PAUCITY OF INTRAHEPATIC BILE DUCTS
The paucity of intrahepatic bile ducts is characterized by reducing the quantity of interlobular bile ducts in re- lation to portal tracts of the liver. There are two defined forms of paucity of intrahepaticbile ducts: syndromatic, which is associated with various extrahepatic abnormalities and nons...
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| Format: | Article |
| Language: | Russian |
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Federal Research Center of Transplantology and Artificial Organs named after V.I.Shumakov
2013-05-01
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| Series: | Vestnik Transplantologii i Iskusstvennyh Organov |
| Subjects: | |
| Online Access: | https://journal.transpl.ru/vtio/article/view/125 |
| _version_ | 1797872157482549248 |
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| author | O. E. Iryshkin I. M. Iljinsky O. M. Tsirulnikova |
| author_facet | O. E. Iryshkin I. M. Iljinsky O. M. Tsirulnikova |
| author_sort | O. E. Iryshkin |
| collection | DOAJ |
| description | The paucity of intrahepatic bile ducts is characterized by reducing the quantity of interlobular bile ducts in re- lation to portal tracts of the liver. There are two defined forms of paucity of intrahepaticbile ducts: syndromatic, which is associated with various extrahepatic abnormalities and nonsyndromatic, being the heterogeneous group of disorders, including congenital infections, metabolic, endocrine, immune disorders, congenital infections and various other disorders. In many instances paucity of intrahepatic bile ducts remains idiopathic. The review contains terminological issues, the description of the classification and the morphological characteristic, the dif- ferences of syndromatic and nonsyndromatic forms of paucity of intrahepatic bile ducts, and also the description of principles of differential diagnosis of paucity of intrahepatic bile ducts and biliary atresia. |
| first_indexed | 2024-04-10T00:54:24Z |
| format | Article |
| id | doaj.art-98660ae4fab54e6eb2d2a88d4ac37117 |
| institution | Directory Open Access Journal |
| issn | 1995-1191 |
| language | Russian |
| last_indexed | 2024-04-10T00:54:24Z |
| publishDate | 2013-05-01 |
| publisher | Federal Research Center of Transplantology and Artificial Organs named after V.I.Shumakov |
| record_format | Article |
| series | Vestnik Transplantologii i Iskusstvennyh Organov |
| spelling | doaj.art-98660ae4fab54e6eb2d2a88d4ac371172023-03-13T10:37:18ZrusFederal Research Center of Transplantology and Artificial Organs named after V.I.ShumakovVestnik Transplantologii i Iskusstvennyh Organov1995-11912013-05-0115213514110.15825/1995-1191-2013-2-135-14168PAUCITY OF INTRAHEPATIC BILE DUCTSO. E. Iryshkin0I. M. Iljinsky1O. M. Tsirulnikova2Academician V.I. Shumakov Federal Research Center of Transplantology and Artificial Organs (Head – academician of RAMSci, prof. S.V. Gautier), Moscow, Russian FederationAcademician V.I. Shumakov Federal Research Center of Transplantology and Artificial Organs (Head – academician of RAMSci, prof. S.V. Gautier), Moscow, Russian Federation Department of Tansplantology and Artificial organs (Head – academician of RAMSci, prof. S.V. Gautier) I.M. Sechenov First Moscow State Medical University (Rector – corresponding member of RAMSci, prof. P.V. Glybochko), Moscow, Russian FederationAcademician V.I. Shumakov Federal Research Center of Transplantology and Artificial Organs (Head – academician of RAMSci, prof. S.V. Gautier), Moscow, Russian Federation Department of Tansplantology and Artificial organs (Head – academician of RAMSci, prof. S.V. Gautier) I.M. Sechenov First Moscow State Medical University (Rector – corresponding member of RAMSci, prof. P.V. Glybochko), Moscow, Russian FederationThe paucity of intrahepatic bile ducts is characterized by reducing the quantity of interlobular bile ducts in re- lation to portal tracts of the liver. There are two defined forms of paucity of intrahepaticbile ducts: syndromatic, which is associated with various extrahepatic abnormalities and nonsyndromatic, being the heterogeneous group of disorders, including congenital infections, metabolic, endocrine, immune disorders, congenital infections and various other disorders. In many instances paucity of intrahepatic bile ducts remains idiopathic. The review contains terminological issues, the description of the classification and the morphological characteristic, the dif- ferences of syndromatic and nonsyndromatic forms of paucity of intrahepatic bile ducts, and also the description of principles of differential diagnosis of paucity of intrahepatic bile ducts and biliary atresia.https://journal.transpl.ru/vtio/article/view/125syndromatic and nonsyndromatic paucity of intrahepatic bile ductsalagille syndromebiliary atresiaextrahepatic and intrahepatic bile ducts |
| spellingShingle | O. E. Iryshkin I. M. Iljinsky O. M. Tsirulnikova PAUCITY OF INTRAHEPATIC BILE DUCTS Vestnik Transplantologii i Iskusstvennyh Organov syndromatic and nonsyndromatic paucity of intrahepatic bile ducts alagille syndrome biliary atresia extrahepatic and intrahepatic bile ducts |
| title | PAUCITY OF INTRAHEPATIC BILE DUCTS |
| title_full | PAUCITY OF INTRAHEPATIC BILE DUCTS |
| title_fullStr | PAUCITY OF INTRAHEPATIC BILE DUCTS |
| title_full_unstemmed | PAUCITY OF INTRAHEPATIC BILE DUCTS |
| title_short | PAUCITY OF INTRAHEPATIC BILE DUCTS |
| title_sort | paucity of intrahepatic bile ducts |
| topic | syndromatic and nonsyndromatic paucity of intrahepatic bile ducts alagille syndrome biliary atresia extrahepatic and intrahepatic bile ducts |
| url | https://journal.transpl.ru/vtio/article/view/125 |
| work_keys_str_mv | AT oeiryshkin paucityofintrahepaticbileducts AT imiljinsky paucityofintrahepaticbileducts AT omtsirulnikova paucityofintrahepaticbileducts |