Sinus of valsalva aneurysm in Blau's syndrome
<p>Abstract</p> <p>Blau syndrome is a rare granulomatous disorder inherited in an autosomal dominant manner characterized by the early appearance of granulomatous arthritis, skin rash and anterior uveitis. There are very few data on the cardiovascular manifestations of Blau syndrom...
| Main Authors: | , |
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| Format: | Article |
| Language: | English |
| Published: |
BMC
2010-03-01
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| Series: | Journal of Cardiothoracic Surgery |
| Online Access: | http://www.cardiothoracicsurgery.org/content/5/1/16 |
| _version_ | 1811249941763325952 |
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| author | Tang Augustine Mourad Faisal |
| author_facet | Tang Augustine Mourad Faisal |
| author_sort | Tang Augustine |
| collection | DOAJ |
| description | <p>Abstract</p> <p>Blau syndrome is a rare granulomatous disorder inherited in an autosomal dominant manner characterized by the early appearance of granulomatous arthritis, skin rash and anterior uveitis. There are very few data on the cardiovascular manifestations of Blau syndrome. Here we report the first case of sinus of valsava aneurysm in Blau syndrome. In isolated unruptured aneurysms of a sinus of Valsalva without compromise of the aortic valve and/or the coronary ostia, repair may be accomplished by simple placation of the aneurysm or excision of the aneurysm(s) and patch closure of the defect(s) between the aortic annulus and the sinu-vascular ridge. Because of the particular conditions in our case, the repair was performed with replacement of the aortic valve and root using a composite graft employing a modified Bentall's technique.</p> |
| first_indexed | 2024-04-12T15:56:18Z |
| format | Article |
| id | doaj.art-975de9aca41f48bcbe958951962e7b0c |
| institution | Directory Open Access Journal |
| issn | 1749-8090 |
| language | English |
| last_indexed | 2024-04-12T15:56:18Z |
| publishDate | 2010-03-01 |
| publisher | BMC |
| record_format | Article |
| series | Journal of Cardiothoracic Surgery |
| spelling | doaj.art-975de9aca41f48bcbe958951962e7b0c2022-12-22T03:26:21ZengBMCJournal of Cardiothoracic Surgery1749-80902010-03-01511610.1186/1749-8090-5-16Sinus of valsalva aneurysm in Blau's syndromeTang AugustineMourad Faisal<p>Abstract</p> <p>Blau syndrome is a rare granulomatous disorder inherited in an autosomal dominant manner characterized by the early appearance of granulomatous arthritis, skin rash and anterior uveitis. There are very few data on the cardiovascular manifestations of Blau syndrome. Here we report the first case of sinus of valsava aneurysm in Blau syndrome. In isolated unruptured aneurysms of a sinus of Valsalva without compromise of the aortic valve and/or the coronary ostia, repair may be accomplished by simple placation of the aneurysm or excision of the aneurysm(s) and patch closure of the defect(s) between the aortic annulus and the sinu-vascular ridge. Because of the particular conditions in our case, the repair was performed with replacement of the aortic valve and root using a composite graft employing a modified Bentall's technique.</p>http://www.cardiothoracicsurgery.org/content/5/1/16 |
| spellingShingle | Tang Augustine Mourad Faisal Sinus of valsalva aneurysm in Blau's syndrome Journal of Cardiothoracic Surgery |
| title | Sinus of valsalva aneurysm in Blau's syndrome |
| title_full | Sinus of valsalva aneurysm in Blau's syndrome |
| title_fullStr | Sinus of valsalva aneurysm in Blau's syndrome |
| title_full_unstemmed | Sinus of valsalva aneurysm in Blau's syndrome |
| title_short | Sinus of valsalva aneurysm in Blau's syndrome |
| title_sort | sinus of valsalva aneurysm in blau s syndrome |
| url | http://www.cardiothoracicsurgery.org/content/5/1/16 |
| work_keys_str_mv | AT tangaugustine sinusofvalsalvaaneurysminblaussyndrome AT mouradfaisal sinusofvalsalvaaneurysminblaussyndrome |