Chao-Lin Lee
Fang-Chun Liu
Ping-Huang Tsai
author_facet Pei-Shan Hsiao
Yuan-Ming Lee
Fu-Sin Chu
Chao-Lin Lee
Fang-Chun Liu
Ping-Huang Tsai
author_sort Pei-Shan Hsiao
collection DOAJ
description Creutzfeldt–Jakob disease (CJD) presents with seizures as an early symptom in only approximately 3% of cases. These seizures often present as nonconvulsive status epilepticus (NCSE) or epilepsia partialis continua (EPC). Here, we describe a case of probable sporadic CJD (sCJD) in an 83-year-old man whose manifest an unusual presentation of left-hand tonic seizures without evolution to EPC, as well as brain MRI findings interpreted as peri-ictal changes, which led to an initial misdiagnosis of focal epilepsy. Keywords: Creutzfeldt–Jakob disease, Seizure, EEG, MRI
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spelling doaj.art-968cd179dbff4741bf6a71bd32b2fd0e2022-12-22T00:02:56ZengElsevierEpilepsy and Behavior Case Reports2213-32322019-01-01117780Probable sporadic Creutzfeldt–Jakob disease mimicking focal epilepsyPei-Shan Hsiao0Yuan-Ming Lee1Fu-Sin Chu2Chao-Lin Lee3Fang-Chun Liu4Ping-Huang Tsai5Department of Laboratory Medicine, National Yang-Ming University Hospital, No.169, Siaoshe Rd., Yilan City, Yilan County 26058, Taiwan; Division of Neurology, Department of Internal Medicine, National Yang-Ming University Hospital, No.169, Siaoshe Rd., Yilan City, Yilan County 26058, TaiwanDepartment of Laboratory Medicine, National Yang-Ming University Hospital, No.169, Siaoshe Rd., Yilan City, Yilan County 26058, TaiwanDivision of Neurology, Department of Internal Medicine, National Yang-Ming University Hospital, No.169, Siaoshe Rd., Yilan City, Yilan County 26058, Taiwan; Center for Dementia Care and Evolution, National Yang-Ming University Hospital, No.169, Siaoshe Rd., Yilan City, Yilan County 26058, TaiwanDivision of Neurology, Department of Internal Medicine, National Yang-Ming University Hospital, No.169, Siaoshe Rd., Yilan City, Yilan County 26058, Taiwan; Center for Dementia Care and Evolution, National Yang-Ming University Hospital, No.169, Siaoshe Rd., Yilan City, Yilan County 26058, TaiwanDivision of Neurology, Department of Internal Medicine, National Yang-Ming University Hospital, No.169, Siaoshe Rd., Yilan City, Yilan County 26058, Taiwan; Center for Dementia Care and Evolution, National Yang-Ming University Hospital, No.169, Siaoshe Rd., Yilan City, Yilan County 26058, TaiwanDivision of Neurology, Department of Internal Medicine, National Yang-Ming University Hospital, No.169, Siaoshe Rd., Yilan City, Yilan County 26058, Taiwan; Center for Dementia Care and Evolution, National Yang-Ming University Hospital, No.169, Siaoshe Rd., Yilan City, Yilan County 26058, Taiwan; Department of Neurology, School of Medicine, National Yang-Ming University, No.155, Sec.2, Linong Street, Taipei 112, Taiwan; Corresponding author at: Division of Neurology, Department of Internal Medicine, National Yang-Ming University Hospital, No.169, Siaoshe Rd., Yilan City, Yilan County 26058, Taiwan.Creutzfeldt–Jakob disease (CJD) presents with seizures as an early symptom in only approximately 3% of cases. These seizures often present as nonconvulsive status epilepticus (NCSE) or epilepsia partialis continua (EPC). Here, we describe a case of probable sporadic CJD (sCJD) in an 83-year-old man whose manifest an unusual presentation of left-hand tonic seizures without evolution to EPC, as well as brain MRI findings interpreted as peri-ictal changes, which led to an initial misdiagnosis of focal epilepsy. Keywords: Creutzfeldt–Jakob disease, Seizure, EEG, MRIhttp://www.sciencedirect.com/science/article/pii/S2213323218301579
spellingShingle Pei-Shan Hsiao
Yuan-Ming Lee
Fu-Sin Chu
Chao-Lin Lee
Fang-Chun Liu
Ping-Huang Tsai
Probable sporadic Creutzfeldt–Jakob disease mimicking focal epilepsy
Epilepsy and Behavior Case Reports
title Probable sporadic Creutzfeldt–Jakob disease mimicking focal epilepsy
title_full Probable sporadic Creutzfeldt–Jakob disease mimicking focal epilepsy
title_fullStr Probable sporadic Creutzfeldt–Jakob disease mimicking focal epilepsy
title_full_unstemmed Probable sporadic Creutzfeldt–Jakob disease mimicking focal epilepsy
title_short Probable sporadic Creutzfeldt–Jakob disease mimicking focal epilepsy
title_sort probable sporadic creutzfeldt jakob disease mimicking focal epilepsy
url http://www.sciencedirect.com/science/article/pii/S2213323218301579
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