Pulmonary artery dissection in long standing idiopathic pulmonary arterial hypertension: A case report
Pulmonary arterial dissection (PAD) is a rare and often lethal complication of chronic pulmonary arterial hypertension (PAH), which may occurs in patients with idiopathic pulmonary arterial hypertension (IPAH) and potentially in those with connective tissue disorders. While rare, sudden death often...
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| Format: | Article |
| Language: | English |
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Elsevier
2022-01-01
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| Series: | Radiology Case Reports |
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| Online Access: | http://www.sciencedirect.com/science/article/pii/S1930043321007494 |
| _version_ | 1818573907379093504 |
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| author | Luis Regalado, BS, MSc Carol Vitellas, BA Lindsay Wright, MD Asvin Ganapathi, MD Bryan A. Whitson, MD, PhD Chiemezie Chianotu Amadi, MD, MA |
| author_facet | Luis Regalado, BS, MSc Carol Vitellas, BA Lindsay Wright, MD Asvin Ganapathi, MD Bryan A. Whitson, MD, PhD Chiemezie Chianotu Amadi, MD, MA |
| author_sort | Luis Regalado, BS, MSc |
| collection | DOAJ |
| description | Pulmonary arterial dissection (PAD) is a rare and often lethal complication of chronic pulmonary arterial hypertension (PAH), which may occurs in patients with idiopathic pulmonary arterial hypertension (IPAH) and potentially in those with connective tissue disorders. While rare, sudden death often occurs secondary to acute cardiac tamponade, as the pulmonary artery dissects into the pericardium; this diagnosis is often made postmortem. Nevertheless, with the proliferation of multidetector computed tomography (MDCT) as a diagnostic test, patients may be identified very early after symptom onset, prompting rapid intervention with decreased morbidity and mortality. We report a case of IPAH complicated by pulmonary artery aneurysm (PAA) and PAD, diagnosed by CT pulmonary angiogram (CTPA), and treated with bilateral lung transplantation, pulmonic valve replacement, and re-anastomosis of the donor main PA to a pulmonary valve conduit. |
| first_indexed | 2024-12-15T00:19:11Z |
| format | Article |
| id | doaj.art-979482b0c26b4674a9e890ffde928155 |
| institution | Directory Open Access Journal |
| issn | 1930-0433 |
| language | English |
| last_indexed | 2024-12-15T00:19:11Z |
| publishDate | 2022-01-01 |
| publisher | Elsevier |
| record_format | Article |
| series | Radiology Case Reports |
| spelling | doaj.art-979482b0c26b4674a9e890ffde9281552022-12-21T22:42:22ZengElsevierRadiology Case Reports1930-04332022-01-01171227231Pulmonary artery dissection in long standing idiopathic pulmonary arterial hypertension: A case reportLuis Regalado, BS, MSc0Carol Vitellas, BA1Lindsay Wright, MD2Asvin Ganapathi, MD3Bryan A. Whitson, MD, PhD4Chiemezie Chianotu Amadi, MD, MA5The Ohio State University, College of Medicine, 370 W 9th Ave, Columbus, OH 43210, USAThe Ohio State University, College of Medicine, 370 W 9th Ave, Columbus, OH 43210, USADepartment of Radiology, The Ohio State University, Wexner Medical Center, 395 W 12th Ave, Columbus, OH 43210, USADivision of Cardiac Surgery, Department of Surgery, The Ohio State University, Wexner Medical Center, 410 W. 10th Ave, Columbus OH 43210, USADivision of Cardiac Surgery, Department of Surgery, The Ohio State University, Wexner Medical Center, 410 W. 10th Ave, Columbus OH 43210, USADepartment of Radiology, The Ohio State University, Wexner Medical Center, 395 W 12th Ave, Columbus, OH 43210, USA; Corresponding author.Pulmonary arterial dissection (PAD) is a rare and often lethal complication of chronic pulmonary arterial hypertension (PAH), which may occurs in patients with idiopathic pulmonary arterial hypertension (IPAH) and potentially in those with connective tissue disorders. While rare, sudden death often occurs secondary to acute cardiac tamponade, as the pulmonary artery dissects into the pericardium; this diagnosis is often made postmortem. Nevertheless, with the proliferation of multidetector computed tomography (MDCT) as a diagnostic test, patients may be identified very early after symptom onset, prompting rapid intervention with decreased morbidity and mortality. We report a case of IPAH complicated by pulmonary artery aneurysm (PAA) and PAD, diagnosed by CT pulmonary angiogram (CTPA), and treated with bilateral lung transplantation, pulmonic valve replacement, and re-anastomosis of the donor main PA to a pulmonary valve conduit.http://www.sciencedirect.com/science/article/pii/S1930043321007494Pulmonary hypertensionPulmonary artery aneurysmPulmonary arterial hypertensionIdiopathic pulmonary arterial hypertensionPulmonary artery dissectionLung transplantation |
| spellingShingle | Luis Regalado, BS, MSc Carol Vitellas, BA Lindsay Wright, MD Asvin Ganapathi, MD Bryan A. Whitson, MD, PhD Chiemezie Chianotu Amadi, MD, MA Pulmonary artery dissection in long standing idiopathic pulmonary arterial hypertension: A case report Radiology Case Reports Pulmonary hypertension Pulmonary artery aneurysm Pulmonary arterial hypertension Idiopathic pulmonary arterial hypertension Pulmonary artery dissection Lung transplantation |
| title | Pulmonary artery dissection in long standing idiopathic pulmonary arterial hypertension: A case report |
| title_full | Pulmonary artery dissection in long standing idiopathic pulmonary arterial hypertension: A case report |
| title_fullStr | Pulmonary artery dissection in long standing idiopathic pulmonary arterial hypertension: A case report |
| title_full_unstemmed | Pulmonary artery dissection in long standing idiopathic pulmonary arterial hypertension: A case report |
| title_short | Pulmonary artery dissection in long standing idiopathic pulmonary arterial hypertension: A case report |
| title_sort | pulmonary artery dissection in long standing idiopathic pulmonary arterial hypertension a case report |
| topic | Pulmonary hypertension Pulmonary artery aneurysm Pulmonary arterial hypertension Idiopathic pulmonary arterial hypertension Pulmonary artery dissection Lung transplantation |
| url | http://www.sciencedirect.com/science/article/pii/S1930043321007494 |
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